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Huge Aneurysm of the Sinus of Valsalva Compressing the Left Atrium
김기훈,양태현,한양천,조환진,엄수정,설상훈,김성만,김대경,김두일,김동수 한국심초음파학회 2008 Journal of Cardiovascular Imaging (J Cardiovasc Im Vol.16 No.4
Sinus of Valsalva aneurysms are rare cardiac anomalies. They can be congenital or acquired, and mainly involve the right or non-coronary sinuses. Unruptured aneurysms are usually asymptomatic unless they compress other structures or produce thrombi. A sinus of Valsalva aneurysm can also produce myocardial infarction through thrombus formation secondary to the turbulent flow in the Valsalva aneurysm. We report a case of a huge sinus of Valsalva aneurysm involving the noncoronary sinus, which was diagnosed as the presumed source of acute myocardial infarction. Sinus of Valsalva aneurysms are rare cardiac anomalies. They can be congenital or acquired, and mainly involve the right or non-coronary sinuses. Unruptured aneurysms are usually asymptomatic unless they compress other structures or produce thrombi. A sinus of Valsalva aneurysm can also produce myocardial infarction through thrombus formation secondary to the turbulent flow in the Valsalva aneurysm. We report a case of a huge sinus of Valsalva aneurysm involving the noncoronary sinus, which was diagnosed as the presumed source of acute myocardial infarction.
석준호 ( Jun Ho Seok ),박종선 ( Jong Seon Park ),김영조 ( Young Jo Kim ),김기식 ( Kee Sik Kim ),허승호 ( Seung Ho Hur ),채성철 ( Shung Chul Chae ),박헌식 ( Hun Shik Park ),차광수 ( Kwang Soo Cha ),김무현 ( Mooh Hyun Kim ),김영대 ( 대한내과학회 2002 대한내과학회지 Vol.63 No.5
Background : Aneurysms of sinus Valsalva are rare anomalies thought to be primarily congenital in origin. To evaluate the clinical features and surgical results associated with ruptured aneurysm of sinus of Valsalva, we reviewed the clinical characteristics and follow up results of the patients. Methods : From January, 1991, through June 2001, 33 patients with ruptured aneurysm of sinus of Valsalva underwent surgical correction from the above five university hospitals. The patients included 24 men and 9 women, with a mean age of 32±13 years. We reviewed symptoms, physical examination findings, ECG findings, the coexistent cardiac anomalies, echocardiographic findings, surgical results in 33 patients.Results : Patterns of fistula tract were right coronary sinus-right ventricle in 24 patients (73%), noncoronary sinus- right atrium in 3 patients (9%), noncoronary sinus - right ventricle in 3 patients (9%), right coronary sinus - right atrium in 2 patients (6%) and right coronary sinus ?right ventricle and right atrium in 1 patient (3%). Combined cardiac anomalies were VSD (20 cases; 61%), ASD (1 case; 3%) and PDA (1 case; 3%). But, only 12 cases of VSD (60%) were diagnosed with preoperative transthoracic echocardiography. The aneurysmal sacs were excised in all patients and the defects were closed with a patch in 21 patients (64%) and without patch in 12 patients (36%). No recurrence was observed during follow-up periods (68±38 months) for all survivors and there was no late complications or symptoms. Conclusion : In sinus of Valsalva aneurysm patients, combined cardiac anomalies, especially VSD, are common. Careful preoperative echocardiography should be performed to detect combined anomalies. And, surgical results are excellent without recurrence.(Korean J Med 63:532-538, 2002) Key Words : Sinus of Valsalva, Aneurysm, Combined anomalies
강민웅,나명훈,유재현,임승평,이영,김시욱,김수일,정인혁 대한흉부외과학회 2007 Journal of Chest Surgery (J Chest Surg) Vol.40 No.5
배경: 대동맥 근부를 보존하는 심장수술이 점차 늘어남에 따라 대동맥 근부의 해부학적 구조에 대한 중요성 또한 증가하고 있다. 본 연구는 외과적 관점에서 필요한 대동맥 근부를 한국인 해부학 실습용 시신에서 실측하여 대동맥 근부의 진단 및 수술적 처치의 기준으로 하고자 한다. 대상 및 방법: 사인이 심혈관 질환이 아닌 시신 62구 중 대동맥 판막이 쌍엽인 1구, 기술적 오류로 대동맥 근부가 손상된 4구, 고정기간 중 변형이 심한 10구를 제외한 47예를 대상으로 하였다. 각 교련사이 간격, 대동맥동의 높이, Sinotubular junction 및 aortic annulus의 길이를 측정하여 비교하였다. 결과: 시신의 사망 나이는 평균 61.3이었으며 남성이 31, 여성이 16구였다. 각 교련사이 간격은 Right coronary sinus 20.73 2.23 mm, Non coronary sinus 19.34 2.08 mm, Left coronary sinus 18.58 2.15 mm였다. 각 대동맥동의 높이는 Right coronary sinus 20.59 2.48, Non coronary sinus 18.61 2.26 mm, Left coronary sinus 17.95 19 mm였으며, 통계 분석에서 교련사이에 길이 및 대동맥동의 높이는 Right coronary sinus가 가장 컸으며, Non coronary sinus, Left coronary sinus 순으로 나타났다. Sinotubular junction의 길이는 70.73 5.94 mm, aortic annulus는 77.94 5.63 mm였으며 Sinotubular junction의 길이, 대동맥 판륜의 길이와 대동맥 판륜에 대한 Sinotubular junction의 길이의 비를 각각 나이와 비교 분석했을 때 상관관계가 없었다(p=0.920, p=0.111, p=0.073). 대동맥 판륜과 sinotubular junction의 기울기는 2.03o에서 7.77o (평균=4.90o)였다. 결론: 각 교련 사이 간격 및 대동맥동의 높이는 non-parametric ANOVA test의 결과 Right coronary sinus, Non coronary sinus, Left coronary sinus의 순으로 유의한 크기차이를 보였다(p=0.00). Sinotubular junction의 둘레 길이는 대동맥 판륜의 길이보다 9.3% 작았고 sinotubular junction이 aortic annulus에 대해 좌후측으로 기울어져 있었다.
안정효,임창영,최석구,유원상,이윤우,김창호 인제대학교 1990 仁濟醫學 Vol.11 No.3
We report 2 cases of aneurysm of Valsalva sinus, of which, the one, aneurysm of right Valsalva sinus, was ruptured into right ventricle, the other, aneurysm of posterior Valsalva sinus, was not ruptured. The patient of aneurysm of right Valsalva sinus was 38 year old female, and complained dyspnea. Perimembranous type of ventricular septal defect was combined. Continuous murmur was heard on auscultation. The patient of aneurysm of left Valsalva sinus was 47 yr. old female, and complained dyspnea and fever. Systolic and diastolic murmur was heard. She was complicated by bacterial endocarditis of Streptococus viridans preoperatively, and died due to recurrent bacterial endocarditis with acute renal failure failure 14 day after operation.
MDCT Findings of Sinus of Valsalva Aneurysms Involving Two Coronary Sinuses: Case Report
김은미,김수영,이성윤,장우익,김창영,허감 대한영상의학회 2010 대한영상의학회지 Vol.63 No.6
A sinus of Valsalva aneurysm is relatively rare and usually involves a single sinus. We describe here the multidetector computed tomography features of a case of an unruptured sinus of Valsalva aneurysms that affected the left and noncoronary sinuses in a 51-year-old woman.
Heo, Jung Ho 고신대학교의과대학 2007 고신대학교 의과대학 학술지 Vol.22 No.1
Anomalous origin of left and right coronary arteries from a single coronary ostium in the right sinus of Valsalva is rare. Accordingly, few reports have described this anomaly. We report a case of a 70-year-old woman with left and right coronary arteries originating from the right sinus of Valsalva. Coronary anomalies are associated with increased mortality, depending on the myocardium at risk. A left main originating from the right coronary sinus is supplying a greater extent of the myocardium and is associated with both an increased incidence of symptoms and of sudden cardiac death. The possibility of such an artery anomaly should always be considered in patients with a history of chest pain or syncope.
이재원 대한흉부심장혈관외과학회 1994 Journal of Chest Surgery (J Chest Surg) Vol.27 No.7
Over the past 3.5 years, 5 cases with ruptured sinus of Valsalva were operated upon at Asan Medical Center. Four patients were congenital and 1 traumatic. Coexistent lesions included 2 subarterial VSD, 3 AR requiring procedures [2 AVR, 1 valvoplasty], 2 subaortic membranes, 1 PDA,and 1 bicuspid AV. The communication is noncoronary sinus to RA in I and fight Coronary sinus to RV in the other 4 patients. The ~rstula was repaired through the aorta whenever possible and reinforced through the right sided chamber. There are no surgical mortality and, no recurrence of rupture yet.
Anomalies of the coronary arteries originating from the right sinus of Valsalva
허정호 고신대학교(의대) 고신대학교 의과대학 학술지 2007 고신대학교 의과대학 학술지 Vol.22 No.1
Anomalous origin of left and right coronary arteries from a single coronary ostium in the right sinus of Valsalva is rare. Accordingly, few reports have described this anomaly. We report a case of a 70-year-old woman with left and right coronary arteries originating from the right sinus of Valsalva. Coronary anomalies are associated with increased mortality, depending on the myocardium at risk. A left main originating from the right coronary sinus is supplying a greater extent of the myocardium and is associated with both an increased incidence of symptoms and of sudden cardiac death. The possibility of such an artery anomaly should always be considered in patients with a history of chest pain or syncope.
Valsalva Aneurysm Filled with Thrombi Mimicking a Cardiac Tumor
Yasuharu Lee,Naoki Mori,Daisuke Nakamura,Takahiro Yoshimura,Masayuki Taniike,Nobuhiko Makino,Hiroyasu Kato,Yasuyuki Egami,Ryu Shutta,Jun Tanouchi,Yoshio Yamada,Masami Nishino 대한심장학회 2012 Korean Circulation Journal Vol.42 No.12
A Valsalva aneurysm filled with thrombi can be difficult to diagnose, because it mimics a cardiac tumor. Both cardiac magnetic resonance imaging (MRI) and transesophageal echocardiogram (TEE) were performed on a patient who showed a low-echoic mass located between the atrial septum and the non-coronary sinus. Based on MRI findings allowing tissue characterization and the accurate location of the mass and the TEE findings of an irregular surface of the mass and a partial defect in the edge of the non-coronary sinus, we diagnosed the mass as a thrombosed Valsalva aneurysm that had perforated the inter-atrial septum. The operative findings coincided with the preoperative di-agnosis. Both MRI and TEE are useful for diagnosing this condition.