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이재성(Jae Sung Lee),김수평(Soo Pyung Kim),정서호(Seo Ho Chung),이영(Young Lee),정인철(In Cheul Jung),윤원식(Won Sik Yoon),이종건(Jong Kun Lee),천연희(Yeon Hee Cheon),이종승(Chong Seung Yi) 대한산부인과학회 2002 Obstetrics & Gynecology Science Vol.45 No.4
The neonatal lupus syndrome is characterized by skin lesions, hepatic and hematologic abnormalities and congenital heart block. Congenital heart block which is believed to be caused by transplacental passage of the anti-Ro (SSA)/La (SSB) antibodies from mother to infant, is known to occur in 1 in 20,000 live births. In contrast to other manifestation of neonatal lupus syndrome, which usually subside within 6 months after birth, congenital heart block is a permanent and potentially fatal complication. We experienced a case of neonatal lupus syndorme with congenital complete heart block in a newborn of asyptomatic mother with anti-Ro (SSA)/ La (SSB) antibodies.