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오용열(Yong Leul Oh),김현일(Hyun Il Kim),엄민섭(Min Sub Um),권한진(Han Jin Kwon),조호(Ho Cho),조욱현(Wook Hyun Cho),박정식(Jeong Sik Park) 대한내과학회 2000 대한내과학회지 Vol.59 No.5
Authors report two cases of hypothermic patients with Osborne's J wave on electrocardiogram. A 46-year-old male with liver cirrhosis was brought to the emergency room by ambulance due to comatous mental status. On exammination, the body temperature was below 35 ℃. By rewarming using warm normal saline intravenous infusion and hot pack application on the chest, his body temperature rose up to 36 ℃ and regained consciousness. Later, he expired with afterdrop phenomenon. Another 41-year-old stuporous quadriplegic male with post-traumatic cerebral palsy was brought to the emergency room by his family complaining weakness and vomiting. On exammination, the body temperature was below 35℃. He was rewarmed using warm normal saline intravenous infusion and hot pack application on the chest. However, he could not regain his normal body temperature and expired due to irreversible shock.(Korean J Med 59:561-564, 2000)
Case Reports : A Case of Primary Adenosquamous Carcinoma of the Liver Presented with Liver Abscess
Oh Sang Kwon,Hong Sik Lee,Dong Wook Koh,Young Jig Cho,Yeon Ho Park,Dong Kyu Park,Yong Leul Oh,Jae Hong Seo,Hoon Jai Chun,Sun Ho Um,Sang Woo Lee,Jai Hyun Choi,Chang Duck Kim,Ho Sang Ryu 대한내과학회 2001 The Korean Journal of Internal Medicine Vol.16 No.4
Primary adenosquamous carcinoma of the liver is a very rare type of cholangiocarcinoma and is defined as a cancer containing both squamous and adenomatous components in the same lesion. Recently, we experienced a primary adenosquamous carcinoma of the live
증례 / 일란성 쌍생아에서 발견된 편측성 폐 발육부전 ( hypoplasis ) 및 무발생 ( agenesis ) 각 1예
오성주(Seung Joo Oh),김현일,엄민섭,오용열(Yong Leul Oh),권한진(Han Jin Kwon),조호(Ho Cho),김수길(Soo Gil Kim),김휘정(Hui Jung Kim),원동준(Dong Jun Won),박정식(Jung Sik Park),김인재(In Jae Kim),정석태(Seok Tae Jeong) 대한내과학회 1999 대한내과학회지 Vol.56 No.3
Unilateral developmental deficiency of lung is rare. As the most of those, unilateral agenesis or Scimitar syndrome(hypogenetic lung syndrome) had been reported. We experienced that two cases of unilateral developmental deficiency of lung, which is different form each other, are found in identical twin. To our knowledge, this condition has not been reported before. We evaluated lung parenchyma and bronchus(; simple chest PA, chest CT(HRCT, 3DCT)), vasculatures(; pulmonary angiography and cardiac catheterization) and combined anomalies (;abdominal ultrasound, echocardiography, routine blood chemistry, and chromosomal study). This 31 yrs old twin female patient was confirmed as an unilateral agenesis of left upper lobe and hypoplasia of left lower lobe without combined anomalies. She's twin younger sister was confirmed as unilateral agenesis of right lung with atrial septal defect(ASD).
물두꺼비 ( Bufo stejnegeri Schmidt ) 섭취에 의한 digoxin - like immunoreactive substance ( DLIS ) 중독증
곽현철(Hyun Cheol Kwak),오용렬(Yong Leul Oh),권한진(Han Jin Kwon),오성주(Seong Joo Oh),김수길(Soo Gil Yoo),김광석(Kwang Seok Kim),유해진(Hae Jin Yoo),원동준(Dong Jun Won),박정식(Jeong Sik Park) 대한내과학회 1998 대한내과학회지 Vol.54 No.4
Everybody knows that toads are not eatable because of their toxins. But water toads are very similar to frogs morphologically, so fried water toads are eaten by some people on occasion. It has been studied that the granular glands of the toads secrete toxins known as digoxin-like immunoreactive substances (DIJS) such as bufogenins and bufotoxins. DLIS have cross-reactivity with micro- particle enzyme immunoassay for the quantitative measurement of digoxin. We report a case of DLIS poisoning in 56-year-old male patient who showed vomiting, syncope, and marked bradyarrhythmia with block (heart rate down to 29 beats per minute) after ingestion of the fried water toads (Bufo stejnegeri Schmidt).
Crystal structure of a clip-domain serine protease and functional roles of the clip domains
Piao, Shunfu,Song, Young-Lan,Kim, Jung Hyun,Park, Sam Yong,Park, Ji Won,Lee, Bok Leul,Oh, Byung-Ha,Ha, Nam-Chul Wiley (John WileySons) 2005 The EMBO journal Vol.24 No.24
<P>Clip-domain serine proteases (SPs) are the essential components of extracellular signaling cascades in various biological processes, especially in embryonic development and the innate immune responses of invertebrates. They consist of a chymotrypsin-like SP domain and one or two clip domains at the N-terminus. Prophenoloxidase-activating factor (PPAF)-II, which belongs to the noncatalytic clip-domain SP family, is indispensable for the generation of the active phenoloxidase leading to melanization, a major defense mechanism of insects. Here, the crystal structure of PPAF-II reveals that the clip domain adopts a novel fold containing a central cleft, which is distinct from the structures of defensins with a similar arrangement of cysteine residues. Ensuing studies demonstrated that PPAF-II forms a homo-oligomer upon cleavage by the upstream protease and that the clip domain of PPAF-II functions as a module for binding phenoloxidase through the central cleft, while the clip domain of a catalytically active easter-type SP plays an essential role in the rapid activation of its protease domain.</P>
위 간질종양의 기원 및 분화에 관한 연구 - 면역조직화학적 방법을 중심으로 -
박동규(Dong Kyu Park),전훈재(Hoon Jai Chun),천황래(Hwang Rae Chun),박재홍(Jae Hong Park),오용열(Yong Leul Oh),박철희(Chul Hee Park),진윤태(Yoon Tae Jin),이홍식(Hong Sik Lee),이상우(Sang Woo Lee),엄순호(Soon Ho Um),최재현(Jai Hyun Cho 대한내과학회 2002 대한내과학회지 Vol.63 No.1
Background: Gastrointestinal stromal tumors (GISTs) have the subject of debate and controversy regarding their histogenesis, criteria on malignancy, prognostic features, site-specificity and their nomenclature. These tumors have various phenotypical features and are generally divided into (1) tumors showing differentiation toward smooth muscle cells (2) tumors showing apparent differentiation toward neural elements (3) tumors showing dual differentiation toward smooth muscle and neural elements (4) tumors lacking differentiation toward either cell type (uncommitted type). This study was performed to identify the possible origin and differentiation of gastric stromal tumor. Methods: This study was performed on 38 patients who had gastric stromal tumors on endoscopy or endoscopic ultrasonography and confirmed by endoscopic or surgical resection between January 1994 and June 1999 at Department of Internal Medicine, Korea University College of Medicine. Formalin-fixed, paraffin-embedded tissues were studied by immunohistochemical method for detecting the presence of CD 34, CD 117, Vimentin, SMA, Desmin, S-100, PGP 9.5 and NSE. Results: The patients' age ranged from 26 to 81 years old, with an average age of 53.8 years. The male to female ratio was 1:1.2. Endoscopic resections were performed on 22 patients and surgical operations on 16 patients. The average tumor size was 25.3 mm in diameter. On immunohistochemical staining method, the uncommitted type was found in 18 patients (47.4%), of which 17 patients (94.4%) were CD117 (+), CD34 (+), Vimentin (+), 12 patients (31.6%) had muscular differentiation, 7 patients (18.4%) showed neural differentiation and 1 patient (2.6%) showed differentiation toward both neural and muscular immunohistochemical pattern. Conclusion: Gastric stromal tumors showed phenotypical diversity in immunohistochemical staining suggesting different histogenesis. Most uncommitted type had a phenotype of intersititial cells of Cajal (ICC) and this evidence supports the hypothesis that uncommitted type has the origin of ICC.(Korean J Med 63:14-22, 2002)