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K - Light Chain Myeloma 에 병발된 성인형 Fanconi 증후군 1 예
김용태(Yong Tae Kim),조진아(Jin A Cho),박찬문(Chan Mun Park),이선화(Sun Hwa Lee),임창훈(Chang Hoon Yim),김은주(Eun Ju Kim),민용기(Yong Ki Min),조동희(Dong Hee Cho),권소영(So Yeong Kwon) 대한내과학회 1995 대한내과학회지 Vol.48 No.3
Adult Fanconi syndrome is a very rare disease characterized by renal glycosuria, generalized aminoaciduria, hypophosphatemia, renal tubular acidosis and hypouricemia due to renal tubular transport defect. It is divided into inherited and acquired forms. Acquired Fanconi syndrome may result from nephrotic syndrome, renal transplantation, multiple myeloma, dysproteinemia, and heavy metal poisoning. A 59-year-old woman was admitted because of severe lower back pain and generalized weakness for the last 5 months. The hemoglobin, leukocyte count, platelet count and, ESR were 7.5 g/dl, 3,080/㎣, 87,000/㎣, and 17mm/hr. The urinalysis showed 3 positive for glucose in spite of normal blood glucose level. The serum creatinine, calcium, phosphate and uric acid were 1.7 mg/dl, 7.2 mg/dl, 1.9 mg/dl, and 1.4 mg/dl. In ABGA, pH was 7.303 and bicarbonate was 14.0 mM/L. k-Light chain myeloma was diagnosed on basis of the presence of immature plasma cells (18.6%) in bone marrow and k -light chain type Bence-Jones protein in serumand urine immunoelectrophoresis. The patient had hypophosphatemic os4eomalacia in the absence of hyperparathyroidism. We are reporting a case of Adult Fanconi syndrome in k-light chain myeloma with brief review of literature.
영양막 질환 환장에서의 혈청 β - HCG 치 및 24 시간 소변의 HCG 양과 갑상선 기능과의 관계
김용태(Yong Tae Kim),조진아(Jin A Cho),박찬문(Chan Mun Park),이선화(Sun Hwa Lee),정호연(Ho Yeon Chung),한인권(In Kwon Han),민현기(Hun Ki Min) 대한내과학회 1996 대한내과학회지 Vol.51 No.2
Objectives: It has been recognized that hyperthyroidism occur in patients with trophoblastic disease, either hydatidiform moles or choriocarcinoma. Recently, several lines of evidence have shown that human chorionic gonadotropin, secreted by the trophoblastic disease, is a thyroid stimulator and cause hyperthyroidism. The study was undertaken to evaluate the incidence of hyperthyoidism in patients with trophoblastic disease and relationship between level of thyroid hormone and human chorionic gonadotropin. Methods: In 51 patients with hydatidiform mole and 13 patients with choriocarcinoma, we measured level of thyroid hormone, serum β -HCG and amount of urinary excretion of HCG. Results: 1) Hyperthyroidism was observed in 19.6% of the patients with hydatidiform mole and in 7,6% of the patients with choriocarcinoma. 2) The level of serum β -HCG and the amount of 24 hour urinary excretion of HCG in patients with hyperthyroidism were more than that in euthyroid patients, 3) The amount of 24 hour urinary excretion of HCG in patients with hydatidiform mole was more than that in choriocarcinoma patients. 4) The level of serum β -HCG and the amount of 24 hour urinary excretion of HCG had significant correlation with serum T3 and T4 levels, but, the level of serum β -HCG had beteer correlation. Conclusion: The occurrence of hyperthyroidism is more frequent in patients with trophoblastic disease, and the degree of thyroid function is related with the level of serum B -HCG and urinary excretion of HCG, but, more closely related with serum β -HCG level.
박찬문 전남사학회 2002 역사학연구 Vol.19 No.-
Erasmus convined of a man's salvation due to his faith in Christ. But he laid emphasis on a man's spiritual, moral efforts after his salvation. He says this much. Therefore, my brother, do not progress slowly by dint of reluctant effort, but by moderate exercice arrive at quick and vigorous adulthood in Chtist. If you will attempt to rise to the limit o( your powers from the body to the spirit, from the visible to the invisible, from the letter to the mystery, from sensible things to intelligible things, from composite things to simple things. He will obligingly come forth to meet you from his inaccessible light and unimagined silence. His soteriology shows moral characters intensely, but his moralism was not simply 'this-worldly' and based on Christo-centrism. His Christo-centrism, as Payne said, had to do primarily with Christ as a teacher and model, but also secondarily with Christ as a Redeemer. His pietas was essentially personal, but had a quality oriented social, communal transformations.