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Thoracic Ectopia Cordis의 산전진단 1 예
오영현(YH Oh),조용훈(YH Cho),윤영돈(YD Yoon),송태복(TB Song),오봉석(BS Oh) 대한산부인과학회 1992 Obstetrics & Gynecology Science Vol.35 No.7
Ectopia cordis means that heart is partially or totally outside the thorax. There are essentially four types of ectopia cordis: central, thoracic, thoracoabdominal, and abdomial. Associated intrathoracic anomalies are common. Death occurs in the first day of life in majority of instances, usually from infection, cardiac failure, or hypoxemia. the sternum is split and the heart protrudes outside the chest in the thoracic form of ectopia cofdis. We present a case of thoracic ectopia cordis which was diagnosed at 25 weeks` gestation by ultrasonography with a brief review of literature.
장연희(YH Jang),임문환(MH Im),심재철(JC Sim),박성기(SK Park),김태우(TW Kim),이창연(CY Lee),오연희(YH Oh),이원재(WJ Lee),박석건(SG Park),유문집(MJ Yu) 대한산부인과학회 1992 Obstetrics & Gynecology Science Vol.35 No.1
The McCune-Albrights syndrome is extremely rare if one considers the complete form which fullfils the triad of cafe au lait spots, fibrous dysplasia, and endocrine disturbances. A current concept about endocrine disturbances in this syndrome is that it is the result of autonomous hyperfunction of peripheral target glands, and that other endocrine disorders (hyperthyroidism, Cushing syndrome, gigantism, and acromegaly)are occasionary accompanied, and that treatment with the aromatase inhibitor testolactone which blocks the synthesis of estogens seems to be successful. The authors report a case of a 22/12-year-old girl with sexual precocity and cafe au lait spots with literature review.
Do we need total colonoscopy in patients with acute diverticulitis on computed tomography?
( Yh Choi ),( Jp Im ),( Js Kim ),( Sj Koh ),( Jw Kim ),( Kl Lee ),( Bg Kim ) 대한내과학회 2013 대한내과학회 추계학술발표논문집 Vol.2013 No.1
Background/Aims: Although colonoscopy verification is warranted after an acute event of diverticulitis to exclude underlying malignancy, little evidence is available to support the recommendations. The aim of this study was to evaluate the yield of a colonoscopy. Methods: From January 2001 to March 2013, patients in whom acute diverticulitis was diagnosed on CT scan were matched with colonoscopy reports within 1 year from the date of CT. Results: A radiological diagnosis of acute diverticulitis was made in 443 patients. One hundred forty-nine patients underwent subsequent colonoscopy within a year from the date of CT. There were no significant differences in clinical characteristics between patients with or without colonoscopy. 12 patients (8.1%) were diagnosed with colon cancer. Conclusion: Yield of colonic malignancy in this cohort was more than that detected on screening asymptomatic average-risk individuals. Patients with diverticulitis on CT are warrants endoscopic verification.Background/Aims: Although colonoscopy verification is warranted after an acute event of diverticulitis to exclude underlying malignancy, little evidence is available to support the recommendations. The aim of this study was to evaluate the yield of a colonoscopy. Methods: From January 2001 to March 2013, patients in whom acute diverticulitis was diagnosed on CT scan were matched with colonoscopy reports within 1 year from the date of CT. Results: A radiological diagnosis of acute diverticulitis was made in 443 patients. One hundred forty-nine patients underwent subsequent colonoscopy within a year from the date of CT. There were no significant differences in clinical characteristics between patients with or without colonoscopy. 12 patients (8.1%) were diagnosed with colon cancer. Conclusion: Yield of colonic malignancy in this cohort was more than that detected on screening asymptomatic average-risk individuals. Patients with diverticulitis on CT are warrants endoscopic verification.