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광범위 전신성 경화증 환자에서 D-penicillamine 치료 중에 발생한 중증 근무력증
박도현 ( Do Hyun Park ),이은영 ( Eun Young Lee ),안만수 ( Man Su Ahn ),김인 ( In Kim ),정선미 ( Son Mi Chung ),신정현 ( Jung Hyun Shin ),이창근 ( Chang Keun Lee ),조유숙 ( You Sook Cho ),유빈 ( Bin Yoo ),김광국 ( Kwang Kuk Kim ) 대한류마티스학회 2002 대한류마티스학회지 Vol.9 No.2
D-penicillamine has been used to reduce skin thickening and prevent the development of significant organ involvement in the treatment of scleroderma. This drug has a number of serious adverse reactions including glomerulonephritis with nephrotic syndrome, aplastic anemia, thrombocytopenia, and myasthenia gravis. A 44-year-old woman was admitted for weakness of the extremity muscle during repeated use. Eight months before admission, she visited dermatology department of our hospital. She was diagnosed as having scleroderma. D-penicillamine was started for the treatment of skin lesions. Based on the fluctuation of proximal muscle weakness, high titer of acetylcholine receptor antibody and definite decremental response of Jolly test, she was diagnosed as myasthenia gravis. D-penicillamine was discontinued because of the suspicion of D-penicillamine induced myasthenia gravis. Muscle weakness improved after D-penicillamine was withdrawn. The development of reversible myasthenia gravis may be regarded as a part of general predisposition for autoimmune disease related to the D-penicillamine therapy.
주현빈(Hyun Bin Ju),정도운(Do-Un Jung),김성진(Sung Jin Kim),김현정(Hyun Jung Kim),박재홍(Jae Hong Park),서영수(Young Soo Seo),문정준(Jung Joon Moon),전동욱(Dong Wook Jeon),김유나(You Na Kim) 대한노인정신의학회 2017 노인정신의학 Vol.21 No.2
Objective:With the burgeoning elderly population, mental health among the elderly has surfaced as an important medical, social, and economic issue. This study was a pilot study testing the assessment module that was developed to survey mental health among the elderly living in the city of Busan. Methods:Basic demographic data and mental health problems were investigated using the General Health Questionnaire-12 (GHQ-12), suicide risk screening tool, subjective memory deterioration scale, sleep disorder and sleep pattern scale, health-related quality of life scale (EuroQoL-5 dimension), and alcohol abuse screening tool (Cut down, Annoyed, Guilty, Eye-opener Questionnaire). Results:Four-hundred adults aged 65 years or older living in either of two districts in the Busan metropolitan city participated in the study, of whom 219 (54.8%) were female. About 26.8% of the participants were obese, while 2.3% were underweight. One hundred and twenty-five (31.3%) participants were in need of attention to or improvement of nutrition management, and 19.1% perceived themselves to be in poor health. In the GHQ-12, 68.8% were in psychological distress (≥2). About 49.8% of the participants had insomnia, 61.8% had subjective memory disturbance, and 6% were at risk of suicide. The GHQ-12 score, proportion of participants with sleep disturbance, and subjective memory deterioration was significantly higher among women than in men, while health-related quality of life was higher in men. Conclusion:A considerable number of older adults living in the Busan region were suffering from psychological stress, were in need of nutrition management, had low quality of life, and had poor mental health, and women were particularly more vulnerable
( Do Young Chung ),( Su Bin Lee ),( Gi Sun Lee ),( Hyun Jung Lee ),( Yoon Soon Lee ) 대한산부인과학회 2019 대한산부인과학회 학술대회 Vol.105 No.-
Objective: Serum antimullerian hormone (sAMH) is regarded as a useful marker in predicting for ovarian functional reserve. The purpose of presented study is to evaluate whether there is difference in postoperative change of ovarian reserve between robotic assisted ovarian cystectomy and laparoscopic approach in patients with ovarian endometrioma as comparing sAMH level recovery. Methods: The perioperative outcomes in 94 patients with ovarian endometrioma who underwent robotic-assisted (n=40) or laparoscopic (n=54) cystectomy were compared retrospectively. The sAMH levels were measured by enzyme immunoassay preoperatively and at 3 month and 6 month after surgery. The difference and ratio of sAMH levels between preoperative and 3 months, 6 months after cystectomy were compared between robotic-assisted and laparoscopic approach for predicting which method is better for preserving ovarian function. Results: Serum AMH levels were obviously decreased at 3 months after the surgery (ratio of sAMH levels between preoperative and 3 months, 0.49 ± 0.46 versus 0.52 ± 0.28 ng/mL, mean ± standard deviation) in both group. Although there was no difference in unilateral ovarian cystectomy of endometrioma, the recovery of sAMH level at 6 months (ratio of 6 months sAMH to preoperative sAMH level) after cystectomy was higher in robotic assisted approach than those of laparoscopic surgery (0.40 ± 0.24 versus 0.21 ± 0.23, p=0.009) in bilateral endometrioma. In multivariate linear regression analysis, the coefficient of robot surgery was 0.442 (p=0.028). Conclusion: In our study, the robotic-assisted cystectomy for bilateral ovarian endometrioma has higher preservation than laparoscopic approach. The robotic-assisted approach is feasible for preserving surgery of ovarian function in patients with bilateral ovarian endometrioma.
( Do Young Chung ),( Su Bin Lee ),( Hyun Jung Lee ),( Yoon Hee Lee ),( Gun Oh Chong ),( Dae Gy Hong ),( Yoon Soon Lee ) 대한산부인과학회 2019 대한산부인과학회 학술대회 Vol.105 No.-
Objective: A high pretreatment neutrophil-to-lymphocyte ratio (NLR) are recognized as associating with poor prognosis in patients with various cancers including cervical cancer. We evaluated the clinical implication of pre- and post-treatment hematologic parameters as a prognostic factor in patents with locally advanced cervical cancer (LACC) who received primary concurrent chemoradiotherapy (CCRT). Methods: We retrospectively analyzed 125 patients with LACC (FIGO stage IIb to IIIb) who received definitive CCRT. Clinical factors and hematologic parameters including NLR were assessed at pre and post CCRT. Univariate and multivariate analysis for disease-free survival (DFS) and overall survival (OS) were performed using clinicopathologic and hematologic parameters. Results: On multivariate analysis, post-treatment NLR (hazard ratio HR, 3.643; 95% confidence interval CI, 1.701-7.802; p=0.0009), ΔNLR (pretreatment NLR / posttreatment NLR) (HR, 3.643; 95% CI, 1.701-7.802; p=0.0009), and Δ platelet-to-lymphocyte ( pretreatment PLR/ posttreatment PLR; HR, 2.077; 95% CI, 1.044-4.133; p=0.0373) were significant prognostic factors for DFS, and only post-treatment NLR were significant prognostic factor for OS among hematologic parameters (HR, 12.639; 95% CI, 4.969-32.144; p < 0.0001). However, pretreatment hematologic parameters were not associated with prognosis. Conclusion: Post-treatment hematologic parameters, especially post-treatment NLR, may be a useful prognostic indicator in patients with locally advanced cervical cancer who were treated with definite CCRT.