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이홍주,김명희,정조원,김성호,최보율,Lee, Hong-Jue,Kim, Myoung-Hee,Jung, Jo-Won,Kim, Seong-Ho,Choi, Bo-Youl 대한예방의학회 2001 Journal of Preventive Medicine and Public Health Vol.34 No.4
Objective : To estimate the prevalence of congenital heart disease from the 1990 student heart disease screening program. Methods : The heart disease screening program for elementary students was conducted in Kyonggi-do, in 1998. The subjects of the present study comprised the 40,402 students who attended the schools in the catchment area of a collaborative university hospital and who participated in the primary examination. The congenital heart disease (CHD) patients were initially identified through a questionnaire about prior medical history, and further through diagnostic tests & medical examinations in the secondary & the tertiary examinations. Certain assumptions were used in the estimation of the number of CHD cases among non-participants of the secondary & tertiary examinations. The overall prevalence of CHD was estimated by adding the CHD detection rates of the participants and the estimated prevalence of the non-participants. Results : Among the 40,402 primary participants, 1,655 were referred further, of whom 79.1% (1,309) participated in the secondary examination. Of these, 121 were referred to the tertiary examination, with a participation rate at this last stage of 80.2%. The positive predictive value (PPV) of the screening tools was the highest when the results of both EKG and the questionnaire were positive. Because 85.9% of the detected cases had a past history of CHD, PPV was higher when the selection criteria in the questionnaire included past CHD history than when it didnt. The CHD defection rate among the participants was 1.76 cases/1,000 and the presumed number of cases among the non-participants was 31; giving an estimated final CHD prevalence of 2.52 cases/1,000 (95% CI : 2.06-3.06). Among the identified cases of CHD, VSD (52.8%) was the most common, followed by PDA (9.7%), TOF (9.7%) & PS (9.7%). Conclusion : Because the characteristics of the non-participants differed from those of the participants, the estimation of prevalence was influenced by the participation rate. Of the detected cases, 85.9% had a past history of diagnosis or operation for CMD. These findings suggested that the prevalence estimated in this study may be an underestimation of the actual condition. Therefore, a birth cohort study is required in order to more accurately estimate the prevalence and the effects of the program.
Yersinia enterocolitica의 생물형별(生物型別)에 관(關)한 고찰(考察)
오흥백 ( Hung Back Oh ),김대식 ( Dae Sik Kim ),조용현 ( Yong Hyun Jo ),정조원 ( Jo Won Jung ),서진태 ( Jin Tae Suh ),지현숙 ( Hyun Sook Chi ),이중달 ( Jung Dal Lee ) 대한임상검사과학회 1984 대한임상검사과학회지(KJCLS) Vol.16 No.1
We have isolated 5 strains of Yersinia enterocolitica with biotypes from 803 fecal specimens of the patients for detection of enteric bacteria from November, 1980 to April, 1981 at Kyung Hee Medical Center. All the rectal swabs was inoculated in MacConkey, SS and Selenite broth and again streaking in MacConkey and S-S agar plates after 18 hours cultivation of Selenite broth. All the agar plates were put into the room temperature. After detecting the suspected colonies through first screen Urea agar, SIM and K.I.A. Media. It was given final identification of API Kit. all the strains were determined by Nilehn & Wauters method for biotypes. and The susceptibility tests were performed by National Committee for Clinical Laboratory Standard (N.C.C.L.S) regulation. The typical biochemical properties of the organisms were urea and ornithine positive, dextrose (no gas) and xylose were fermentative, lactose was oxidative, and indol & V.P. were variable at the room temperature, motility was negative at 35℃ and positive at 25℃. The pinpoint of colorless colonies showed red color after 72 hours at room temperature. It was difficult at times to detect the organisms. because of the size and color change of the colonies. As the result of susceptibility test, all the strains were highly susceptible to Gentamycin, Kanamycin, Amikacin, Chloramphenicol, Oxytetracycline but two strains (No 1 & 5) were susceptible to Ampicillin & Carbenicillin (Biotype 2). All the strains were resistant Cephalothin. Three of 5 strains was identified as biotype 3 and the rest as biotype 2 by Nilehn & Wauters method.
척수성 근위축증 증상을 보인 사립체 호흡연쇄효소 복합체 I 결핍에 의한 뇌근병증
이지숙(Ji Sook Lee),안미선(Mi Sun Ahn),유경화(Kyung Hwa Ryu),황진순(Jin Soon Hwang),정조원(Jo Won Jung),김성환(Sung Hwan Kim) 대한소아신경학회 2006 대한소아신경학회지 Vol.14 No.2
저자들은 척수성 근위축증 증상이 사립체 호흡연쇄효소 복합체 I 단독 결핍증의 새로운 임상표현형으로 나타날 수 있음을 세계에서 처음 보고하면서, 임상양상이 척수성 근위축증과 유사하나 SMN 유전자의 결손이 없거나 추적관찰 중 비전형적인 임상증상이 나타나는 경우 반드시 사립체 호흡연쇄효소 복합체의 효소 활성도 검사를 시행하여 사립체질환의 가능성을 고려할 것을 보고하는 바이다. Two female patients with clinical features resembling spinal muscular atrophy are introduced. Patient 1 presented with hypotonia and proximal weakness of extremities at the age of 4 months. The electromyography revealed motor neuronopathy suggestive of spinal muscular atrophy. Patient 2 presented with severe hypotonia, motor weakness, and joint contractures since birth. The muscle biopsy finding was consistent with spinal muscular atrophy. However, deletions in the survival motor neuron genes and the neuronal apoptosis inhibitor protein genes were not found in both the patients. They finally showed the clinical features against spinal muscular atrophy; epileptic seizures, cardiomyopathy, and spasticity. We measured the mitochondrial respiratory chain complex enzyme activities in cultured skin fibroblasts, whose results were suggestive of isolated complex I deficiency in both the patients. In conclusion, for the patients who have clinical features resembling SMA without any deletions in the SMA genes it should be considered a possibility of the mitochondrial respiratory chain complex I deficiency.
서유진(Yu Jin Suh),조재웅(Jae Woong Cho),이진호(Jin Ho Lee),이규성(Keu Sung Lee),김선신(Sun Sin Kim),이수걸(Soo Keol Lee),홍지만(Ji Man Hong),김장성(Jang Sung Kim),정조원(Jo Won Jung),남동호(Dong Ho Nahm),박해심(Hae Sim Park) 대한천식알레르기학회 2001 천식 및 알레르기 Vol.21 No.1
Kawasaki disease (KD) is an acute vasculitis of undetermined etiology in infancy and early childhood. There is no diagnostic test to confirm this disease and its diagnosis is made on clinical backgrounds. Most patients diagnosed are under 4 years of age. Here, we report a case of KD in an adult presented with clinical features of fever, headache, and skin rash. A 26-year-old male was presented with fever and headache of four days' duration and skin rash of three days' duration. Nausea and vomiting developed and the patient was treated with antibiotics under the impression of aseptic meningitis and became afebrile two days later. Laboratory findings revealed thrombocytosis, atypical lymphocytes, and elevated liver enzymes. Kawasaki disease was diagnosed, and intravenous immunoglobulin and low-dose aspirin (200mg/d) was administered. Hocardiogram did not reveal any coronary artery changes and the skin lesions disappeared. The patient was discharged after near normalization of the liver enzymes and is now being followed at our clinic. (J Asthma Allergy Clin Immunol 21: 96-102, 2001)
정조원,홍창호,소동문,이철주 아주대학교 의과학연구소 1996 아주의학 Vol.1 No.1
Atrial septal defect is common congenital heart disease in children. Inheritance follows the multifactorial mode primarily but in certain families autosomal dominant transmission is evident. In Korea, there has been no case report of twins with ASD or any other congenital heart diseases in children, while there have been several reports of sildings and twins with ASD or other congenital heart diseases in other countries. Herewith we report a monozygotic pair of twins with atrial septal defects who were diagnosed by cardioc catheterizarion and confirmed by operation, with brief reriew of the literature.
이지연,정조원,홍창호 아주대학교 1997 아주의학 Vol.2 No.1
Pulmonary artery sling is a rare congenital vascular anomaly in which the left pulmonary artery arises aberrantly from the proximal part of the right pulmonary artery and encircles the right main bronchus and distal trachea before entering the hilum of the left lung. This causes compression of the trachea and right main bronchus, and most infants with this anomaly have severe respiratory distress within the first year of life. Associated anomalies are common, and particularly, tracheobronchial anomalies occur in 40% of the patients. Major cardiovascular anomalies including ventricular septal defect, atrial septal defect, patent ductus arteriosus, tetralogy of Fallot, common ventricle, and coarctation of the aorta, occur in about half of the affected infants. We have experienced an 11-month-old male infant with respiratory distress, wheezing, and cyanosis. He was diagnosed as pulmonary artery sling associated with left bronchial hypoplasia by echocardiography, angiography, and chest CT scan. Other associated anomalies were left kidney agenesis, right megaureter and right kidney hypertrophy, diagnosed by abdominal sonography and IVP. We report this case with a brief review of literature.