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( Jae Hoon Lee ),( Ju Hyun Cho ),( Ha Yan Kwon ),( Yong Won Park ),( Young Han Kim ) 대한주산의학회 2014 Perinatology Vol.25 No.3
An umbilical vein aneurysm is rare, but appears to be associated with fetal morbidity and mortality. There are no specific guidelines for a pregnancy with umbilical vein aneurysm and the management is substantially up to the clinician. We report a case of intra-amniotic umbilical vein aneurysm prenatally diagnosed by ultrasound at 35 gestational weeks. Because the aneurysm was growing rapidly, prompt cesarean delivery was conducted. After delivery, a huge fusiform umbilical cord was noted, which was confirmed to be umbilical vein aneurysm by pathological examination. We also reviewed previous reported cases and summarized the management in prenatally detected umbilical vein aneurysms. Additionally, this case report is about one of the umbilical vein aneurysms with the largest size ever reported.
비장 종대 및 범혈구 감소증을 동반한 간외 문맥류 1 예
이현아(Hyeon A Yi),남궁은경(Eun Kyung Namgung),허경열(Kyung Yul Hur),윤석구(Suk Gu Yoon),원종호(Jong Ho Won),홍대식(Dae Sik Hong),이혜경(Hae Kyung Lee),송영식(Young Sik Song),박희숙(Hee Sook Park) 대한내과학회 1996 대한내과학회지 Vol.51 No.5
Aneurysm of the portal vein is a rare entity. Portal vein aneurysms are lesions whose etiology, clinical features, and management are not well understood. Recently we experienced a case of portal vein aneurysm which was diagnosed by ultrasonography, abdominal computed tomography and angiography. A 26-year-old woman was admitted because of palpable mass on left upper quadrant abdomen and general weakness. Physical examination revealed remarkable splenomegaly. Laboratory date yieled the following results: WBC 2,000/㎣, Hb 8.7g/dl; Hct 22.5%; platelet 32,000/㎣, PT 57%; HBs Ag(+); HBs Ab(-); HBc Ab IgG(-); HCV Ab(-). Two D and coronal view of three D abdominal computed tomography demonstrated well defined circumscribed, oval and enhancing mass in the portal vein and enhancing mass that contained thrombosis in the splenic vein. Arterial portography via splenic artery showed fusiform portal vein aneurysm and splenie vein aneurysm containing thrombosis. She has achieved clinical improvement after splenectomy.
Neonatal vitelline vein aneurysm with thrombosis
Soo-Hong Kim,Hyeong Won Yu,Hyun-Young Kim,Heui Seung Jo 대한외과학회 2015 Annals of Surgical Treatment and Research(ASRT) Vol.89 No.6
Vitelline veins are a pair of embryonic structures. The veins develop the portal vein system. Serious problems occur if the vitelline vein does not regress and becomes an aneurysm. Thrombus formation in the vitelline vein aneurysm could lead to portal vein thrombosis and portal hypertension unless promptly and correctly treated. Though vitelline vein aneurysm is an extremely rare anomaly, it rapidly progresses to portal vein thrombosis that requires prompt diagnosis and treatment. We reported a case of neonatal vitelline vein aneurysm and thrombosis that was cured by prompt operation.
Unusual Presentation of a Cervical Mass Revealed as External Jugular Venous Aneurysm
김수완,장지원,이석재 대한혈관외과학회 2016 Vascular Specialist International Vol.32 No.4
Venous aneurysms of the jugular vein are one of the rare causes of neck swelling, and primary venous aneurysms of the external jugular vein are extremely rare. A 46-year-old woman presented with a painless and suddenly growing mass in the left neck. A computed tomography angiography revealed a fusiform venous aneurysm of the external jugular vein containing intraluminal thrombus. We performed resection of the aneurysm and ligation of the external jugular vein. Removal of the aneurysm of the neck vein was necessary because venous aneurysms with thrombosis may lead to serious thrombotic complications such as pulmonary embolism.
김명신 ( Myung Sin Kim ),양혜진 ( Hye Jin Yang ),임형수 ( Hyung Soo Lim ),조정연 ( Jeong Yeon Cho ),전종관 ( Jong Kwan Jun ) 대한산부인과학회 2009 Obstetrics & Gynecology Science Vol.52 No.3
The vein of Galen aneurysm is a rare vascular malformation but it can be detected by using conventional ultrasonography and diagnosed by using power Doppler ultrasonography. The prognosis of the vein of Galen aneurysm depends on congestive heart failure caused by cerebral shunt. Embolization at proper times can provide good outcome. We report a case of spontaneous delivery at 41 weeks of gestation by a 35-year-old woman presenting with a fetal vein of Galen aneurysm is described. The vein of Galen aneurysm was prenatally diagnosed by power Doppler ultrasonography and treated postnatally by embolization. This case is a report of successful prenatal diagnosis and postnatal management of the vein of Galen aneurysm.
Variations of azygos vein: a cadaveric study with clinical relevance
Ananya Priya,Shalom Elsy Philip,Anjali Jain,Aparajita Sikka 대한해부학회 2023 Anatomy & Cell Biology Vol.56 No.4
The azygos vein can be formed as a single root, two roots, and three roots, namely lateral, intermediate and the medial roots respectively. The hemiazygos vein and the accessory hemiazygos vein are the tributaries of azygos vein rather than its left side equivalents. Its variations, especially in young persons without any relevant risk factors, may result in thromboembolic illness. This study aimed to describe the morphological and morphometric variations of azygos system of veins. The present study was conducted on thirty formalin fixed adult human cadavers by dissecting azygos vein from formation to termination and variations were noted. The azygos vein was formed by a single root in 56.7%, by two roots: the lateral root and intermediate root in 36.7% cases and by the lateral root and medial root in 6.6%. The vertebral level of termination of azygos vein was seen at the level of T4 vertebrae in 70% cases, at the level of T3 vertebrae in 20% of cases and at the level of T5 vertebrae in 10% cases. The course of azygos vein was varying in 13.3%. These morphological variations can be useful while performing mediastinal surgery, mediastinoscopy, surgery of the deformations of the vertebral column, neurovascular surgeries of the retroperitoneal organs, disc herniation and fracture of thoracic vertebrae.
( Jae Min Lee ),( Jemma Ahn ),( Young Jae Hwang ),( Seung Han Kim ),( Jong Su Lee,),( Sung Jae Choi ),( Young Ho Lee ),( Jong Dae Ji ),( Gwan Gyu Song ) 대한류마티스학회 2013 대한류마티스학회지 Vol.20 No.1
Behcetsdisease is a chronic inflammatory disease characterized by oral ulcers, genital ulcers, uveitis, and skin lesions. Furthermore, Behcets disease can manifest as vascular lesions, such as, those of vasculitis, venous thrombosis, or thrombophlebitis or as an arterial aneurysm. Here, the authors report the case of a pulmonary artery aneurysm and deep vein thrombosis in a 41-year-old woman with a previous diagnosis of Behcets disease. The patient presented with hemoptysis and a cough, and was found to have a bleeding pulmonary artery aneurysm at the right lower lung. Pulmonary arteriography was performed and the aneurysm was embolized with coils. As a result, hemoptysis did not subsequently recur. However, five years later, deep vein thrombosis occurred in the left leg. Left leg pain improved after the regional infusion of thrombolytics.
Chris Tae Young Chung,고현민,Hyo Kee Kim,Hyejin Mo,Ahram Han,Sanghyun Ahn,Sangil Min,Seung-Kee Min 대한혈관외과학회 2019 Vascular Specialist International Vol.35 No.3
A 58-year-old male patient with severe claudication due to thrombosis of the left ilio-femoro-popliteal artery aneurysm. He also had a venous stasis ulcer with a history of multiple embolotherapy of arteriovenous malformation. Duplex sonography revealed reflux and varicose veins of the left great saphenous vein (GSV). A sequential bypass surgery was performed that consisted of excision of the left external iliac and common femoral artery aneurysm, external iliac to deep femoral interposition with an expanded polytetrafluoroethylene graft, and femoro-posterior tibial artery bypass with the reversed left GSV. Symptoms of claudication were alleviated and the chronic ulcer was healed in time. To our knowledge, this is the first report of successful bypass in a patient with arterial aneurysm, arteriovenous malformation, and venous insufficiency that can be diagnosed as an atypical case of Parkes Weber syndrome. Long-term follow-up is needed to define the fate of aneurysms and varicose vein graft.
Fatal Pulmonary Thromboembolism Caused by Popliteal Vein Aneurysm
최규헌,하홍일,박소형 대한법의학회 2018 대한법의학회지 Vol.42 No.3
Popliteal venous aneurysms can be a cause of fatal pulmonary thrombo-embolism. We report a case of a 47-year-old woman who suddenly died of fatal pulmonary thromboembolism. Deep vein thrombosis was not observed, but a venous aneurysm with intraluminal thrombi formation was identified on the left popliteal vein. This case illustrates that venous aneurysms can be presented as fatal pulmonary thromboembolism, and that they should be considered as a rare cause of pulmonary thromboembolism.
Su Wan Kim,Jonggeun Lee,Seogjae Lee,Jee Won Chang,Chang Lim Hyun Institute for Medical Science 2023 The Journal of Medicine and Life Science Vol.20 No.4
Aneurysmal venous dilatation is a frequent complication of arterio venous fistulas (AVFs) created for hemodialysis. Venous aneurysm rupture can lead to lethal hemorrhage. A 49-year-old male patient presented with a giant aneurysmal dilatation of his AVF 10 years after its creation. The patient had complaints of pulsating pain and discomfort due to swelling of the left forearm. We performed an aneurysm resection and revised the overlying dermal lesion through a brachial plexus block. Here, we describe the pathological features of the arterialized venous aneurysm compared to simple venous aneurysms.