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Epstein-Barr virus(EBV)와 연관된 Nasal type T/Natural Killer(NK)-cell lymphoma 1예
지두현,최지호,성경제,문기찬,고재경 울산대학교 의과대학 1996 울산의대학술지 Vol.5 No.1
Nasal type T/NK-cell lymphoma는 병리조직학적으로 응고성 괴사가 동반된 혈관중심성 침윤을 특징으로하며 T-cell과 NK-cell 항원을 모두 표현하는 면역조직화학염색 소견을 보이는 매우 드문 피부 림프종으로서 EBV와의 연관성이 흔히 보고되고있다. 저자들은 42세 여자에서 발생한, 전신적인 홍반성 구진, 판, 결절의 임상양상을 보였으며 피부 병변에서의 EBV-encoded RNA(EBER)에 대한 in situ hybridization상 양성소견을 보였고 전산화단층촬영, 골주사, 갈륨주사 등의 검사상 비강, 위장관 및 다른 내부장기 침범소견은 보이지 않아서 피부에만 국한된 경우로 사료되는 nasal type T/NK-cell lymphoma 1예를 보고하는 바이다.
지두현 ( Doo Hyun Chi ),성경제 ( Kyung Jeh Sung ),고재경 ( Jai Kyoung Koh ) 대한피부과학회 1995 大韓皮膚科學會誌 Vol.33 No.6
Background : The incidence of primary epithelial skin cancers is rising steadily, but little is khown of the clinical features of primary epithelial skin cancers, and limited data are available in Korea. Objective : Our purpose was to analyze the clinical characteristics of primary epithelial skin cancers. Methods : A retrospective analysis was conducted of 106 cases of primary epithelial skin cancers observed between 1989 and 1995. Results : 1. Basal cell curcinoma(BCC), 41 cases, was the most common skin cancer. The numbers of cases of squamosis cell carcinoma(SCC) and Bowens disease(BD) were 33 and 24, respectively. There were 3 cases of mixed type(BCC + SCC), 2 cases of Pagers disease and 3 cases of extramammary Pgets disease. 2. The average age at ciragnosis and the mean duration of disease were as follows . BCC(65.5 years old 4.34 years), SCC(70.2 years old-1.63 years), BD(59.3 years old-2.85 years) 3. The face was the most common anatomic site for BCC(93%) and SCC(70%), but the trunk was the most common site for BD. 4. The most common c inical type of BCC was the noduloulcerative type(65% ) and the solid type was t.he most frequert histologic type of BCC. 5. In histologic grading of SCC, grade I and II lesions occupied in 88% of total cases. The numbers of special variants of SCC were as follows aenoid(4), spindle cell(1), verrucous(2) Conclusions : 1. The average age of patient with primary epithelial skin cancers was older thar: in earlier reports in Korea, and was closer to the recent, reports in western count.ries. 2. The number of cases of BD was much higher than that reported previously. This emphasizeci the importance of tissue examination for the pigmented lesions of the skin, especially on the trunk and extremities. (Kor J Dermatol 1995;33(6): 1085-1090)
혈관중심성 T - 세포 림프종 : 4예의 임상 및 병리조직학적 관찰
지두현 ( Doo Hyun Chi ),서호석 ( Ho Seok Suh ),최지호 ( Jee Ho Choi ),성경제 ( Kyung Jeh Sung ),허주령 ( Joo Ryung Huh ),고재경 ( Jai Kyoung Koh ) 대한피부과학회 1996 대한피부과학회지 Vol.34 No.4
Background: Angiocentric T-cell lymphoma(AL) is a rare subtype of cutaneous T-cell lymphoma and recently many cases have been reported from Taiwan and Japan. But little is known about the clinical and histopathologic features of AL and few data are available in Korea. Objective : Our purpose was to characterize the clinical and histopathologic features of the specific cutaneous manifestauons of AL and to investigate the association with Epstein-Barr virus (EBV), Methods : Clinical records and histopathologic evaluation of skin biopsy specimens from four patients with AL were reviewed. We also performed immunohistochemical staining using monoclonal antibodies against, surface markers of lymphocytes and in situ hybridization for EBV-encoded RNA(EBER) in lesional skin. Results : 1. The most common clinical finding in our patients was indurated plaque predominantly on the trunk. 2. The common histopathologic finding in skin biopsy specimens from all four patients was angiocentric, angioinvasive, and angiodestructive infiltrate containing atypical lymphocytes. 3. In three of four patients, EBER was demonstrated in lesional skin by in situ hybridization. Conclusion : AL is an unique clinicopathologic entity showing strong association with EBV in Korea. (Kor J Dermatol 1996;34(4): 555-560)
지두현 ( Doo Hyun Chi ),김현수 ( Hyun Su Kim ),성경제 ( Kyung Jeh Sung ),문기찬 ( Kee Chan Moon ),고재경 ( Jai Kyoung Koh ) 대한피부과학회 1995 대한피부과학회지 Vol.33 No.4
Granular cell tumors were originally described in 1926 by Abrikossoff as myoblastic myomas. They usually occur as solitary tumors but can be multiple in about 10% of cases. They have a predilection for the skin, subcutaneous tissue and tongue, but also occur in many other organs. We report a case of solitary granular cell tumor on the palm. This is a very unusual location of this disease which merits consideration. (Kor J Dermatol 19S5;33(4): 780-783)
Cutaneous Angiocentric T-cell Lymphoma
Choi, Jee-Ho,Chang, Sung-Eun,Chi, Doo-Hyun,Jang, Kyoung-Ae,Koh, Jai-Kyoung 울산대학교 의과대학 1995 울산의대학술지 Vol.4 No.2
Angiocentric T-cell lymphoma는 혈관중심성의 부정형 림프구 침윤을 특징으로 하는 매우 드문 피부 T세포 림프종의 한 아형으로서 전세계적으로 대만, 일본등 동아시아 국가에서 주로 보고되고 있다. 저자들은 62세 여자에서 발생한, 국소적으로 비교적 경계가 명확한 홍반성 판의 임상양상을 보였으며 전신 증상은 동반되지 않았고 전산화단층촬영, 골주사, 갈륨주사 등의 검사상 내부장기 침범소견은 보이지 않아서 피부에만 국한된 경우로 사료되는 Angiocentric T-cell lymphoma 1예를 보고하는 바이다.