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( Cheol Jin Lee ),( Se Hun Lim ),( Chee Mahn Shin ),( Young Jae Kim ),( Young Kyun Choe ),( Soon Ho Cheong ),( Kun Moo Lee ),( Jeong Han Lee ),( Young Hwan Kim ),( Kwang Rae Cho ),( Sang Eun Lee ),( J 대한마취과학회 2010 Korean Journal of Anesthesiology Vol.59 No.1
There are many causes of prolonged postoperative muscle weakness, including drugs, residual anesthetics, cerebrovascular events, electrolyte imbalance, hypothermia, and neuromuscular disease. Neuromuscular diseases are relatively rare, with the most common being myasthenia gravis and Lambert-Eaton myasthenic syndrome (LEMS). We report an unusual case in which a patient who was given a muscle relaxant during mediastinoscopy developed postoperative muscle weakness that was ultimately diagnosed as secondary to LEMS. (Korean J Anesthesiol 2010; 59: 45-48)
안구증상으로 발현한 Lambert-Eaton Myasthenic Syndrome (LEMS)
한우호,석정임,이규철,권오대,김숙영 대한신경과학회 2010 대한신경과학회지 Vol.28 No.1
Lambert-Eaton myasthenic syndrome (LEMS) is characterized clinically by fluctuating muscular weakness; presentation with ocular symptoms is unusual. A 60-year-old man had developed diplopia and ptosis 2 years previously. The findings of a neurologic examination were normal except for bilateral ptosis and ophthalmoplegia. The amplitude of compound muscle action potentials recorded on the abductor digiti minimi increased (by more than 500%) during 50-Hz stimulation. This case demonstrates that LEMS should be included in the differential diagnosis of myasthenic symptom confined to the ocular muscles.
한지훈,우상하,박유경,최성훈,이윤규,이정희,김재수,이현종,Han, Ji Hoon,Woo, Sang Ha,Park, Yu-kyeong,Choi, Seong-Hun,Lee, Yun-kyu,Lee, Jung Hee,Kim, Jae Soo,Lee, Hyun-Jong The Korean Medicine Society for the Herbal Formula 2021 大韓韓醫學方劑學會誌 Vol.29 No.4
This case study reports the effects of complex Korean medicine treatment, including Nangan-jeon, on Lambert-Eaton myasthenic syndrome (LEMS) accompanied by chronic constipation and abdominal pain as the main symptoms. A 39-year-old woman diagnosed with LEMS with major symptoms, including chronic constipation and acute abdominal pain, received Western treatment. The treatment efficacy was weak and symptoms recurred, so the patient received outpatient treatment and 13 days of hospitalization for active Korean medicine treatment, including Nangan-jeon. During outpatient treatment and hospitalization, defecation frequency and the numeric rating scale (NRS) for abdominal pain and abdominal cold feeling were measured. The NRS for abdominal pain and cold decreased from 8 at admission to 3 and 0, respectively, at discharge. Defecation frequency increased significantly from once or twice a month to once every 2-3 days during hospitalization. This study results that complex Korean medicine treatment, including Nangan-jeon may be useful for treating patients who mainly complain of autonomic neurological symptoms, among patients diagnosed with LEMS. In addition, it is believed that it could be basic data applicable to more LEMS patient treatment cases.
송승원,조진혁,정승호 대한신경과학회 2021 대한신경과학회지 Vol.39 No.3
A 79-year-old man visited neurology clinic due to gait ataxia and vertigo for 10 months. Neurologic examination revealed saccadic pursuit, mild dysmetria, impaired tandem gait, and areflexia that recovers after exercise. The amplitude of compound muscle action potentials recorded on the abductor digiti minimi increased up to 6,639.4% during repetitive nerve stimulation at 50 Hz stimulation. This case demonstrates that clinicians should consider Lambert-Eaton myasthenic syndrome as a differential diagnosis when a patient complains of gait ataxia and vertigo.
완전 관해를 보인 Lamber-Eaton 근무력증후군에서 전이성 뇌종양으로 재발한 소세포 폐암
하상욱,김종국,허소영 대한근전도전기진단의학회 2011 대한근전도 전기진단의학회지 Vol.13 No.1
We present a patient of Lamber-Eaton myasthenic syndrome (LEMS) with small cell lung cancer recurred as metastatic brain tumor after one year of remission. This is a case of remitted LEMS by chemotherapy with regardless of tumor recurrence. Though it is difficult to interpret due to the rarity, LEMS can be the initial and transient finding in the natural course of small cell lung cancer.
이정환,신하영,김승민,선우일남 대한신경과학회 2012 Journal of Clinical Neurology Vol.8 No.4
Background Lambert-Eaton myasthenic syndrome (LEMS) is a presynaptic neuromuscular junction disorder that is most frequently associated with small-cell lung cancer (SCLC). The titers of antibodies against voltage-gated calcium channels are frequently increased in LEMS, but only rarely is titer of anti-acetylcholine-receptor-binding antibodies (AChR-abs) increased. Case Report A 57-year-old male was admitted to our hospital due to dry mouth and eyes and progressive proximal limb weakness of 2 months duration. The results of a repetitive nerve stimulation test disclosed all criteria for the electrophysiological LEMS pattern, and the patient’s AChRabs titer was 0.587 nmol/L. At a follow-up performed 5 years after successful treatment of SCLC and LEMS, his AChR-abs titer had decreased to 0.001 nmol/L. Conclusions We suggest that this was a case of transient pseudopositivity of AChR-abs in SCLC with LEMS.
진단 딜레마: 반복신경자극검사가 정상인 램버트-이튼근무력증후군
정유훈,석흥열 대한신경과학회 2022 대한신경과학회지 Vol.40 No.2
It is important for the diagnosis of Lambert-Eaton myasthenic syndrome (LEMS) to confirm the incremental response at high-rate stimulation or after brief exercise in the repetitive nerve stimulation (RNS) test. Therefore, it may be difficult to diagnose LEMS if the RNS test is normal initially. We report a patient with LEMS whose diagnosis was delayed due to normal RNS findings. We believe that anti-P/Q-type voltage-gated calcium channel antibody testing is crucial in the diagnosis of LEMS.
소세포 폐암의 확진을 위한 수술후 호전된 소세포 폐암에 의한 Lambert-Eaton 근무력 증후군
박성하 ( Sung Ha Park ),최선아 ( Sun Ah Choi ),유태현 ( Tae Hyun Yu ),김길동 ( Gil Dong Kim ),김세규 ( Se Kyu Kim ),장준 ( Joon Chang ),신동환 ( Dong Hwan Shin ),선우일남 ( Il Nam Sunwoo ),이원영 ( Won Young Lee ) 대한결핵 및 호흡기학회 1998 Tuberculosis and Respiratory Diseases Vol.45 No.3