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산전 검사 상 발견된 태아 뇌실 확장증의 초음파적 예후 인자
김윤환 ( Yun Hwan Kim ),이시은 ( Si Eun Lee ),박찬욱 ( Chan Wook Park ),손유경 ( Yoo Kyung Sohn ),오수영 ( Soo Young Oh ),심순섭 ( Soon Sup Shim ),박중신 ( Joong Shin Park ),전종관 ( Jong Kwan Jun ),윤보현 ( Bo Hyun Yoon ),신희철 대한산부인과학회 2005 Obstetrics & Gynecology Science Vol.48 No.2
Objective: The aim of this study was to find out the prognostic indicators of antenatally detected ventriculomegaly. Methods: During the study period (Nov. 1995 through Jan. 2003), we identified 96 cases of fetal ventriculomegaly and reviewed their antena
임신 말기 뇌실확장증 및 미성숙폐가 합병된 과도신전 경부의 태아
정재원 ( Jae Won Chung ),이은성 ( Eun Sung Lee ),백유진 ( Yu Chin Paek ),이경희 ( Kyung Hee Lee ),설현주 ( Hyun Joo Seol ),오민정 ( Min Jeong Oh ),김해중 ( Hai Joong Kim ) 대한주산의학회 2006 Perinatology Vol.17 No.3
과도신전된 태아두(hyperextended neck)는 산전초음파로 발견되어질 수 있는 다양한 태위들 중 하나로 과도신전된 태아두를 진단하는 것은 중요한 일인데 특히 질식분만을 시도하게 되는 경우 경추손상의 위험도가 증가하기 때문이다. 또한 지속적인 과도신전된 경부를 보이는 태아에서는 구조적 이상의 동반 및 다양한 증후군과 연관될 가능성이 높고 구조적 이상이 동반된 경우 자궁내 또는 출생 후 사망이나 질병이환률이 현저히 증가한다고 알려져 있다. 따라서 과도신전된 경부를 보이는 태아에서 다른 구조적 이상여부 확인을 위해 좀 더 자세한 평가를 하고 그에 따르는 적절한 조치가 필요하다. 본 저자들은 산전임신중반기에 발견된 과도신전된 경부를 가진 태아가 임신후반기에 뇌실확장 및 폐미성숙 소견을 보였던 1예를 경험하였기에 증례 보고하는 바이다. Hyperextended neck of the fetal head is among the various fetal attitudes detected by prenatal sonography. Various etiologies may lead to hyperextension of the fetal head, including fetal anomalies such as structural abnormalities, conjoined twins and fetal neck masses, nuchal cord and uterine factors such as leiomyoma and uterine malformations. The importance of the precise prenatal diagnosis of this condition relates not only to the delivery mode, but also to the detection of associated conditions, as noted above. We report a case of a fetus whose persistent hyperextended neck was detected by midtrimester sonography, and who later demonstrated ventriculomegaly and lung immaturity in the 3rd trimester.
경도인지장애를 동반한 파킨슨병 환자의 서울신경심리검사와 뇌 자기공명영상에서 뇌실 체적 변화에 대한 상관관계
이현용(Hyunyong Lee),김현진(Hyeonjin Kim),임인철(Inchul Im),이재승(Jaeseung Lee) 한국방사선학회 2014 한국방사선학회 논문지 Vol.8 No.5
본 연구는 경도인지장애가 동반된 파킨슨병 환자에 대하여 인지 기능 평가를 위한 서울신경심리검사와 뇌 자기공명영상에서 영역별 뇌실에 대한 체적 변화를 분석하여 경도인지장애가 동반된 파킨슨병에 대한 진단적 기준을 판단할 수 있는 가이드라인을 제시하고자 하였다. 이를 위하여 파킨슨병으로 진단 받은 환자(경도인지장애군: 34명, 비인지장애군: 34명)를 대상으로 주의력, 언어, 기억력, 시공간, 그리고 전두엽 집행 기능에 대한 서울신경심리검사와 뇌 자기공명영상 검사를 시행하였다. 또한 영역별 뇌실에 대한 체적 변화를 비교하기 위하여 정상인 32명(정상 대조군)을 추가선정하여 추가적으로 뇌 자기공명영상 검사를 시행하였으며 영역별 뇌실에 대한 체적 분석은 프리서퍼(Freesurfer Ver. 5.1, Boston MA, USA)를 통해 수행되었다. 결과적으로 경도인지장애군은 시공간 및 기억력에 대한 수행 능력이 비인지장애군과 비교하여 통계적으로 유의하게 감소되었다(p<0.05). 영역별 뇌실에 대한 체적 변화는 좌ㆍ우측뇌실, 좌ㆍ우하측뇌실, 제3뇌실에서 통계적으로 유의한 체적 변화를 나타내었으며 객관화된 비교를 위하여 정규화한 백분율을 적용한 체적의 변화는 비인지장애군보다 경도인도장애군에서 확장되어 나타났다. 특히 경도인지장애를 동반한 파킨슨병 환자의 좌ㆍ우측뇌실의 확장은 서울신경심리검사에서 시공간 및 기억력 영역에 대하여 뚜렷한 양적 선형관계를 보였다(r>0.5, p<0.05). 따라서 뇌 자기공명영상에서 프리서퍼를 이용하여 영역별 뇌실의 체적 변화를 관찰하고 서울신경심리검사와 상관관계를 분석함으로써 경도인지장애를 동반한 파킨슨병 환자의 진단적 기준을 마련할 수 있을 것으로 판단되었다. The purpose of this study were to analyze that the Seoul neuropsychological screening battery (SNSB) for the evaluating cognitive assessment of the Parkinson's disease patients with mild cognitive impairment (PD-MCI) and the changes of the cerebral ventricle volume in the brain magnetic resonance imaging (MRI), and we has been bring forward the guideline to determine the diagnostic criteria for the PD-MCI. To achieve this, we was diagnosed with Parkinson's disease patients (PD-MCI group: 34 patients; Parkinson's disease with normal cognition, PD-NC group: 34 patients) to perform the SNSB test for the attention, language, memory, visuospatial, and frontal/executive functions and the brain MRI. Additionally, to compared the change of the cerebral ventricle volume, we performed the brain MRI for the 32 normal control (NC) group. The volumetric analysis for a specific cerebral ventricle performed by using Freesurfer Ver. 5.1 (Massachusetts general Hospital, Boston MA, USA). As a results, compared to the PD-NC group, the PD-MCI group were statistically significant reduction in the ability to perform the memory and the visuospatial function (p<0.05). The volumetric changes for a specific cerebral ventricle were statistically significant variation in the left and right lateral ventricle, left and right inferior lateral ventricle, and 3rd ventricle. Although, in order to compared the objectification, the normalized percentage applied to the volumetric changes showed to extend the PD-MCI group than the PD-NC group. Specially, the left and right ventricle extension for the PD-MCI patients conspicuously had showed a quantitative linear relationship between the memory and the visuospatial function for the SNSB (r>0.5, p<0.05). Therefore, we were able to judge the diagnostic criteria of the PD-MCI through that can observe the volumetric variation of the specific cerebral ventricle by using Freesurfer in brain MRI, and to analyze the correlation between the SNSB.
산전 진단된 단독 태아 뇌실확장증의 임상적 고찰: 175예의 후향적 분석
정의 ( Eui Jung ),오지영 ( Jee Young Oh ),김선권 ( Sun Kwon Kim ),심재윤 ( Jae Yoon Shim ),원혜성 ( Hye Sung Won ),이필량 ( Pil Ryang Lee ),김암 ( Ahm Kim ) 대한산부인과학회 2006 Obstetrics & Gynecology Science Vol.49 No.6
Objective: The objective of this study is to evaluate the natural course, postnatal outcome, and association between the degree of ventriculomegaly and neurodevelopmental delay in isolated fetal ventriculomegaly. Methods: We reviewed the medical records of pregnant women diagnosed with isolated fetal ventriculomegaly from October 1996 to June 2004. We defined mild ventriculomegaly as atrial width of 10-14.9㎜ and overt ventriculomegaly as 15㎜ or more. Neonatal brain ultrasonography was performed in all cases and brain MRI was performed as necessary. Neurodevelopmental outcome was evaluated by medical records and telephone interviews. We analyzed the final outcome of isolated fetal ventriculomegaly according to the ventricular width. Results: There were 175 cases of isolated fetal ventriculomegaly, with a large proportion of male fetuses (68.6%), and one case of trisomy 21. While the group with prenatally resolved ventriculomegaly (n=119) had a smaller ventricular width and more unilaterality, there was no resolution in cases with a ventricular width of 15㎜ or more. One hundred and thirty one fetuses with an initial ventricular width of 10 to 11.9㎜ had no developmental delay, however, there were 2 cases of cerebral palsy and 2 cases of genetic disorder. Seventeen fetuses had ventricular dilatation of 15㎜ or more, with 6 corresponding cases of developmental delay and one case of cerebral palsy. Conclusion: Among isolated fetal ventriculomegaly, mild, unilateral or stable ventriculomegaly seems to have a favorable neurological outcome, especially those cases with ventricular width of less than 12㎜. However, management of the condition and counseling of parents are still crucial, because it can be a marker of genetic disorder or brain developmental delay.
김윤숙 ( Yoon Sook Kim ),이슬기 ( Seul Kee Lee ),황인철 ( In Chul Hwang ),서정호 ( Jung Ho Seo ),선우재근 ( Jae Gun Sunwoo ),김민관 ( Min Kwan Kim ),배동한 ( Dong Han Bae ) 대한산부인과학회 2003 Obstetrics & Gynecology Science Vol.46 No.2
Fetal intracranial hemorrhage is quite rare. It refers to the bleeding that occurs antenatally from a blood vessel into ventricles, subdural space, or parenchyme of the brain. Factors that may place the fetus at risk for intracranial hemorrhage include ma
김성(Sung Kim),이동민(Dong Min Lee),김호영(Ho Young Kim),김재연(Jae Yun Kim),최영렬(Young Ryoul Choi),유재경(Jae Kyoung Yoo),윤길중(Gil Jung Yoon),황인수(In Su Hwang) 대한산부인과학회 1999 Obstetrics & Gynecology Science Vol.42 No.11
The prenatal diagnosis of spine bifida include the combined use of maternal serum α-fetoprotein (MSAFP) screening and fetal sonography. Sonographically, spina bifida is characterized by direct signs of the visualization of the spinal defect, and indirect signs of the cranial markers : the lemon sign, the banana sign, and ventriculomegaly. These ultrasonographic signs are more accurate in defining the cranial malformations associated with spina bifida than evaluation of the spine. Recently, three cases of spina bifida which was diagnosed as splaying of the posterior ossification centers, meningomyelocele sac at the lumbosacral area, lemon sign, banana sign and ventriculomegaly by ultrasonography at 21+2 gestational weeks in a 32 years old nullipara, at 21+2 gestational weeks in a 26 years old nullipara, at 23+6 gestational weeks in a 26 years old multipara were experienced at our department. We present this cases with a brief review of literatures
박인양 ( In Yang Park ),김현정 ( Hyun Jeong Kim ),김정 ( Jeong Kim ),안현영 ( Hyun Young Ahn ),신종철 ( Jong Chul Shin ),김수평 ( Soo Pyung Kim ) 대한주산의학회 2003 Perinatology Vol.14 No.4
무뇌회증은 염색체 이상, 감염 등의 여러 원인에 의하여 일어난다고 알려져 있다. 질환의 발생 빈도는 매우 드문 것으로 되어있으며 진단적 소견으로는 뇌실질 조직의 붕괴, 대뇌 피질층의 소실 등이 있으며 뇌실의 확장 소견과 동반되는 것으로 알려져 있다. 또한 Dandy-Walker syndrome이나 Miller-Dieker syndrome과 동반되어 나타날 수 있는 것으로 알려져 있다. 본 증례의 경우 정상적인 산전 진찰을 시행 받던 중 임신 31주 경부터 태아의 뇌실 확장 소견과 구(sulcus)의 감소 소견을 보였으며 유도 분만에 의하여 분만 후 신경학적 검사상 이상 소견을 보여 시행한 MRI상 무뇌회증으로 진단되었으며 염색체 검사상 특이 소견을 보이지 않았다. 산전 초음파 검사상 뇌실 확장 소견을 보이는 경우 이와 동반될 수 있는 질환군 중 매우 드문 형태의 소견을 보여 문헌고찰과 함께 보고하는 바이다. Lissencephaly is a rare disorder that is characterized by the disorganized and unlayered cortex. The cause of this disorder is related to chromosomal abnormalities or infection. The pathogenesis of lissencephaly is faulty migration of neuroblast. Lissencephaly is associated with Dandy-Walker syndrome and Miller-Dieker syndrome. A woman at 35 weeks of gestaion was transferred to our hospital due to abnormal antenatal sonographic findings (ventricular dilation and decreased sulci in cerebral cortex after 31 weeks of gestation). The antenatal studies showed none-specific findings. The infant was diagnosed lissencephaly by postnatal MRI evaluation and showed normal karyotype. We report the prenatal diagnosis of lissencephaly case with a literature.
최호정,이기자,안세준,권영항,정기영,이희천,이영원 한국임상수의학회 2011 한국임상수의학회지 Vol.28 No.1
This study was performed to evaluate the size and asymmetry of the lateral ventricles in CT images of three different small breed dogs. CT examinations were performed on thirty Yorkshire terriers, malteses, and shihtzu dogs, respectively. The size and asymmetry of their lateral ventricles were evaluated at three different levels of brain, and dogs were categorized on the basis of the percentage of their ventricular height (Vh) to brain height (Bh). Degree of asymmetry was also categorized based on the rVh (ratio of right and left ventricular heights) as normal (rVh < 1.5), mild (1.5 < rVh < 2.0), or severe (2.0 < rVh). Clinically insignificant ventricular dilation was common in these breed dogs. However, severe asymmetry was not presented in clinically normal dogs. We suggested 11 mm as an upper limit of ventricular size in normal small breed dogs.