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원발성 담즙성 견경변증과 Isolated pulmonary hypertension을 동반한 미만성 경피증(Diffuse scleroderma)
장현규 ( Hyun Kyu Chang ),정상식 ( Sang Sig Chung ),정행섭 ( Haing Sub R. Chung ),이성희 ( Sung Hee Lee ),허환 ( Hwan Herr ) 대한류마티스학회 1997 대한류마티스학회지 Vol.4 No.2
Primary biliary cirrhosis is frequently associated with a variety of disorders presumed to be autoimmune in nature, such as Sjogren`s syndrome, scleroderma, rheumatoid arthritis, systemic lupus erythematosus, and autoimmune thyroiditis. Scleroderma has been recognized in association with primary biliary cirrhosis. Most cases present as the CREST (calcinosis cutis, Raynaud`s phenomenon, esophageal dysmotility, sclerodactyly, and telangiectasia) syndrome. Isolated pulmonary hypertension develops in a small proportion of patients, nearly all of whom have limited cutaneous involvement. We report a case who has diffuse scleroderma associated with primary biliary cirrhosis and isolated pulmonary hypertension.
문희범,정두련,진재용,정상식,김광훈,송재훈,주용선 대한감염학회 1993 감염 Vol.25 No.3
Malakoplakia is a relatively rare chronic inflammatory disease, usually involving the bladder and upper urinary tract. It represents a peculiar inflammatory response to infection by gram negative bacteria, most frequently by E. coli. Malacoplakia is characterized by the presence of large histiocytes called "von Hansemann cells" and small basophilic inclusion called "Michaelis-Gutmann bodies". We report a case of malakoplakia involving renal parenchyme and perinephric space, also associated with E. coli empyema. The patient was a 66-year-old female with a long history of steroid treatment for rheumatoid arthritis. The patient also had a history of diabetes mellitus. The patient was admitted to the Asan medical Center because of high fever and pleuritic pain on right chest. The chest X-ray showed pleural effusion on right chest, which was characterized by low pH(6.3), markedly increased WBC count (63360/㎖, poly 94%) and increased LDH level (43643 ICU) on thoracentesis. The culture of pleural fluid revealed E. coli, which was sensitive to cefazolin and gentamicin. The chest and abdominal CT scan showed huge mass shadow extending from right diaphragm to posterior aspect of right kidney as well as pleural effusion on right chest. Despite prolonged therapy with cefazolin and gentamicin, mass shadow progrssively increased in size. PCNB showed typical Michaelis-Gutmann bodies suggestive of malakoplakis. Ultimately, the patient was treated with sugical resection and prolonged course of parenteral antibiotics.