http://chineseinput.net/에서 pinyin(병음)방식으로 중국어를 변환할 수 있습니다.
변환된 중국어를 복사하여 사용하시면 됩니다.
症例(증례) : 골수에서 발생한 CD34, CD99를 동반 발현하는 원시성 신경외배엽 종양
임호영 ( Ho Young Yhim ),김성식 ( Sung Sik Kim ),민경훈 ( Kyung Hoon Min ),이나리 ( Na Ri Lee ),송은기 ( Eun Kee Song ),곽재용 ( Jae Yong Kwak ),최삼임 ( Sam Im Choi ),임창열 ( Chang Yeol Yim ) 전북대학교 의과학연구소 2004 全北醫大論文集 Vol.28 No.1
Primitive neuroectodermal tumor (PNET) is a small round cell neoplasm that develops in children and young adults. The identification of immunoreactivity for CD99 is important for diagnosis of PNET. But, there have been no reports that PNET is immunoreactive for CD34. Therefore, we report a case of PNET developed in a 26 year-old man, which occurred primarily in the bone marrow. He was presented with hypercalcemia and pancytopenia. Bone marrow aspiration biopsy revealed that tumor cells were composed of round cells with hyperchromatic unclear chromatin and minimal eosinophilic cytoplasm. Rosette formations were occasionally observed. The tumor cells were diffusely immunopositive for CD99 and CD34, while they were immunonegative for vimentin, neuron specific enolase, cytokeratin, desmin, leukocyte common antigen, synaptophysin. He was treated with chemotherapy after general medical supportive care, and still alive during the 6 months of follow-up.
症例(증례) : 특발성 혈소판 감소성 자반증과 동반된 Takayasu 동맥염 1예
민경훈 ( Kyung Hoon Min ),임호영 ( Ho Young Yhim ),정혜진 ( Hey Jin Jeong ),이민희 ( Min Hee Lee ),김성국 ( Sung Kuk Kim ),이기훈 ( Ki Hoon Lee ),정수진 ( Su Jin Jung ),이가영 ( Ka Yeong Yi ),이선화 ( Sun Hwa Lee ),정치량 ( Chi Ry 전북대학교 의과학연구소 2004 全北醫大論文集 Vol.28 No.1
Takayasu 동맥염과 특발성 혈소판 감소성 자반증은 두 질환 모두 발병원인 및 병태생리에 있어 자가면역성이 중요한 역할을 한다고 할 수 있다. 본 저자들은 Takayasu 동맥염과 특발성 혈소판 감소성 자반증이 동반된 57세 남자 증례를 보고하는 바이다. 본 증례 남지는 1년전 특발성 혈소판 감소성 자반증을 전단받았다. 복통 및 혈변배설을 주소로 내원한 환자는 좌측 위팔동맥(Left brachial artery)의 맥박이 감소된 소견을 보였으며, 청진 소견상 복부 잡음(abdominal bruit) 소견 을 보였고, 흉복부 컴퓨터 단층 촬영 및 3차원 대동맥 혈관 재구성 컴퓨터 단층 촬영 소견 상 좌측 쇄골밑 동맥(left subclavian artery), 흉복부 대동맥(thoracoabdominal aorta), 복강 동맥(celiac trunck), 상 창자간막 동맥(superior mesenteric artery)의 다발성 혈관염 소견을 보여 Takayasu 동맥염에 합당한 소견을 보였다. 고용량 스테로이드 치료 후, 환자의 임상적 증상과 혈침속도가 호전되었다. Takayasu`s arteritis (TA), a chronic inflammatory arteriopathy of unknown etiology, lead to both stenotic and ectatic changes, particularly occlusion. The common sites of involvement are the aorta and its main branches, and pulmonary artery. A specific etiology for TA has not been found. Autoimmunity has been found to play an important role in TA, and association with various autoimmune disorders has been reported in selected cases. There is no case report that TA coexists with idiopathic thrombocytopenic purpura (ITP). We report a case of TA associated with ITP in a 57-year-old man. He suffered from ITP 1 years earlier. On admission, the patient presented with periumbilical abdominal pain. TA diagnosed on the basis of decreased pulsation of the left brachial artery, bruit over the abdominal aorta and multifocal vasculitis in the left subclavian artery, thoracoabdomianl aorta, celiac trunk and superior mesenteric artery on thoracoabdominal computerized tomography and 3-D aortic arch reconstruction computerized tomography. Following the high dose steroid therapy, his clinical symptoms improved and erythrocyte sedimentation rate decreased.
症例(증례) : 간헐적으로 육안적 혈뇨를 동반한 Nutcracker Syndrome 1예
김성식 ( Sung Sik Kim ),임호영 ( Ho Young Yhim ),정수진 ( Su Jin Jeong ),이상연 ( Sang Youn Lee ),김성국 ( Sung Kuk Kim ),이가영 ( Ka Yeoung Yi ),이선화 ( Sun Hwa Lee ),유창우 ( Chang Woo Rheu ),강경표 ( Gyung Pyo Kang ),이식 ( S 전북대학교 의과학연구소 2004 全北醫大論文集 Vol.28 No.1
Nutcracker syndrome (renal vein entrapment syndrome) refers to compression of left renal vein between aorta and superior mesenteric artery that results in elevation of pressure in left renal vein and development of collateral veins. This syndrome occurs in relatively young and previously healthy patients and is characterized by intermittent gross hematuria due to left renal vein hypertension, at times associated with flank pain, abdominal pain or varicocele. We report a 22 year ole male patient with this syndrome presented with intermittent gross hematuria, proteinuria for 2 months. Urinalysis revealed protein (3+), blood (++), and RBC (many/HPF). Excretory urography in resting state and cystoscopy showed no remarkable finding. Renal venography showed the pressure gradient between left renal vein and inferior vena cava was 6 mmHg. The nutcracker syndrome should be considered as one of the causes of nonglomerular hematuria. All patients with unexplained severe left flank or abdominal pain, or unilateral hematuria from the left on cytoscopy, should be studied by selective renal venography and pressure measurement in inferior vena cava and renal veins. The paitent with this nutcracker syndrome could be treated with conservative treatment.
박성철 ( Sung Chul Park ),정주영 ( Joo Young Jung ),이현 ( Hyun Lee ),박호성 ( Ho Sung Park ),전소연 ( So Yeon Jeon ),임호영 ( Ho Young Yhim ),이나리 ( Na Ri Lee ),곽재용 ( Jae Yong Kwak ),임창열 ( Cahng Yeol Yim ),송은기 ( Eun K 전북대학교 의과학연구소 2012 全北醫大論文集 Vol.36 No.1
위의 암육종은 암종과 육종의 특징을 보이는 조직이 혼재되어 있는 형태의 종양으로 매우 드물게 발생하는 악성종양이다. 저자들은 위 암육종을 수술적 절제로 치료하였으나 짧은 시간 만에 재발 및 간전이가 된 증례를 경험하게 되어 보고하는 바이다. 수술적으로 절제되었던 종 양 및 재발 이후 다시 시행된 조직검사 모두에서 조직은 암종의 형태와 육종의 형태를 각각 보였으며 면역염색에 의해서도 서로 각기 다른 염색 상태를 보였다. 암육종은 매우 진행이 빠르고 예후가 불량하기 때문에 수술적 절제가 더욱 중요하다고 할 수 있겠다. 또한, 위암에 대 한 병리조직검사 시에는 드물지만 이러한 형태의 혼재된 종양이 아닌지에 대한 세심한 주의를 요하겠다.
진행성 골수섬유화증을 동반한 역형성 대세포 림프종 환자에게 시행된 자가 말초혈액 조혈모세포 이식
이나리 ( Na Ri Lee ),송은기 ( Eun Kee Song ),임호영 ( Ho Young Yhim ),장규윤 ( Kyu Yun Jang ),최삼임 ( Sam Im Choi ),임창열 ( Chang Yeol Yim ),곽재용 ( Jae Yong Kwak ) 대한내과학회 2010 대한내과학회지 Vol.79 No.1
Myelofibrosis is a myeloproliferative neoplasm characterized by abnormal bone marrow megakaryocyte proliferation with reticulin and collagen fibrosis, leukoerythroblastosis, anemia, increased level of serum lactate dehydrogenase and splenomegaly. Myelofibrosis associated with malignant lymphoma is rare and survival rates appear to have been poor. Herein, we describe our experience in a patient who remained in complete remission with high-dose therapy (HDT) with autologous peripheral blood stem cell transplantation (PBSCT) for ALK-negative ALCL presenting with rapidly progressing myelofibrosis. (Korean J Med 79:77-81, 2010)
症例(증례) : 관상동맥 스텐트로 치료한 베체트병에 동반된 급성 심근경색증 1예
정혜진 ( Hey Jin Jeong ),김세인 ( Se In Kim ),김소리 ( So Ri Kim ),이규선 ( Kyu Sun Lee ),고은영 ( Eun Young Ko ),김성훈 ( Seong Hun Kim ),김성식 ( Sung Sik Kim ),임호영 ( Ho Young Yhim ),민경훈 ( Kyung Hoon Min ),이상일 ( Sang Il 전북대학교 의과학연구소 2004 全北醫大論文集 Vol.28 No.1
베체트병은 반복되는 아프타성 구강궤양과 성기궤양 및 포도막염과 같은 눈의 반복적인 염증성 병변을 특징으로 하는 전신 질환이다. 베체트병에 동반된 심근경색은 매우 드물어서 소수의 증례만이 보고 되고 있다. 저자들은 베체트병 환자에서 발생한 심근 경색증 1예를 경험하였기에 보고하는 바이다. Behcet`s disease is a systemic disease of unknown cause, belonging to vasculitis pathologically. It rarely involves the coronary arteries. Coronary arteritis may lead to myocardial infarction and death, and the management of coronary lesions due to Behcet`s disease has been described only in a small number of patients. We experienced a -36-year-old man with Behcet`s disease who presented with acute coronary syndrome, and underwent balloon angioplasty and coronary stent implantation. The reduction of the coronary stenosis by balloon angioplasty induced immediate relief of chest pain. He has been still in reltively good health without chest pain during the 24 months of follow-up.
박진경 ( Jin Kyoung Park ),소민석 ( Min Seok So ),전소연 ( So Yeon Jeon ),박윤지 ( Yuen Ji Park ),임호영 ( Ho Young Yhim ),곽재용 ( Jae Yong Kwak ) 전북대학교 의과학연구소 2011 全北醫大論文集 Vol.35 No.1
본 저자들은 비내강 종괴로 내원한 79세 남자 환자에서 시행한 조직검사에서 광범위 B형 대세포 림프종을 진단하였고 병기 설정 을 위해 시행한 골수검사에서 비증상성 다 발성 골수종이 동반된 증례를 경험하여 문 헌 고찰과 함께 보고하는 바이다. Although several cases of coexisting multiple myeloma and lymphoma have been reported, the coexistence of multiple myeloma and non-Hodgkin B cell lymphoma is a rare events. Recently, a 79-year-old man was presented with nasal cavity mass. Microscopic examination of nasal cavity mass revealed diffuse large B-cell lymphoma. Bone marrow showed increased immature plasma cell (20%) and serum protein electrophoresis showed monoclonal gammopathy (0.95g/L). But, he was asymptomatic and had no lytic bone lesions or other clinical features of myeloma. So, he was diagnosed smoldering multiple myeloma with diffuse large B-cell lymphoma. The patient received five cycles of R-CHOP (rituximab,cyclophosphamide,daynorubicin, vincristin, prednisolone) with intrathecal MTX chemotherapy, but died of pneumonia.
방사선치료로 완전관해에 이른 Helicobacter pylori 음성인 위의 MALT 림프종
전소연 ( So Yeon Jeon ),김강 ( Kang Kim ),김선희 ( Sun Hee Kim ),김승범 ( Seung Bum Kim ),문진창 ( Jin Chang Moon ),박윤지 ( Yun Ji Park ),정래영 ( Lae Young Jung ),임호영 ( Ho Young Yhim ),곽재용 ( Jae Yong Kwak ) 전북대학교 의과학연구소 2011 全北醫大論文集 Vol.35 No.1
위에서 발생하는 MALT 림프종은 92% 이상에서 H. pylori 감염과 연관되어 있어 H. pylori의 제균요법이 일차 치료로 추천되고 있다. H. pylori 음성인 위의 MALT 림프종은 빈도가 낮고 병인 또한 밝혀진 바가 없어 아직까지 정립된 표준 치료는 없다. H. pylori 음성인 위의 MALT 림프종 환자 중, 병기 IE와 IIE 에서는 방사선 치료로 완전 관해에 이를 수 있다는 보고가 있다. 저자들 은 H. pylori 음성인 위의 MALT 림프종 환자에서 방사선 단독 치료만으로 11개월째 관해를 유지하고 있는 증례를 보고하는 바 이다. Most gastric MALT (mucosa associated lymphoid tissue) lymphomas are associated with Helicobacter pylori infection. Therefore, H. pylori eradication therapy is generally accepted first-line therapy for H. pylori-positive gastric MALT lymphoma. However, among the gastric MALT lymphoma, 5-10% patients have no evidence of H. pylori infection. There is no standard therapy for H. pylori-negative gastric MALT lymphoma. Currently, radiation therapy is the effective treatment for H. pylori-negative or antibiotic-resistant localized gastric MALT lymphoma. Herein, we describe a 65-year-old man with H. pylori-negative gastric MALT lymphoma who achieved complete remission by radiation monotherapy.
중복 원발암의 증례 1예: 위선암 및 방사선조사후 소장에서 발생한 혈관육종
김강 ( Kang Kim1 ),김선희 ( Sun Hee Kim ),문진창 ( Jin Chang Moon ),박윤지 ( Yoon Ji Park ),박진경 ( Jin Kyung Park ),서승영 ( Seung Young Seo ),정래영 ( Lae Young Jung ),임호영 ( Ho Young Yhim ),곽재용 ( Jae Yong Kwak ) 전북대학교 의과학연구소 2011 全北醫大論文集 Vol.35 No.1
Angiosarcomas are rare malignant neoplasms, which mainly occur on the skin and superficial tissue. Angiosarcoma in the small intestine after radiation therapy is very rare and there are less than 20 cases of small-intestine angiosarcoma after pelvic irradiation. We report a case of double cancer with gastric adenocarcinoma and postradiation angiosarcoma of the small intestine which has been diagnosed 20 years after pelvic irradiation therapy for uterine cervical cancer.