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모성환,박관응,김창욱,김미자,정회상,박유환,정춘해,이호영,이호준 朝鮮大學校 附設 醫學硏究所 1996 The Medical Journal of Chosun University Vol.21 No.2
Miliary tuberculosis is commonly associated with various hematologic changes, such as, anemia, leukopenia, leukocytosis, monocytosis, leukemoid reaction, basophilia, dissemianted intravascular coagulation, and rarely pancytopenia. Pancytopenia in miliary tuberculosis has proved to be a grave prognostic indicator. The precise mechanism of pancytopenia in miliary tuberculosis is not yet known, so there is still much controversy. Bone marrow invasion is accepted as one of the possible mechanisms of pancytopenia acompanied with miliary tuberculosis. Authors experienced a rare case of pancytopenia and bone marrow invasion associated with miliary tuberculosis in a 47-year-o1d female. The bone marrow examination revealed caseous granulomas with a reactive plasmacytosis. The pancytopenia and symptoms were resolved by anti-tuberculosis chemotherapy and active supportive care. Tuberculosis os a common infection. Therefore, in the presence of pancytopenia, accompanied with pyrexia, milliary tuberculosis should always be considered.
박치영,모성환,문철호,곽재정,김태종,전용준,박유환,정춘해 朝鮮大學校 附設 醫學硏究所 1995 The Medical Journal of Chosun University Vol.20 No.2
von Willebrand's disease (vWD) is the most common autosomal-dominant inherited disorder resulting from a quantitative or a qualitative defect of von Willebrand factor (vWF). The most diagnostic pattern is the combination of a prolonged bleeding time, a reduction in plasma vWF concentration, a parallel reduction in ristocetin cofactor activity, and reduced factor Ⅷ activity, In this case, ristocetin-induced platelet aggregation data were compatible with that of vWD. Bleeding times were prolonged over 4 minutes, vWF antigen levels were 45%. vWF ristocetin cofactor activities were 0~1% and factor Ⅷ levels were 31%, when compared to the normal control. We report the case of a family with vWD. characterized by a quantitative defect in vWF
과도한 운동으로 발생한 횡문근융해증에 의한 급성신부전증 1예
문철호,류보열,모성환,김태종,기장도,박용관,김용환,정종훈 조선대학교 1995 The Medical Journal of Chosun University Vol.20 No.1
Rhabdomyolysis may be defined as a clinical and laboratory syndrome which releases muscle cell contents into the plasma, such as creatine phosphokinase, due to skeletal muscle injuries. It can be the result of many diverse causes including muscle disease, ischemia, genetic disorder, metabolic disorder, infectious disease, drugs, comatose state, trauma or vigorous exercise that can lead to acute renal failure as a complication. Since first reported in 1941, rhabdomyolysis-induced acute renal failure has been documented many times, and the major causes of this disease are carbon monoxide poisoning, snake bites, and etc in Korea Reports of acute renal failure after exercise-related rhabdomyolysis with myoglobinemia are rare. We report a case of acute renal failure caused by exercise-related rhabdomyolysis in a 20 year old man.
기장도,박치영,류보열,김태종,모성환,곽재정,문철호,박근홍,박유환,정춘해 朝鮮大學校 附設 醫學硏究所 1996 The Medical Journal of Chosun University Vol.21 No.1
Chronic neutrophilic leukemia is a very rare myeloproliferative disorder which is characterized by severe sustained mature neutrophilic leukocytosis in peripheral blood (PB), hepatosplenomegaly, elevated leukocyte alkaline phosphatase, serum uric acid. serun viatmin B 12 and the bleeding tendency despite normal platelet count and coagulation time, absence of philadelphia chromosome, and the absence of fever or underlying infection or disease sufficient to mimic a leukemoid reaction. We have experienced a 34-years-old male patient with atypical chronic neutrophilic leukemia. On admission, the leukocyte count was 56,860/uL. severe neutrophic leukocytosis with 76% neutrophils and rare immature forms on PB smear. Many neutrophils had toxic granules, and vacuoloes. Leukocyte alkaline phosphatase score was decreased. The cytogenetic study showed Philadelphia chromosome negative with normal karyotype.
담관 폐쇄에 의한 백서간의 형태학적변화와 항산화효소 생성량과의 관계
박찬국,김명철,김창욱,김만우,유기동,김영학,이만재,모성환,기근홍 대한소화기학회 1998 대한소화기학회지 Vol.31 No.2
Background/Aims: Obstructive cholestasis has been known to cause heaptic injury, resulting in morphological change in the liver. Rats with biliary obstruction may be believed to be susceptible to oxidative stress and free radical related liver injury by the infiltration of inflammatory cells. Using biliary obstruction in rats, we studied the relationships between morphologic changes and the levels of antioxidant enzymes. Methods: The proximal portion of the common bile duct of Sprague-Dawley rats were ligated with silk. We observed morphological changes, estimated the antioxidant enzymes within the liver tissue, and assayed aspartate aminotransferase, total bilirubin, and alkaline phosphatase within serum at every week for 4 weeks. Results: After biliary obstruction, the activities of superoxide dismutase, catalase, and glutathione peroxidase gradually increased in rat liver. Histologically, proliferation of bile ductules and fibrosis developed 3 to 4 weeks later after ligation of common bile duct. Hepatic lobular destruction and severe portal triaditis were noted 2 weeks later. Conclusions: Due to the increased activities of the antioxidant enzymes after biliary obstruction, it is believed that the oxygen free radicals play an important role in hepatic injury by cholestasis in rats, and that morphological changes may partially result from the release of oxygen free radicals by the inflammatory cells.
탐측자 심첨부 회전법에 의한 좌심방이 관찰에 대한 연구
정재용(Jae Yong Chung),장경식(Kyoung Sig Chang),류보열(Bo Yeol Ryu),모성환(Sung Whan Mo),김태종(Tae Jong Kim),문철호(Chel Ho Moon),진영기(Young Kei Chin),박유환(Yoo Whan Park),이승일(Seung Il Lee),홍순표(Soon Pyo Hong) 대한내과학회 1997 대한내과학회지 Vol.52 No.6
Objectives: Visualization of the left atrial appendage(LAA) by the transesophageal echocardiography(TEE) is excellent, but it is difficult to visualize the LAA by the modified parasternal short-axis view(MPSA) in transthoracic echocardiography(TTE). We studied to determine the usefulness of the apical horizontal view(AHV) abtained by the apical rotation method of the transducer for the detection of the LAA. Methods: We studied the MPSA and AHV in 602 patients, The LAA was observed during diastole of the LAA. We obtained an apical horizontal view by 45 degree clockwise rotation of the transducer from the apical 2 chamber view and compared with the visualization of the LAA in AHV and MPSA. Results: Among 602 patients, LAA could not be visualized in 88(14.6%) because of a poor echo-window. LAA was more clearly visualized in 222 patients by the AHV than the MPSA and 56 patients by the MPSA than the AHV. LAA was same degree visualization in patients by the AHV and MPSA. In male and female, more than 55 ages and less than 55 ages, visualization of inner margin of the LAA by the AHV was more clear than by the MPSA. Conclusion: The AHV was a useful, noninvasive and reproducible method for the visualization of the LAA.