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변준호(June-Ho Byun),최문정(Moon-Jeong Choi),이종실(Jong-Sil Lee),노규진(Gyu-Jin Rho),김종렬(Jong-Ryoul Kim),박봉욱(Bong-Wook Park) 대한구강악안면외과학회 2008 대한구강악안면외과학회지 Vol.34 No.6
Mesenchymal chondrosarcoma is a rare malignant tumor of bone and soft tissue. This aggressive form of chondrosarcoma represents only 3% to 9% of all chondrosarcomas. This neoplasm is characterized by sheets or clusters of undifferentiated spindle or round cells surrounding discrete nodules of well-differentiated cartilage. We experienced a case of mesenchymal chondrosarcoma on mandibular body. Two years ago, the patient had been treated the intrabony cystic lesion on mandiblular left body. At that time, cartilage portion was not detected in the cystic specimen. Two years after cyst enucleation, the recurred large neoplasm in the mandibular left body was noted, and it was diagnosed as 4.5 cm sized mesenchymal chondrosarcoma. The mandibular tumor was widely resected and rigid-plate and cervical musculocutaneous flap were used for reconstruction of resected bone and soft tissues. No complications and recurrence were noted for 6 months postoperatively.
서준호(Joon-Ho Suh),김여갑(Yeo-Gab Kim),권용대(Yong-Dae Kwon),최병준(Byung-Joon Choi),김영란(Young-Ran Kim),이백수(Baek-Soo Lee) 대한구강악안면외과학회 2010 대한구강악안면외과학회지 Vol.36 No.2
Mesenchymal chondrosarcoma is very aggressive and represents approximately 1% of all chondrosarcomas. While it affects a very wide age range, the peak frequency is in the second decade of life. It may occur in the head and rib region with a predilection for the maxillofacial skeleton. The small cell undifferentiated component may assume a hemangiopericytoma-like vascular pattern and should be distinguished from hemangiopericytoma. Treatment is en bloc resection, the intended tissue margins of excision should be designed to extend well beyond the actual tumor margin, as mesenchymal chondrosarcomas. Aggressive behavior of mesenchymal chondrosarcoma of the jaw, with a tendency for delayed recurrence and metastasis even many years after treatment. The most frequent site of metastasis was the lung. Here we present 52 years old , female case of mesenchymal chondrosarcoma occurs on Rt. mandible.
권오현,김정득,박상준,김의중,윤성문,Kwon, O Hyun,Kim, Jung Deuk,Park, Sang June,Kim, Eui Joong,Yoon, Sung Moon 대한신경외과학회 2001 Journal of Korean neurosurgical society Vol.30 No.11
Mesenchymal chondrosarcoma is a rare tumor occurring in both bone and soft tissues and exhibits characteristic of a malignant nature. The authors experienced a case of mesenchymal chondrosarcoma occurring in a 23-year-old woman which had invaded the cervical spine. The patient presented with severe both shoulder pain, left upper extremity weakness(Grade IV) and paresthesia at admission. Radiologic studies of the cervial spine showed an aggressive osteolysis of C4 vertebral body, pedicle and lamina with compression of the spinal cord posteriorly on C3, C4, C5 levels. The tumor was totally removed by a combined anterior and posterior approach. The removed vertebral body was replaced with autogenous bone and stabilized by Codman locking plate symtem. The pathological examination showed characteristic of mesenchymal chondrosarcoma.previous symptoms well improved postoperatively. The authors present a case of mesenchymal chondrosarcoma with review of literature.
Primary Spinal Dumbbell-Shaped Mesenchymal Chondrosarcoma Located Intradurally and Extradurally
Bae, Gyu-Seong,Choi, Seung-Won,Youm, Jin-Young,Kim, Seon-Hwan The Korean Neurosurgical Society 2011 Journal of Korean neurosurgical society Vol.50 No.5
Mesenchymal chondrosarcomas are rare malignant tumors of the bone and soft tissue. Spinal mesenchymal chondrosarcomas are even rarer and, to the best of our knowledge those that are concomitantly located in the intradural and extradural regions, have never been reported. We report a case of a 25-year-old man with back pain and bilateral progressive weakness of the lower extremities. Magnetic resonance imaging revealed a markedly enhanced dumbbell-shaped mass at the T7 level. The lesion was intradurally located at the left side of the spinal cord, and extended extradurally to the extraforminal space through the T7-8 intervertebral foramen. The tumor was completely excised through a posterior approach. Microscopic examination and immunohistochemical studies confirmed mesenchymal chondrosarcoma. Postoperative radiation therapy and chemotherapy were also performed to prevent local recurrence and metastasis. The patient has been symptom-free for two years after surgery. Herein, we reviewed and discussed the clinical characteristics, treatments, and outcomes of primary intraspinal mesenchymal chondrosarcomas in the literature.
간엽성 연골육종 : 3례 보고 3 Cases Report
구미진,최준혁,김미진,최원희,신덕섭,서장수,배영경 영남대학교 의과대학 2000 Yeungnam University Journal of Medicine Vol.17 No.1
저자들은 영남대학교 의과대학 부속병원에서 간엽성 연골육종으로 진단 받은 3례를 대상으로 임상·병리학적 특징을 분석하여 다음과 같은 결과를 얻었다. 환자의 연령은 25세에서 32세였고 평균연령은 28세였다. 종양의 평균 크기는 7.3cm였다. 조직학적으로 종괴는 이형성의 소세포로 구성된 고밀도의 부분과 분화가 좋은 초자양의 연골 조직이 섞여 있었다. 3례에서 종양 세포들은 S-100단백과 NSE에 양성이었고 desmin에 모두 음성이었다. Mesenchymal chondrosarcoma is a rare malignant tumor of skeletal and extraskeletal origin, and which shows aggressive local behavior as well as a high metastatic potential. We report 3 cases of mesenchymal chondrosarcoma. Two cases male and one was female. Their ages ranged from 25 to 32 years(mean: 28 years). Tissue was obtained by wide excision in two patients, and by incisional biopsy in one. The mass was located in the rib(case 1), orbital floor (case 2), and abdominal wall(case 3). Roentgenographically, the tumor resembles ordinary chondrosarcoma, showing osteolytic and obstructive appearance with stippled calcification. Grossly, the tumor was lobulating, solid fish-fleshy like mass with calcification and ossification. Histologically, the tumor shows characteristic bimorphic pattern composed of islands of well differentiated hyaline cartilage admixed with a cellular area of undifferentiated small cells. The small cells usually displayed a hemangiopericytoid or an alveolar pattern.
골격외 간엽성 연골육종의 세침흡인 세포학적 소견 - 1예 보고 -
정명자,오소영,강명재,이동근,최호열,김상호,Chung, Myoung-Ja,Oh, So-Yeong,Kang, Myoung-Jae,Lee, Dong-Geun,Choi, Ho-Yeul,Kim, Sang-Ho 대한세포병리학회 1997 대한세포병리학회지 Vol.8 No.2
Extraskeletal mesenchymal chondrosarcoma is a relatively rare tumor and its cytologic findings have rarely been reported. We experienced a case of mesenchymal chondrosarcoma of soft tissue of the right lateral neck diagnosed by fine needle aspiration biopsy in a 59 year-old man. Cytologic findings showed two cell components. One was an undifferentiated, small cell component with moderate amount of cytoplasm and spindle nuclei. The second population was a chondroid component. These cytologic findings were diagnostic to mesenchymal chondrosarcoma.
두개강내 뇌수막에 발생한 간엽성 연골육종 : 증례 보고 A Case Report
오창진,권익승,홍승관,문명선,신미경 대한신경외과학회 1990 Journal of Korean neurosurgical society Vol.19 No.1
Recently, the authors have experienced a case of intracranial meningeal mesenchymal chondrosarcoma. Mesenchymal chondrosarcoma is a rare tumor of the bone and soft tissue. It has been reported that the most common site of their extra-osseous origin is the central nervous system. Precise differential diagnosis should be done because of 1) its similarity to angioblastic meningioma or hemangiopericytoma in pathological aspect, 2) much more malignant tendency. We present one case of intracranial meningeal mesechymal chondrosarcoma with a brief review of the relevant literature.
Chien Ter Hsing,Sung Yong Oh,Suee Lee,권혁찬,Sung-Hyun Kim,Tae-Ho Park,Jong Soo Woo,Seo Hee Na,김효진 대한암학회 2007 Cancer Research and Treatment Vol.39 No.3
Mesenchymal chondrosarcoma is a rare cartilaginous neoplasm of an extraskeletal origin, and this predominately occurs in the head and neck, and also in the lower extremities. Fewer than twenty cases of cardiac mesenchymal chondrosarcoma have so far been reported on. For the most part, the results of treatment for patients with this condition have been dismal. In this study, we describe a case of cardiac mesenchymal chondrosarcoma that responded to chemotherapy following surgical biopsy. A 46-year-old man was referred for evaluation of his pleural effusions in both lungs. Chest computed tomography revealed an ovoid-shaped mass in the posterior wall of the patient’s left atrium. The echocardiogram revealed a large ovoid-shaped immobile mass (11×6 cm2) in the pericardiac space, which was attached tothe posterior wall of the left atrium. Emergency pericardiostomy with closure thoracostomy was performed. Seven days later, a thoracotomy was performed for reduction and diagnosis of the cardiac mass. The pathological diagnosis was extraskeletal mesenchymal chondrosarcoma of the heart.. Postoperative chemotherapy was performed for the huge remaining mass with a combined regimen of etoposide, ifosfamide and cisplatin. After 6 cycles, the patient showed a partial response without symptoms. Although cardiac mesenchymal chondrosarcoma has been reported to be chemotherapy- resistant with a short survival duration, chemotherapy may prove to be an effective treatment modality. (Cancer Res Treat. 2007;39:131-133)
A rare case of primary ovarian mesenchymal chondrosarcoma in pregnancy
Sepideh Azizi,Elena Ghotbi,Setare Nassiri The Korean Society for Reproductive Medicine 2022 Clinical and Experimental Reproductive Medicine Vol.49 No.4
Mesenchymal chondrosarcoma is a rare tumor that is more common in young people; it is an uncommon type of chondrosarcoma with a poor prognosis. In two-thirds of cases, it affects the bone, especially the spine. However, parts of the body other than the skeletal system are occasionally involved. These rarer types have a worse prognosis, with a high likelihood of metastasis and death. Due to the possible misdiagnosis of mesenchymal chondrosarcoma, the integrated use of imaging, immunohistochemistry, and pathology can be helpful.