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모체 혈액 내 융모성선자극호르몬의 증가가 있는 임신에서 양수 내 angiogenin 과 interleukin-6 의 농도 변화
원혜성(Hye Sung Won),유혜경(Hye Kyung Yoo),김소라(So Ra Kim),정지윤(Ji Yoon Jung),정복경(Bok Kyung Jung),이필량(Pil Ryang Lee),이인식(In Sik Lee),김암(Ahm Kim) 대한산부인과학회 2002 Obstetrics & Gynecology Science Vol.45 No.4
Objective : This study is to measure the level of concentration of angiogenin, a cause of potent neovascularization and a marker of ischemia, and of interleukin-6 (IL-6), an indicator of acute inflammation, in the amniotic fluid of patients with elevated maternal serum free β-hCG level during the second-trimester. Materials and Methods : Twenty patients with elevated maternal serum free β-hCG level (>2.5 MoM) at double screening test of Down syndrome were compared with the controlled group (<2.0 MoM). This study includes singleton gestation, gestational age of 14-18 weeks, and has no evidence of fetal structural and chromosomal anomalies. The levels of amniotic angiogenin and IL-6 were measured by enzyme-linked immunosorbent assay (ELISA) method. Data were analyzed by Mann-Whitney U test. p value <0.05 was considered significant. Results : Amniotic angiogenin levels in the studied group were much lower than those in the controlled group (p<0.05), whereas the difference of IL-6 levels between the two groups was not significant. Nine studied patients delivered small for gestational age infants, but only one controlled patient (p<0.05) had the same infant. Other variables of perinatal outcome were not different between the two groups. Conclusion : That amniotic fluid angiogenin levels are significantly lower in patients with elevated maternal serum free β-hCG suggests an inadequate angiogenesis. Elevated maternal serum free β-hCG levels correlate with fetal growth restriction. IL-6 values in both groups have no significant difference.
자간전증이 합병된 임신에서 인간 태반의 산화질소 합성효소의 발현 및 활성도의 변화
원혜성(Hye Sung Won),이필량(Pil Ryang Lee),이인식(In Sik Lee),김암(Ahm Kim),남주현(Joo Hyun Nam),목정은(Jung Eun Mok) 대한산부인과학회 2000 Obstetrics & Gynecology Science Vol.43 No.7
Objective : The changes of the production of nitric oxide in preeclampsia are still controversial. To determine the changes of nitric oxide production in preeclamptic pregnancies, NOS activity and eNOS and iNOS expression in preeclamptic placentae were compared with those in normal placentae, and to determine the changes of nitirc oxide production according to the sites of placenta, NOS activity and eNOS expression in preeclamptic placentae were also compared with those in normal placentae. Methods : Human placentae were obtained from 15 normal and 15 preeclamptic pregnant women at the time of cesarean section. NOS activity was assessed by measuring the conversion of [3H]-arginine into [3H]-citrulline. The eNOS and iNOS expression were assessed by using western blot analysis. Data were analyzed by Student t-test and paired t-test where appropriate. Results : The NOS activity(judged by measurement of [3H]-citrulline production) was significantly increased in preeclamptic placentae compared to normal(P<0.05). In normal and preeclamptic pregnant placentae, the NOS activity in main stem villi was increased compared to that in terminal villi. However, the difference of NOS activity between main stem villi and terminal villi was not significant(P>0.05). Quantification of the autoradiographic images demonstrated that the integrated optical density of the immunoreactive bands of eNOS were significantly lower in preeclamptic placentae compared to normal(p<0.05). Conversely, the integrated optical densities of the bands of iNOS were significantly higher in preeclamptic placentae compared to normal(p<0.05). Conclusion : Although the eNOS expression in preeclamptic placentae was lower than that in normal placentae, the NOS activity was significantly higher in preeclamptic placentae than that in normal in this study. These are result from increased production of iNOS in the compensatory mechanisms for the decreased nitric oxide production in pre-eclamptic placentae
원혜성 ( Mi Young Lee ),( Hye Sung Won ),( Jae Yoon Shim ),( Pil Ryang Lee ),( Byong Sop Lee ),( Ellen Ai Rhan Kim ),( Young Hwue Kim ),( Jeong Jun Park ),( Tae Jin Yun ),( Ahm Kim ) 대한산부인과학회 2015 대한산부인과학회 학술대회 Vol.101 No.-
Objective: To report our experiences in the prenatal diagnosis of atrial isomerism and postnatal outcomes. Methods: A total of 80 fetuses prenatally diagnosed with atrial isomerism were retrospectively analyzed between 1999 and 2011 at a single institution. Results: Of 43 fetuses with prenatally diagnosed right atrial isomerism (RAI), 40 cases were analyzed. The diagnostic accuracy was 93%. The main intracardiac anomalies in RAI were atrioventricular septal defect (AVSO), abnormal pulmonary venous connection, bilateral superior vena cava (BSVC), and pulmonary atresia. Among 28 live births, three infants were lost to follow up, and the overall survival rate was 60%. Of 37 fetuses with prenatally diagnosed left atrial isomerism (LAI), 35 were evaluated. The diagnostic accuracy was 97%. The main intracardiac anomalies in LAI were ventricular septal defect, BSVC, AVSD, double outiet right ventricle, and bradyarrhythmia. Among seven patients with bradyarrhythmia, only one showed a complete atrioventricular block. All fetuses had an interrupted inferior vena cava with azygous continuation. The overall survival rate was 90%. Conclusion: Our study confirms the previous findings of fetal atrial isomerism. We also demonstrates a much lower prevalence of AVSO and complete heart block In LAI and a better survival rate in RAI. Although the postnatal outcomes lor RAI were worse than those for LAI, successful postnatal surgery with active management improved the survival rate.
혈액투석이 필요한 심한 부종양 고칼슘혈증으로 발현한 식도암
안혜신 ( Hye Shin Ahn ),윤종민 ( Jong Min Yun ),이영복 ( Yeong Bok Lee ),고유미 ( Yu Mi Ko ),이정은 ( Jung Eun Lee ),원혜성 ( Hye Sung Won ),김성수 ( Sung Soo Kim ),김영옥 ( Young Ok Kim ) 대한소화기학회 2015 대한소화기학회지 Vol.65 No.6
Paraneoplastic hypercalcemia without bone metastasis occurs rarely in esophageal cancer. A 75-year-old man was admitted for general weakness and lethargy. Laboratory data showed high serum calcium level (corrected calcium 14.6 mg/dL), low parathyroid hormone level (3.3 pg/mL) and high parathyroid hormone-related peptide level (3.5 pmol/L). Esophagogastroscopy showed a malignant tumor in the esophagus. Histology showed moderately differentiated squamous cell carcinoma. Bone scan showed no evidence of bone metastasis. Since the patient’s calcium levels remained high and mental state did not show improvement despite intravenous fluid therapy, diuretics and intravenous bisphosphonate, hemodialysis was started. After hemodialysis treatment, the serum calcium level subsequently normalized and his mental status improved. Herein, we report a rare case of paraneoplastic hypercalcemia in a patient with esophageal cancer. (Korean J Gastroenterol 2015;65:361-365)
22q11.2 결손 증후군 (DiGeorge 증후군)의 산전 진단 2예
박성균 ( Sung Kyun Park ),전균호 ( Gyun Ho Jeon ),노현진 ( Hyun Jin Roh ),안송미 ( Song Mi Ahn ),김선권 ( Sun Kwon Kim ),심재윤 ( Jae Yoon Shim ),김성훈 ( Sung Hoon Kim ),원혜성 ( Hye Sung Won ),이필량 ( Pil Ryang Lee ),김암 ( Ah 대한산부인과학회 2004 Obstetrics & Gynecology Science Vol.47 No.9
Before the exact location of its chromosomal abnormality was identified, 22q11.2 deletion syndrome was described as many different names depending on its presenting clinical features. Patients with this syndrome have a wide range of findings such as cardi