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양성규,이병천,고윤아,김준엽 대한신경과학회 2022 대한신경과학회지 Vol.40 No.4
Vascular EhlersDanlos syndrome (vEDS) is caused by dysfunctional COL3A1 gene for type III procollagen. It presents with translucent skin, easy bruising, and arterial dissection. It has the worst prognosis among various types of EDS with holloworgan rupture as the leading cause of death, mounting to the median life expectancy of mid40s. We report a rare case of vascular EhlersDanlos syndrome presenting late in the fifth decade of life with multiple arterial dissections isolated to cerebral arteries.
림프구 침윤을 보이는 피부질환에서 Ki - 67 항원의 발현
양성규,조광현,김철우 (Seong Gyu Yang,Kwang Hyun Cho and Chul Woo Kim) 대한피부과학회 1996 대한피부과학회지 Vol.34 No.2
Background: A number of reports have stressed the usefulness of cell kinetic estimations as an aid in the prognostic and diagnostic classification of malignant lymphoma. But very limited information is available concerning cell cycle distirbutions in cutaneous lymphoid infiltrate, although a number of these conditions present tremendous problems in diagnosis and management. Objective : The purpose of this study is to evaluate the proliferative activities in various cutaneous lymphoid infiltrates and its usefulness in diagnosis or foretelling a prognosis. Methods : Fifty two arehival biopsy specimens were studies. These included cases of peripheral T-cell lymphoma, lichen planus, lupus erythematosus, polymorphous light eruptions, and pseudolymphomas such as insect bite, lymphomatoid papulosis, and other lymphocytoma cutis. Ki-67 was identified by immunoperoxidase technique using MIB1, a monoclonal antibody that recognizes a fixation and embedding resistant epitope on the Ki-67 protein. Results : Higher Ki-67 positive rates were observed in high grade angiocentric T-cell lymphomas, which was helpful in differentiating from benign disease. In two cases of lymphomas which Ki-67 positive rate were more than 80 percent despite of minimal lymphoid infiltrate in skin biopsy specimen, evaluation of Ki-67 expression was profoundly helpful in diagnosing them as malignancies. Conclusion : Use of this technique was useful in evaluation of proliferative activity of cutaneous lymphoid infiltrate. In some cases, use of this technique may aid us in differential diagnosis of malignant lymphoma from benign chronic inflammatory disease of the skin. (Kor J Dermatol 1996;34(2): 219-226)
양성규,이병천,오다나,윤창호,윤지은 대한수면연구학회 2022 Journal of sleep medicine Vol.19 No.2
Obesity hypoventilation syndrome (OHS) is defined as the combination of daytime hypercapnia (awake PaCO<sub>2</sub> ≥45 mm Hg) and obesity (body mass index ≥30 kg/m<sup>2</sup>). Untreated OHS is associated with comorbidities, including cardiovascular diseases, heart failure, pulmonary hypertension, and metabolic syndrome. Continuous positive airway pressure (PAP) therapy with non-invasive ventilation is the gold standard for treating OHS. PAP therapy is highly effective; however, some adverse effects can affect long-term compliance. Air leakage through the mouth or around a mask is a common adverse effect of PAP therapy. Air leakage through the nasolacrimal duct or due to unsealed circuits has also been reported as a complication of PAP therapy; however, it is relatively rare. Considering the negative association between the level of air leakage and adherence to PAP therapy, clarifying the cause of air leakage during PAP therapy and minimizing it are key to successful outcomes. We report a case of air leakage through the nasolacrimal duct that was improved by inserting a gel foam patch inside the lacrimal sac of a patient with OHS with a history of reconstructive surgery for nasolacrimal duct obstruction.