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Henoch-Schonlein 자반증 임상양상으로 나타나 진단이 늦어졌던 웨게너 육아종증
송세빈 ( Se Bin Song ),최혜숙 ( Hye Sook Choi ),김이형 ( Yee Hyung Kim ),최천웅 ( Cheon Woong Choi ),박명재 ( Myung Jae Park ),유지홍 ( Jee Hong Yoo ),강홍모 ( Hong Mo Kang ),김윤화 ( Yoon Hwa Kim ),박주철 ( Joo Cheol Park ) 대한결핵 및 호흡기학회 2007 Tuberculosis and Respiratory Diseases Vol.63 No.6
Wegener`s granulomatosis is a systemic vasculitis of the medium and small arteries, as well as of the venules, arterioles, and occasionally large arteries, and primarily involves the upper and lower respiratory tracts and the kidneys. Renal symptoms of Wegener`s granulomatosis are indistinguishable from those of vasculitis such as Henoch-Schonlein purpura and microscopic polyangiitis. This case, though initially diagnosed as Henoch-Schonlein purpura, was confirmed as Wegener`s granulomatosis from a lung biopsy fifteen years after the initial diagnosis. We report this case with a review of the literature. (Tuberc Respir Dis 2007;63:531-536)
송세빈 ( Se Bin Song ),문송미 ( Song Mi Moon ),조창현 ( Chang Hyun Cho ),황연희 ( Yeon Hee Hwang ),임효석 ( Hyo Seok Lim ),손준성 ( Jun Seong Son ),이미숙 ( Mi Suk Lee ) 대한내과학회 2010 대한내과학회지 Vol.78 No.3
Patients infected with human immunodeficiency virus (HIV) may develop various liver diseases, including viral hepatitis, granulomatous inflammation, malignancies, vascular disease, drug-induced hepatitis and, sometimes, diseases of unknown origin. In this case, a 35-year-old HIV-infected man presented with fatigue, myalgia, elevated liver enzymes, and multiple skin lesions for 3 months. Since the abdominal computed tomography (CT) and viral marker tests failed to explain the cause of his symptoms and signs, a liver biopsy was performed. This revealed a granuloma consisting of epithelioid cells without necrosis. His symptoms, skin lesions, and abnormal liver enzymes improved without changing his management, including the anti-retroviral agents. He was diagnosed with idiopathic granulomatous hepatitis based on the pathologic findings of the liver and clinical course. Aggressive diagnostic methods, such as a liver biopsy, should be considered for HIV-infected patients with liver disease. (Korean J Med 78:391-395, 2010)
송세빈 ( Se Bin Song ),김양균 ( Yang Gyun Kim ),이설라 ( Sul Ra Lee ),이동영 ( Dong Young Lee ),정경환 ( Kyung Hwan Jeong ),문주영 ( Ju Young Moon ),이상호 ( Sang Ho Lee ),임천규 ( Chun Gyoo Ihm ),이태원 ( Tae Won Lee ) 대한신장학회 2010 Kidney Research and Clinical Practice Vol.29 No.5
목적: 경동맥의 내막-중간막 두께(carotid artery-intima-media thickness, cIMT)는 혈액 및 복막 투석을 받고 있는 만성 신부전 환자에서 심혈관 질환과 관련된 사망의 예측인자임은 이미 알려져 있으나 투석 전 만성신질환 환자에 대한 연구 결과는 부족하였다. 이에 만성신질환 환자들의 신기능 단계에 따른 경동맥의 내막-중간막 두께 변화를 확인하고자 본 연구를 계획하였다. 방법: 2005년 1월1일부터 2009년4월30일까지 경희대학교 부속병원에 내원한 사구체 여과율 60 ml/min/1.73m2 미만의 만성신질환 환자 중 고해상도 B모드 경동맥 초음파를 시행한 환자 88명 (남:여=49:39)을 대상으로 정상 신기능의 대조군 30명 (남:여=13:17)과 경동맥 내막-중간막 두께를 비교하였다. 결과: 경동맥의 평균 내막-중간막 두께는 사구체여과율의 감소에 따른 만성신질환의 단계가 증가될수록 통계적으로 유의하게 증가하였는데 그 두께는 만성신질환 단계가 3, 4, 5단계로 악화되면서 각각 0.82±0.19 mm, 0.93±0.13 mm, 그리고 1.04±0.27 mm로 증가하였다. 또한 정상 성인과 비교하여 모든 만성신질환 단계에서 경동맥 내막-중간막 두께가 통계적으로 유의하게 증가된 상태임을 확인하였다. (p=0.002). 당뇨성 신질환의 경우 비당뇨성 신질환에 비해 그 두께는 증가하였으나 통계적으로 유의하지 않았다. (0.96±0.32 vs. 0.92±0.20, p=0.142). 다중회귀분석에서는 나이와 사구체여과율, 만성신질환 단계가 경동맥 내막-중간막 두께와 유의한 상관성을 보였다. 결론: 만성신질환 환자에서 투석전 초기 신기능 저하 단계에서부터, 경동맥의 동맥경화는 진행되어 있었으며 경동맥의 내막-중간막 두께는 나이 및 사구체여과율 만성신질환 단계와 상관관계가 있었다. Purpose: Carotid artery intima-media thickness (cIMT) has been reported as the predictive factor of mortality of cardiovascular disease in dialysis patients but only a few reports are available on the patients with earlier stages. We compared cIMT according to the stage of chronic kidney disease, and analyzed the data in association with cardiovascular risk factors. Methods: Study subjects were 88 patients with chronic kidney disease less than 60 ml/min/1.73m2 of glomerular filtration rate. cIMT was measured by means of high- resolution B-mode ultrasonography. Cardiovascular risk factors and cIMT were analyzed and compared with 30 subjects with normal renal function. Results: cIMT was significantly increased with the stage of chronic kidney disease. When the stage was increased from 3 to 5, cIMT was increased (p=002). cIMT was further increased in all stages of chronic kidney disease than in patients with normal kidney function. But association of diabetic chronic kidney disease with non-diabetic chronic kidney disease was not significant (p=0.127). Multiple regression analysis showed that cIMT in patients with chronic kidney disease was significantly correlated to age, glomerular filtration rate, and the stage of chronic kidney disease. Conclusion: We suggest that carotid atherosclerosis could increase in no dialysis patients with early stage of chronic kidney disease. Carotid artery intima-media thickness was correlated with age, glomerular filtration rate, and the stage of chronic kidney disease.
이설라 ( Sul Ra Lee ),송세빈 ( Se Bin Song ),최소영 ( So Young Choi ),정경환 ( Kyung Hwan Jung ),이태원 ( Tae Won Lee ),임천규 ( Chun Kyu Lim ) 대한신장학회 2010 Kidney Research and Clinical Practice Vol.29 No.2
Purpose: This study was aimed at finding clinical factors to be associated with a progressive course of IgA nephropathy. Methods: We investigated the association between the prognosis of IgA nephropathy and clinical and laboratory findings including age, sex, hypertension, diabetes mellitus, 24-hour urine protein, macroscopic hematuria, hematuria duration, serum uric acid, serum creatinine, GFR, upper respiratory infection, pathological observation, and treatment protocols. One hundred seventy seven patients were followed up for more than 2 years at Kyung Hee university medical center from January 1997 through December 2006. Kidney size and echogenicity were measured by abdominal ultrasonography. Resistive index was calculated by doppler ultrasonography. Results: Long hematuria duration, increased uric acid, elevated creatinine of chronic renal failure group were distinguished from those of normal and acute renal failure group statistically. Using multivariate analysis, three factors, elevated serum uric acid, decreased GFR, ACE inhibitor or ARB and steroid combination treatment proved to be independent prognostic indicators of acute renal failure of IgA nephropathy. Heavy proteinuria, long hematuria duration, and severe histopathologic findings by Haas` classification were associated with significant risk factors for developing chronic renal failure. Conclusion: At diagnosis of IgA nephropathy, hematuria continuation and histological damage in Haas` classification were related with the reduction of renal function.