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다발성골수종의 형태학적 분류 및 임상 소견에 관한 연구
김휘준,이동화,이성희 순천향의학연구소 1996 Journal of Soonchunhyang Medical Science Vol.2 No.1
1984년 1월부터 1992년 12월까지 9년간 순천향대학병원에서 다발성골수종으로 진단된 28명의 환자를 대상으로 임상 검사 소견 및 생존 기간을 분석하고, 골수천자도말에서 형질세포 분화 정도에 따른 형태학적 분류를 하고, 골수생검상 형질세포 침윤 양샹에 따른 분류를 한 후 이와 같은 분류가 임상 경과 및 예후와 어떤 관련이 있는지를 알아 보았다. 1. 골수천자도말에서 형질세포 분화 정도에 따른 분류를 하여 mature형과 immature형을 비교한 결과 진단 당시 임상 및 혈액학적 변수들간에 유의한 차이는 없었다. 2.골수생검상 형질세포 침윤 양상에 따른 분류를 하여 diffuse형과 packed형 을 비교한 결과 진단 당시 임상 및 혈액학적 변수들간에 유의한 차이는 없었다. 3. 위와 같은 분류가 예후 추정인자로서 의의가 있는지를 알아 보기 위해 평균 생존율을 구해 보았으나 유의한 차이는 없었다. 이상과 같은 결과는 본 연구의 증례가 너무 적었고, 처음 진단이 늦었으며 대부분의 환자가 고령이어서 일찍 치료를 포기한 이유로 생각되며, 추후에 더 많은 증례에 대한 연구가 계속되고 환자에 대한 교육을 실시하여 추적 관찰을 계속한다면 위와 같은 분류 방법이 다발성골수종의 예후를 추정하는데,유용한 지표로 사용될 수 있으리라 사료된다. The maturity of myeloma cells in the bone marrow aspirates and the pattern of infiltratin in the biopsy are known to be highly significant in predicting the prognosis. This study was performed to analyse clinical. hematological, and morphological features of the bone marrow smears and biopsy in multiple myeloma at the time of diagnosis and investigate the correlation between clinical and pathologic findings for the evaluation of survival rate. The subjects for the study were 28 cases of multiple myeloma from January 1984 to December 1992 diagnosed at Soonchunhayang University Hospital. There were no statistical differences between clinical parameters and cell types and pattern of infiltrating in the bone marrow. And there were no statistical differences in survival rate depending on the cell types and pattern of infiltration pattern in the bone marrow. Above findings seemed to be resulted from insufficient subjects and failure of complete follow-up study. However, if a cooperative study of the impact of morphological classification in myeloma is performed in the future, morphological classificatin of myeloma could be considered as a prognostic factor.
백창렬,이동건,최정현,정현화,조유경,박훈준,이승훈,박윤희,이교영,민우성,김춘추,신완식 대한감염학회 2001 감염 Vol.33 No.4
As a result of the enlarging pool of unvaccinated children and young adults, there has been an increase in measles in our countries. In these situation, it has been reported that measles associated pneumoinia is easily complicated with fatal respiratory failure, espycially in immunocompromised patients. Herein we report the case of lethal measles pneumonia after allogenic hematopoietic stem cell transplantation in adults proven by autopsy. Recently, one case of measles was encountered in 39-year-old female patients after allogenic bone marrow transplanted case (chronic myelogenous leukemia), who progressed into interstitial pneumonia pattern, despite treatment including antibiotics, immunoglobulin. The patient died of giant cell pneumonia compatible with that of measles which was comfirmed in the section of necropsy lung specimen. (Korean J Infect Dis 33:301∼309, 2001)
이건화 ( Gun Wha Lee ),김동균 ( Dong Kyun Kim ),나현식 ( Hyun Sik Na ),배준용 ( Jun Yong Bae ),최준호 ( Jun Ho Choi ),김양기 ( Yang Ki Kim ),김기업 ( Ki Up Kim ),어수택 ( Soo Taek Uh ),김동훈 ( Dong Hoon Kim ),황정화 ( Jung Hwa Hw 대한결핵 및 호흡기학회 2005 Tuberculosis and Respiratory Diseases Vol.58 No.1
Pulmonary sequestration is a very rare congenital malformation in which a mass of pulmonary tissue is detached from the normal lung and receives its blood supply from a systemic artery. It may be clinically asymptomatic or it has a wide spectrum of variou
이건화,김동균,나현식,배준용,최준호,김양기,김기업,어수택,김동훈,황정화,구동억,Lee, Gun-Wha,Kim, Dong-Kyun,Na, Hyun-Sik,Bae, Jun-Yong,Choi, Jun-Ho,Kim, Yang-ki,Kim, Ki-up,Uh, Soo-taek,Kim, Dong-hoon,Hwang, Jung Hwa,Goo, Dong-Erk 대한결핵및호흡기학회 2005 Tuberculosis and Respiratory Diseases Vol.58 No.1
폐격리증 치료의 고식적인 방법에는 폐엽 절제술이 있고 덜 침습적인 방법으로는 기형혈관을 동맥색전술로 폐색시키는 방법이 있다. 최근 국내에서 폐격리증을 동맥색전술만으로 치료한 증례가 있으나 모두 소아에서 치료한 경우였다. 저자들은 17세 남자 환자에서 폐격리증을 젤폼과 코일을 이용한 동맥 색전술로 특별한 합병증 없이 치료 하였고 6개월 후 흉부전산화 단층촬영으로 추적 관찰 하였기에 문헌 보고하는 바이다. Pulmonary sequestration is a very rare congenital malformation in which a mass of pulmonary tissue is detached from the normal lung and receives its blood supply from a systemic artery. It may be clinically asymptomatic or it has a wide spectrum of various clinical manifestations. The clinical therapeutic approach is to resect the sequestered lobe to prevent frequent complication such as infection. The arterial embolization of feeding artery is a new technique and a less invasive treatment than conventional surgical removal. We have experienced a 17-year-old male with pulmonary sequestration whose complaints were pain in left lower chest. He was diagnosed by computed tomography and aortography and successfully treated with embolization of feeding artery. We report a case of pulmonary sequestration treated with arterial embolization instead of surgery.
전동휘,주정화,이기찬,김성학 대한신경외과학회 1977 Journal of Korean neurosurgical society Vol.6 No.2
A case is presented in which left-sided hemiparesis was caused by a fibromuscular dysplasia of the right internal carotid artery in the neck, and is used as a basis for discussion of the angiographic features. The 24-year-old woman was admitted to our Department of Neurosurgery, Korea University hospital, with the complaints of headache and left-sided hemiparesis which developed abruptly about one month before this admission. The carotid angiography was performed by puncture of the right common carotid artery under the clinical impression of cerebral thrombosis. which showed no gross intracranial abnormalities. But the characteristic findings were observed under extracranial right internal carotid artery by demonstrating alternating zones of narrowing and widening of the arterial lumen which are so-called loose stocking appearance or 'string of beads' appearance and are the typical feature of fibromuscular dysplasia. No surgical interventions such as arterial reconstruction and grafting, or arterial dilatation with bougies were applied on the patient, and she was discharged from the hospital three days after the admission. Fibromuscular dysplasia is a rare sclerotic, noninflammatory lesion of unknown etiology involving the wall of large arteries. This disease is found most frequently in early adult life and women are afflicted more often than men. This condition has been described most often in the renal arteries, where it has been found to be a cause of hypertension. Among the involvement of carotid system, the cervical portion of the internal carotid artery is most often affected, and the involvements are often bilateral. When localized to the internal carotid arteries, it can give symtoms of intermittent or permanent cerebral ischemia, but is usually asymptomatic. The typical angiographic appearance is the main parameter for diagnosis of fibromuscular dysplasia.
전동휘,주정화,이기찬,최종구,최용일 대한신경외과학회 1976 Journal of Korean neurosurgical society Vol.5 No.2
The majority of current shunting procedures involve wither a ventriculoperitoneal or a ventriculoatrial placement. The ventriculoperitoneal placement have less serious associated morbidity than the atrial placement hut revision of the placement is occasionally requested by complications associated with the shunting procedure. A case of ventriculoperitoneal shunt complicated by ascitis and hydrothorax was reported, in which the shunting procedure was indicated for relief of hydrocephalus in an infant.
전영수,김호연,이경식,김동집,김우중,양기화 대한내과학회 1986 대한내과학회지 Vol.30 No.4
Although Sjogren's syndrome is a common disease presenting overlap syndrome, the association with scleroderma is extremly rare. Clinical and immunopathological studies have been presented in 48 year-old female patient who had suffered from dry eye, dry mouth and Raynaud's phenomenon in recent 2 years. The diagnosis of Sjogren's syndrome and scleroderma has been made on the basis of clinical symptom, laboratory findings and biopsy of lower lip and dorsal skin of the finger. The clinical symptoms of Sjogren's syndrome and Raynaud's phenomenon were significantly responded after administration of systemic steroid, calcium channel blocker and local artificial tear.
전동휘,주정화,이기찬,최호익 대한신경외과학회 1977 Journal of Korean neurosurgical society Vol.6 No.1
A teratoma is a true tumor or neoplasm composed of multiple tissue of kinds foreign to the part in which it arises. Predilection site of intracranial teratoma are the pineal body, the pituitary region and the posterior fossa in order of frequency. We have reported a case of teratoma experienced in a boy aged 12 who disclosed various clinical manifestations of right frontal lobe tumor. The teratoma was malignant histologically and located deeply in the white matter of the right posterior frontal lobe.