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증 례 : 최소변화콩팥병증이 동반된 골수형성이상증후군 환자에서 스테로이드 치료
이상아 ( Sang Ah Lee ),임장환 ( Jang Hwan Lim ),장지훈 ( Ji Hun Jang ),장순희 ( Soon Hee Chang ),곽은경 ( Eun Kyoung Kwak ),이덕현 ( Duk Hyun Lee ),이선아 ( Sun Ah Lee ) 대한내과학회 2016 대한내과학회지 Vol.90 No.1
Glomerulonephritis associated with malignancy is deemed to be paraneoplastic glomerulonephritis. Myelodysplastic syndrome (MDS) is a group of heterogeneous clonal hematopoietic stem cell disorders characterized by impaired hematopoietic cell differentiation and cytopenia. The pathophysiology of MDS is thought to be immune-mediated in part. A few reports have documented various forms of glomerulonephritis in patients with MDS and suggested that immune dysregulation is important in the development of paraneoplastic glomerulonephritis. Here, we report a patient with MDS and refractory anemia with excess blast-2 accompanied by minimal change nephrotic syndrome. The patient was treated with prednisolone, and the nephrotic-range proteinuria and pancytopenia improved markedly. (Korean J Med 2016;90:63-67)