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정지예 ( Ji Ye Jung ),홍준석 ( Joon Seok Hong ),김혜진 ( Hye Jin Kim ),손유경 ( Yoo Kyung Sohn ),심순섭 ( Soon Sup Shim ),박중신 ( Joong Shin Park ),전종관 ( Jong Kwan Jun ),윤보현 ( Bo Hyun Yoon ),신희철 ( Hee Chul Syn ) 대한주산의학회 2006 Perinatology Vol.17 No.2
목적 : 본 연구의 목적은 입술 및 입천장갈림증의 유형에 따른 임신 결과 및 생후 장애를 비교하고, 입천장갈림증의 유무에 따른 위험도를 평가하는 것이다. 방법 : 990년 1월부터 2004년 7월까지 서울대학교병원에서 분만, 유산, 또는 임신중절된 입술 및 입천장갈림증 96례를 후향적으로 분석하였다. 입술 및 입천장갈림증의 분류는 Nyberg 등의 방법을 중심으로 입천장갈림증 단목을 추가하였다. 유형별로 동반 기형, 염색체 이상의 빈도를 평가하고, 임신 중절, 자연유산, 자궁 내 태아사망, 영아사망의 빈도를 비교하였다. 생존아 중 장기 추적이 가능한 경우에 중이 환기관 삽입, 청각장애, 언어발달 장애를 비교하였다. 입천장갈림증이 있는 경우에 입술갈림증 단독 군보다 어느 정도 위험이 증가하는지 평가하였다. 결과 : 동반 기형은 입술갈림증만 있는 경우 23.7% (9/38)이었고, 입천장갈림증이 있는 경우는 55.2% (32/58)이었다. 동반 기형으로는 심장기형이 가장 많았고 중추신경계, 근골격계, 위장관계, 비뇨생식기계 기형도 흔하였으며, 67.4% (29/43)의 증례에서 다발성 기형으로 관찰되었다. 입천장갈림증이 있는 생존아의 경우 입술갈림증만 있는 경우보다 중이 환기관 삽입 (70.0% [14/20] vs 3.1% [1/32])과 언어발달 장애 (42.1 % [8/19] vs 10.7% [3/28])의 발생이 유의하게 많았다. 입천장갈림증이 있는 경우에 입술갈림증만 있는 군보다 동반기형(OR 3.97), 임신중절(OR 5.20), 영아사망(OR 12.96), 중이 환기관 삽입 (OR 72.33), 언어발달 장애 (OR 6.06) 발생의 위험이 증가하였다. 결론 : 입천장갈림증을 동반한 군이 입술갈림증만 단독으로 가진 군에 비하여 임신 결과, 중이 질환, 언어발달 장애에 있어서 불량한 예후를 보이고 있다. 따라서, 산전 정밀초음파 검사시에 입술갈림증 뿐만 아니라 입천장갈림증 유무의 진단에도 주의를 기울여야 한다. Objective : The objective of this study is to compare the pregnancy outcomes and postnatal developmental problems according to the types of cleft lip and/or palate, and to evaluate the increase of the risk of the presence of cleft palate. Methods : Retrospective analysis was performed in 96 cases of cleft lip and/or palate that were delivered, aborted, or terminated at Seoul National University Hospital from January 1990 to July 2004. The cases of cleft lip and/or palate were categorized based on the Nyberg`s classification, and cleft palate alone was added to it. According to the types, the frequencies of associated anomaly and chromosomal anomaly were assessed, and the frequencies of termination, spontaneous abortion, fetal death in utero, and infant death were compared. When long-term follow-up was possible among the surviving infants, we compared the frequencies of ventilatory tube insertion into the middle ear, hearing problem, and speech-language problem. We evaluated the increase of the risk in the presence of cleft palate. Results : Associated anomalies were present in 23.7% (9/38) of cases with cleft lip alone and in 55.1 % (32/58) of those with cleft palate. The most common associated anomaly was cardiac anomaly. The surviving infants with cleft palate showed significantly higher rates of ventilatory tube insertion (70.0% [14/20] vs 3.1% [1/32]) and speech-language problem (42.1 % [8/19] vs 10.7 % [3/28]) than those with cleft lip alone. The presence of cleft palate increased the risk of occurrence of associated anomaly (OR 3.97), termination (OR 5.20), infant death (OR 12.96), ventilatory tube insertion (OR 72.33), and speech-language problem (OR 6.06). Conclusion : Associated cleft palate in patients with cleft lip has a poor impact on pregnancy outcomes, middle ear disease, and speech-language problem. Therefore, during the prenatal screening ultraso-nography, the careful examination should be directed for the detection of cleft palate in cases with cleft lip.
천식 환자에서 전반적 자기 평가와 한국 성인 천식 환자의 삶의 질 평가 설문과의 비교 분석
정지예 ( Ji Ye Jung ),손지영 ( Ji Young Son ),홍수정 ( Soo Jung Hong ),이용원 ( Yong Won Lee ),신유섭 ( Yu Seob Sin ),박중원 ( Jung Won Park ),홍천수 ( Chein Soo Hong ) 대한천식알레르기학회 2008 천식 및 알레르기 Vol.28 No.2
Background: The Quality of Life Questionnaire for Adult Korean Asthmatics (QLQAKA) is a valid and reproducible tool for evaluating and monitoring Korean adult asthmatics. However, the questionnaire is still burden to some patients, so we developed a simplified global self-assessment scoring. Objective: The goal of this study is to compare the patient``s global self-assessment scoring method with the QLQAKA and evaluate how it reflects quality of life (QOL) of asthmatics. Method: One hundred ninety-nine adult asthmatics were enrolled and asked to answer the QLQAKA composed of 17 items in 4 domains (activity, symptom, emotion and exposure to environmental stimuli) and one more global self-assessment question with a 5-point scale was added. According to the Global Initiative for Asthma (GINA) 2006 guidelines, patients were divided into 3 groups: controlled, partly controlled and uncontrolled groups. Then, we analyzed the relationships between the QLQAKA scores, global self-assessment scores and various clinical parameters. Result: The mean QLQAKA score and global self-assessment score were statistically significantly different between the 3 groups. Pulmonary function tests were also statistically significantly different between the 5 QLQAKA score subgroups as well as 5 self-assessment score subgroups. Moreover, global self-assessment scores were well correlated with QLQAKA scores. Conclusion: In a busy outpatient clinic, we may estimate the QOL of asthma patients using a simplified patient``s global self-assessment scoring method. (Korean J Asthma Allergy Clin Immunol 2008;28:134-142)
우중하엽 폐허탈 및 폐쇄세기관지기질화 폐렴을 유발한 기관지 지방종
손지영 ( Ji Young Son ),정지예 ( Ji Ye Jung ),하유정 ( You Jung Ha ),홍수정 ( Soo Jung Hong ),정민규 ( Min Kyu Jung ),정문재 ( Moon Jae Chung ),서용성 ( Yong Sung Seo ),문지애 ( Ji Ae Moon ),변민광 ( Min Kwang Byun ),박병훈 ( Byun 대한결핵 및 호흡기학회 2008 Tuberculosis and Respiratory Diseases Vol.65 No.4
Lipoma is a common neoplasm in soft tissues. However, an intrapulmonary lipoma is a rare benign tumor. Patients with a bronchial lipoma might have a malignant potential related to their smoking history due to the case reports of lung cancer accompanied with lipoma. Endobronchial lipoma can cause irreversible parenchymal lung damage if not diagnosed and treated early. Therefore, it should initially be treated by fiberoptic bronchoscopy or surgery depending on the status of distal parenchymal lung damage. Bronchiolitis obliterans with organizing pneumonia (BOOP) is a pathological syndrome that is defined by the presence of buds of granulation tissue consisting of fibroblasts and collagen within the lumen of the distal air spaces. BOOP is caused by drug intoxication, connective tissue disease, infection, obstructive pneumonia, tumors, or an unknown etiology. We encountered a 58 year-old male patient with endobronchial lipoma, causing the collapse of the right middle and lower lobes, and BOOP due to obstructive pneumonia. (Tuberc Respir Dis 2008;65:313-317)
결핵 환자에서 Rifampin에 의한 Henoch-Shonlein Purpura
김혜련 ( Hye Ryun Kim ),박병훈 ( Byung Hoon Park ),손지영 ( Ji Young Son ),정지예 ( Ji Ye Jung ),안정련 ( Jung Ryun Ahn ),정윤숙 ( Yoon Suk Jung ),임주은 ( Ju Eun Lim ),정주원 ( Ju Won Jung ),문지애 ( Ji Ae Moon ),변민광 ( Min Kwa 대한결핵 및 호흡기학회 2008 Tuberculosis and Respiratory Diseases Vol.65 No.2
Rifampin is one of the first line drugs for treating tuberculosis, but it might be associated with serious adverse effects, including renal failure. We report here on a case of a 57-year-old patient who developed Henoch-Shonlein purpura during antituberculosis therapy that included rifampin. The patient converted to negative on the AFB smear for tuberculosis two weeks after the initial administration of antituberculosis medication. After treatment for 60 days, this patient was diagnosed with Henoch-Shonlein purpura by the purpura lesion on the lower legs, the leukocytoclastic vasculitis, the renal impairment and the pathological examination. After stopping rifampin, the skin lesions disappeared in about 10 days and his renal function gradually improved. This case study showed that Henoch-Schonlein purpura can be caused by rifampin during antituberculosis therapy and we recommend that the use of rifampin should be restrained when clinical symptoms of Henoch-Shonlein purpura are observed. (Tuberc Respir Dis 2008;65:116-120)
궤양성 대장염에서 나타난 폐쇄성 세기관지염 기질화 폐렴
이현정 ( Hyun Jung Lee ),박병훈 ( Byung Hoon Park ),손지영 ( Ji Young Son ),정지예 ( Ji Ye Jung ),황세나 ( Se Na Hwang ),전영은 ( Young Eun Chon ),김은영 ( Eun Young Kim ),임주은 ( Ju Eun Lim ),이경종 ( Kyung Jong Lee ),윤여운 ( Y 대한결핵 및 호흡기학회 2010 Tuberculosis and Respiratory Diseases Vol.68 No.3
The ulcerative colitis is a chronic inflammatory bowel disease with an unknown etiology. The major symptoms of ulcerative colitis are diarrhea, abdominal pain and hematochezia. However, arthritis, skin disorders, hepatobiliary inflammation and uveitis are occasionally recognized as systemic complications. Although there are few reports of coexistent pulmonary and inflammatory bowel disease, the lung is not generally considered to be a target organ in ulcerative colitis. We report a patient with ulcerative colitis-related bronchilolitis obliterans organizing pneumonia confirmed by video-assisted thoracoscopic surgery, who responded to corticosteroid therapy.
인삼양영탕(人蔘養榮湯) 투여로 호전된 갱년기장애(更年期障碍) 15예(例)에 대한 임상고찰
조성희,양승정,박경미,조현정,정지예,반혜란,Jo, Seung-Hee,Yang, Seung-Jung,Park, Gyeong-Mi,Jo, Hyeon-Jeong,Jeong, Ji-Ye,Ban, Hye-Ran 대한한방체열의학회 2006 대한한방체열의학회지 Vol.5 No.1
Objective: The purpose of this study is to evaluate the effects of Insamyang-yeongtang on menopausal disorder patients Methods : We surveyed 15 menopausal disorder patients who had been administered Insamyang-yeongtang. The patients of menopausal disorder had been estimated twice with Kupperman's index. Result : When patients had been not administered Insamyang-yeongtang. the mean of Kupperman's index score are $42.73(SD{\pm}19.16)$. When administered Insamyang-yeongtang, the mean of kupperman's index score are $25.87(SD{\pm}19.16)$. The difference mean of first and last score are 16.87(p-value 0.001). Conclusion : This study suggests that Insamyang-yeongtang is significantly effective on menopausal disorder patients.
Btk 유전자 인트론 2 돌연변이에 의한 X연관 무감마글로불린혈증
정문재 ( Moon Jae Chung ),정지예 ( Ji Ye Jung ),손지영 ( Ji Young Son ),구철룡 ( Cheol Ryong Ku ),박병훈 ( Byung Hoon Park ),변민광 ( Min Kwang Byun ),문지애 ( Ji Ae Moon ),김영삼 ( Young Sam Kim ),김세규 ( Se Kyu Kim ),장준 ( Jo 대한결핵 및 호흡기학회 2008 Tuberculosis and Respiratory Diseases Vol.65 No.3
X-linked agammaglobulinemia is the most common type of primary immunodeficiency disorder. Mutation ofthe cytoplasmic tyrosine kinase gene, Btk (Bruton`s tyrosine kinase), is known to be the etiology of X-linked agammaglobulinemia. The patients with this disease manifest a B-cell deficiency and low levels of serum immunoglobulin; due to the deficient antibodies, they suffers from recurrent upper and lower respiratory infections. We report here a 24-year-old male with an initial clinical impression of recurrent pneumonia and bronchiectasis. The patient presented with marked pan-hypogammaglobulinemia and the absence of circulating B-lymphocytes on the immunologic study, and he carried a splicing mutation of intron 2 in the Btk gene (IVS2 -3C>G). (Tuberc Respir Dis 2008;65:207-211)
쌍태 임신에서 경질초음파를 이용한 임신 주수에 따른 자궁경부 길이의 정상역 설정에 관한 연구
김혜진 ( Hye Jin Kim ),홍준석 ( Joon Seok Hong ),박교훈 ( Kyo Hoon Park ),정지예 ( Ji Ye Jung ),박혜은 ( Hye Eun Park ),김현준 ( Hyun Jun Kim ),한상훈 ( Sang Hoon Han ),전용탁 ( Yong Tark Jeon ),지병철 ( Byung Chul Jee ),김용범 ( 대한산부인과학회 2006 Obstetrics & Gynecology Science Vol.49 No.2