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신용범,신명준,장재혁,차영선,고현윤 대한재활의학회 2014 Annals of Rehabilitation Medicine Vol.38 No.1
Birth brachial plexus palsy (BBPP) is usually caused by plexus traction during difficult delivery. Although the possibility of complete recovery is relatively high, 5% to 25% of BBPP cases result in prolonged and persistent disability. In particular, muscle imbalance and co-contraction around the shoulder and elbow cause abnormal motor performance, osseous deformities, and joint contracture. Physical and occupational therapies have most commonly been used, but these conventional therapeutic strategies have often been inadequate, in managing the residual muscle imbalance and muscle co-contraction. Therefore, we attempted to improve the functional movements, by using botulinum toxin type A, to reduce the abnormal co-contraction of the antagonist muscles.
A형 보툴리눔독소를 이용한 흉곽출구증후군의 치료 1례 -증례보고-
신용범,손현주,장재혁,박형욱,차영선,고현윤 대한재활의학회 2008 Annals of Rehabilitation Medicine Vol.32 No.1
The true neurogenic thoracic outlet syndrome (TOS), one type of the TOS, has vague and controversial clinical symptoms, so a variety of diseases can mimic the presentation of TOS, especially ulnar neuropathy or cervical root lesion. For most patients with TOS, common practice is to offer a course of conservative treatment, but its kinds are not enough and pain is too severe to do that in the chronic state. We experienced a case of true neurogenic thoracic outlet syndrome with distinctive clinical symptom and abnormal electrodiagnostic findings. The symptom was not controlled by conservative management including oral medication or physical therapy. So we injected type A botulinum toxin (BotoxⓇ) in the scalene and pectoralis minor muscles with ultrasonography guide. After 2 weeks, the pain decreased in visual analogue scale nine to four, and the compliance to physical therapy was improved. The result appeared to demonstrate that botulinum toxin injection may be helpful in controlling symptoms and making the patient adapt in physical therapy in the difficult case to management by any other methods.
Partial Trisomy 1q41 Syndrome Delineated by Whole Genomic Array Comparative Genome Hybridization
신용범,남상욱,서을주,김형회,장철훈,이은엽,손한철,황상현 대한의학회 2008 Journal of Korean medical science Vol.23 No.6
Partial trisomy 1q syndrome is a rare chromosomal abnormality. We report on a male infant with 46,XY,der(11)t(1;11)(q41;p15.5) due to unbalanced segregation of the maternal reciprocal balanced translocation 46,XX,t(1;11)(q41;p15.5). The baby presented with a mild phenotype, characterized by a triangular face, almond-shaped eyes, low ears, short stature with relatively long legs, and mild psychomotor retardation. We utilized whole genomic array comparative genome hybridization (CGH) with 4,000 selected bacterial artificial chromosomes (BACs) to define the chromosomal breakpoints and to delineate the extent of the partial trisomy in more detail. To our knowledge, this is the first case of nearly pure “partial trisomy 1q41” defined by whole genomic array CGH.
기관지동맥 비후에 의한 식도압박으로 유발된 삼킴장애 1례-증례 보고-
신용범,손현주,장재혁,한지의,김경민,고현윤 대한재활의학회 2008 Annals of Rehabilitation Medicine Vol.32 No.2
Recurrent respiratory tract infections and dysphagia after the first years of life are rarely caused by vascular compression of the esophagus. We experienced a case of dysphagia and frequent vomiting resulted from esophageal compression by bronchial artery hypertrophy, which might had been aggravated by recurrent aspiration pneumonia caused by underlying swallowing difficulty. The patient initially had significant motor delay and swallowing difficulty. Videofluoroscopic swallowing studies demonstrated deglutition abnormalities and aspiration. In addition, significant amount of swallowed food was regurgitated through esophagus. On barium esophagography and angiography, posterior indentation of the esophagus without proximal dilatation and bronchial artery hypertrophy were noted without congenital heart disease. Pulmonary trunk and its branches showed normal appearance. Therefore, we considered that bronchial artery hypertrophy attributed to pulmonary artery fibrosis due to recurrent aspiration pneumonia may cause esophageal compression, which in turn contribute to dysphagia, frequent vomiting and recurrent aspiration pneumonia.
경막 외 스테로이드 주사에 반응 없는 추간판성 요통에 대한 추간판 내 시술 효과
신용범,고현윤,손현주,장재혁,박형욱,신명준,김수연 부산대학교 병원 암연구소 2008 부산대병원학술지 Vol.- No.23
Objective: To determine the effect of intradiscal therapy with discography in patients with back pain of no effect using epidural steroid. Subject and methods: Thirty patients with herniated nucleus pulposus (HNP) who had not have any improvement using repeated epidural steroid were studied. Degree of disc degeneration, provocation pain and intradiscal pressure were evaluated in 41 discs. Intradiscal triamcinolone was injected to degenerated discs and intradiscal electrothermal therapy (IDET) was performed to the patients who had no improvement using intradiscal steroid. Patients were asked to report pain according to a visual analogue scale (VAS). Results: Thirty of 41 discs showed significant degeneration. In 19 of 30 (63.3%) patients, VAS was reduced over 50% after intradiscal steroids. Low intradiscal pressure without provocation pain and ruptured discs were significantly higher in these patients (p<0.05). After IDET, 8 of 9 patients noted over 50% reduction of VAS. Conclusions: In patients with discogenic back pain combined with radicular pain, intradiscal therapy according to discography may be helpful in patients with no improvement using epidural steroid.
신용범,한지의,김경민,양송현,임대성 대한재활의학회 2005 Annals of Rehabilitation Medicine Vol.29 No.6
Lesch-Nyhan syndrome is a rare X-linked recessive metabolic disorder characterized by developmental delay, hyperuricemia, choreoathetosis, spasticity, mental retardation, and compulsive self-injurious behavior. This disorder results from a complete deficiency of the purine salvage enzyme, hypoxanthine-guanine phosphoribosyltransferase (HGPRT). This syndrome is often misdiagnosed to cerebral palsy and clinical manifestations are usually related to the degree of enzyme deficiency. Complete HGPRT deficiency presents with severe specific neurologic manifestation and nephrolithiasis leading to fatal kidney damage. This report highlighted the importance of clinical awareness leading to early diagnosis and therapy for prevention of the self mutilation and renal failure, even if we couldn't inhibit the progression of neuro-psychotic symptoms.