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21-Hydroxylase결핍의 선천성 부신증식증에 의한 여성반음양 치험 1 예
주갑순,김해중,박상진 대한산부인과학회 1990 Obstetrics & Gynecology Science Vol.33 No.4
위와 같이 CAH중 Heterozygous 21-hydroxylase의 결핍으로 인한 것으로 사료되는 여성 반 음향 1례를 치험하였기에 간단한 문헌 고찰과 함께 보고하는 바이다. Female hermaphroditism is a condition in which individuals with a 46, XX chromosomal constitution differentiate partially as phenotypic males, usually manifesting masculinization of the external genitalia. Most female hermaphrodites have one of the types of congenital virilizing adrenal hyperplasia. Congenital adrenal hyperplasia is an inborn error transmitted by an autosomal recessive gene and may be due to a defect in any of the enzymic steps in the biosynthesis of cortisol. Most affected individuals have a failure of 21-hydroxylation which prevents the conversion of 17-hydroxyprotesterone to 11-deoxycortisol. A defect in 21-hydroxylase leads not only to inefficient formation of cortisol but also to excessive production of adrenal androgens causing virilization. A case of female hermaphroditism due to congenital adrenal hyperplasia is presented with a brief review of the literature.
주갑순,Ju, Gap-Soon 대한생식의학회 1977 Clinical and Experimental Reproductive Medicine Vol.4 No.2
A total of 636 patients of primary infertility were analyzed by computer on the basis of statistical evaluation of etiological factors and therapy with the outcome of the pregnancy. In this report, it included the results of the study analyzed the single etioligic factors responsible for the primary infertility with the outcome of the pregnancy. 1. Two hundred and fourty one patients out of a total 636(37.9%) achieved pregnancy. 2. Four hundred and fifty nine patients out of a total 636(72%) had a single etuiologic factor responsible for the primary infertility. 3. One hundred and seventy six patients out of 459 parients (38.3%) who had a single etiologic factor responsible for the primary infertility achieved a pregnancy. 4. The endometriosis was the most frequent responsible factor for the primary infertility. 5. The success rate of the pregnancy was different in each etioligic factor responsible for the primary infertility. The highest success rate of the pregnancy was in the patients who had the intermediate factor responsible for the primary infertility as much as 66.7% of the patients. 6. The expectancy of the pregnancy in terms of the duration of the therapy and the follow-up was variable and depended upon the etiologic factor of the primary infertility.