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신경섬유종증에서 갈색세포종의 영향으로 발생된 뇌동맥류 파열 1예
권민관 ( Min Kwan Kwon ),김다희 ( Da Hee Kim ),최성진 ( Sung Jin Choi ),이혜영 ( Hye Young Lee ) 대한내과학회 2015 대한내과학회지 Vol.89 No.3
Neurofibromatosis 1 (NF-1) shows an autosomal dominant pattern of inheritance with complete penetrance and variable expression. Vascular abnormalities are frequently associated with NF-1. Pheochromocytoma occurs in 0.1-5.7% of patients with NF-1. Spontaneous intracerebral hemorrhage in patients with NF-1-related pheochromocytoma is very rare. Herein, we report a case of subarachnoid hemorrhage caused by multiple ruptured cerebral aneurysms in a patient with concurrent NF-1 and pheochromocytoma. Coil embolization of the aneurysms and subsequent adrenalectomy for pheochromocytoma were successfully performed, and the patient remained normotensive thereafter. This case demonstrates the importance of a careful search for a remediable cause of episodic hypertension in patients with NF-1, who are predisposed to cerebral hemorrhage from fluctuating blood pressure. (Korean J Med 2015;89:327-330)
최성진 ( Seong Jin Choi ),권민관 ( Min Kwan Kwon ),박문 ( Moon Park ),배수야 ( Soo Ya Bae ),오현호 ( Hyun Ho Oh ),이종호 ( Jong Ho Lee ),문지인 ( Ji In Moon ),박찬선 ( Chan Sun Park ),원종철 ( Jong Chul Won ),고경수 ( Kyung Soo K 대한천식알레르기학회 2015 Allergy Asthma & Respiratory Disease Vol.3 No.4
Insulin-induced allergy is a rare adverse drug reaction since the introduction of recombinant human insulin. However, recombinant insulin-induced allergy is still being reported in 0.1% to 2% of all patients treated with insulin. This allergic reaction varies from mild localized skin reactions to life-threatening anaphylaxis. It has been shown that one-third of insulin allergy cases is related to insulin itself and the remaining occur due to preservatives contained in the insulin preparations, such as protamine, zinc, or metacresol. This case report describes a 75-year-old woman with poorly controlled diabetes who experienced insulin allergy. She complained of urticaria with itching after the injection of insulin. Allergic skin tests showed positive responses to all available human insulin preparations, and specific IgE to human insulin was also detected, which suggested that her urticaria was developed by insulin itself. This is the first case of insulin allergy that was sensitive to all available human insulin preparations and confirmed by the presence of specific IgE to human insulin. It is important to remember that allergic reactions to insulin may be directly associated with adherence and can be the reason of poor glucose control. (Allergy Asthma Respir Dis 2015;3:302-306)