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성인에서 호산구성 점액에 의해 발생한 중간엽증후군 2예
황하원 ( Ha Won Hwang ),김주희 ( Joo Hee Kim ),김숙연 ( Suk Yeon Kim ),이선호 ( Sun Ho Lee ),이수행 ( Soo Haeng Lee ),박성훈 ( Sunghoon Park ),황용일 ( Yong Il Hwang ),장승훈 ( Seung Hun Jang ),정기석 ( Ki Suck Jung ),이인재 ( In 대한천식알레르기학회 2016 Allergy Asthma & Respiratory Disease Vol.4 No.2
Right middle lobe syndrome (RMLS) is defined as a transient or recurrent, chronic collapse of the middle lobe of the right lung by certain pathologic conditions. RMLS is a relatively uncommon condition having multiple etiologies and various clinical presentations. Two patients were referred to Hallym University Sacred Heart Hospital, one for the treatment of coughing and the other for the treatment of pneumonia. A diagnosis of RMLS was identified through X-ray and computed tomography image evaluation for each condition. Bronchoscopy revealed mucus obstruction in the right middle lobe bronchus. Biopsy of the aspirated mucus showed mucus containing many eosinophils and Charcot-Leyden crystals. After removal of impacted mucus, clinical and radiological improvements were observed in both patients. Therefore, eosinophilic mucus impaction can be considered a potential cause of RMLS, irrespective of any underlying asthmatic symptoms. (Allergy Asthma Respir Dis 2016;4:149-153)
김숙연 ( Suk Yeon Kim ),김주희 ( Joo Hee Kim ),황하원 ( Ha Won Hwang ),김광윤 ( Kwang Youn Kim ),박성훈 ( Sung Hoon Park ),황용일 ( Young Il Hwang ),장승훈 ( Seung Hun Jang ),정기석 ( Ki Suck Jung ) 대한천식알레르기학회 2015 Allergy Asthma & Respiratory Disease Vol.3 No.5
Good’s syndrome is an acquired immunodeficiency state associated with thymoma. It is characterized by recurrent infection, autoimmune disease, and immunologic abnormality. The insufficient immunity can be managed by intravenous immunoglobulin (IVIG) replacement therapy. We describe 2 patients who presented with Pneumocystis jiroveci pneumonia and Cytomegalovirus pneumonia after thymectomy for a thymoma. Immunologic study revealed hypogammaglobulinemia with very low B-cell count, consistent with Good’s syndrome. They were successfully treated with trimethoprim/sulfamethoxazole and gancyclovir respectively, and they are all well without additional infections, receiving regular IVIG replacement. (Allergy Asthma Respir Dis 2015;3:365-369)