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이윤찬 ( Yoonchan Lee ),심경아 ( Gyeongah Sim ),김병수 ( Byung-su Kim ),현정원 ( Jungwon Hyun ),김현철 ( Hyunchul Kim ),백문성 ( Moon Seong Baek ),김철홍 ( Cheol-hong Kim ),현인규 ( In-gyu Hyun ),최정희 ( Jeong-hee Choi ) 대한천식알레르기학회 2021 Allergy Asthma & Respiratory Disease Vol.9 No.2
The Sézary syndrome is a leukemic form of cutaneous T-cell lymphoma characterized by the presence of erythroderma covering at least 80% of the body-surface area, lymphadenopathy, and the presence of clonally related neoplastic T cells with cerebriform nuclei (Sézary cells) in the blood, skin, and lymph nodes. Hypereosinophilia can be caused by hematologic malignancy with clonal abnormality, which is often associated with Sézary syndrome. Sézary syndrome has rarely been reported in Korea. However, hypereosinophilia in the Sézary syndrome has not been reported in Korea. Here, we report a case of 75-year-old man with hypereosinophila, erythroderma, and cutaneous T-cell lymphoma which was finally diagnosed as Sézary syndrome. (Allergy Asthma Respir Dis 2021;9:93-98)