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심한 호중구 감소증을 보인 X-관련성 범저감마글로불린혈중 1례
이경연 ( Kyoung Yeon Lee ),이동규 ( Dong Kyu Lee ),박준은 ( Jun Eun Park ),이재호 ( Jae Ho Lee ),이명익 ( Myung Ik Lee ) 대한소아알레르기호흡기학회 2002 소아알레르기 및 호흡기학회지 Vol.12 No.4
저자들은 폐렴치료 중 1개월 이상 심한 호중구 감소증이 지속되었던, 유전자 분석으로 확진된 XLA 환아를 경험하였기에 문헌고찰과 함께 보고하며, 만성 혹은 반복되는 감염의 증상과 함께 호중구 감소증이 나타날 때 XLA를 포함한 면역결핍질환을 의심하는 것이 필요하다고 사료된다. X-linked agammaglobulinemia(XLA) is characterized by markedly reduced number of B lymphocytes, panhypogammaglobulinemia, recurrent bacterial infections in the first few years of life because of genetic defect for Bruton`s tyrosine kinase at Xq22 region. A
한국 소아 천식 환자의 보호자 삶의 질에 대한 설문 개발 및 유용성 평가를 위한 다기관 공동 연구
차재국(Jae Kook Cha),오재원(Jae Won Oh),홍수종(Soo Jong Hong),이혜란(Hae Ran Lee),이명익(Myung Ik Lee),김규언(Kyu Earn Kim),이준성(Joon Sung Lee),이하백(Ha Baik Lee),이상일(Sang Il Lee) 대한천식알레르기학회 2000 천식 및 알레르기 Vol.20 No.3
Background: and objective: Asthma is the most common chronic disease among children. Thus, when children have asthma, it can have a significant impact on health-related quality of life, not only for children, but also for parents and family. We developed to measure asthma- specific quality of life in caregivers of children with asthma age 7~17 years and evaluated the measurement properties of the questionnaire. Materials and method: The questionnaire of caregivers of children with asthma include 13 items in two areas(activity limitation-4 items, emotional function-9 items) and the response options for each item are on a 5-point scale where 1 indicates maximum impairement and 5 indicates no impairement. Results are expressed as the mean score for overall quality of life as well as for each of the domains. At follow-up visit, we asked caregivers whether they had experienced any change in their overall quality of life related to their children's asthma since the previous visit. They responded on a 11-point scale from -5(a very great deal worse) to 0(no change) to +5(a very great deal better). We recruited 195 caregivers of children with asthma from thirty-three general hospitals and evaluated the measurement properties of the questionnaire. Result: The questionnaire of caregivers of children with asthma showed excellent responsiveness in changed group, but the change in score of stable and changed group has no difference. It was reproducible in subjects who are stable. There was no longitudinal and cross- sectional correlations between caregiver's questionnaire score and the child's asthma status, while cross-sectional correlations were found between caregiver's questionnaire score and PEFR Conclusion The questionnaire of caregivers of children with asthma is simple and easy to use, and is applicable.
한국 호아 천식 환자의 삶의 질에 대한 설문 개발 및 유용성 평가를 위한 다기관 공동 연구
차재국(Jae Kook Cha),오재원(Jae Won Oh),홍수종(Soo Jong Hong),이혜란(Hae Ran Lee),이명익(Myung Ik Lee),김규언(Kyu Earn Kim),이준성(Joon Sung Lee),이하백(Ha Baik Lee),이상일(Sang Il Lee) 대한천식알레르기학회 2000 천식 및 알레르기 Vol.20 No.3
Background:and object: Traditional asthma outcome measures such as symptoms, spirometry. And medication requirements usually provide valuable information about the asthmatic status but they rarely capture the functional impairments. Thus, many clinicians are increasingly recognizing the importance of an assessment of health-related quality of life(HRQL) as an outcome measure in asthma. We developed a questionnaire to measure asthma-specific quality of life in Korean children and evaluated the measurement properties. Materials and methods : The questionnaire for children with asthma included 14 items in three domains (symptoms-6 items, activity limitation-4 items, and emotional function-4 items) and the response options for each item were on a 5-point scale where 1 indicated maximum impairment and 5 indicated no impairment. Results were expressed as the mean score for overall quality of life as well as for each of the domains. At #follow-up clinic visit, patients completed global assessment of change related to their symptoms, activities and emotions. We recruited children (7-17 years of age) with asthma from thirty-three general hospitals. Results Data from 214 patients(144 boys and 70 girls) who completed the questionnaire were analyzed. The mean age was 10.0 years and the disease severity consisted of mild intermittent (26.6%), mild persistent(36.0%), moderate persistent(32.2%), and severe persistent (3.3%). The questionnaire for children with asthma showed a high index of responsiveness, reproducibility, and both longitudinal and cross-sectional correlations with the conventional asthma indices and with the questionnaire score. But there was no relationship between changes in questionnaire score of the domain of emotional function and changes in FEV1 or PEFR. Conclusion: The questionnaire of children is straight forword, and easy to apply.
Mycoplasma pneumoniae 폐렴의 임상적 고찰
이은경(Eun Kyung Lee),홍영진(Young Jin Hong),이명익(Myung Ik Lee),안돈희(Don Hee Ahn),손근찬(Keun Chan Sohn) 대한소아알레르기호흡기학회(구 대한소아알레르기 및 호흡기학회) 1993 소아알레르기 및 호흡기학회지 Vol.3 No.2
N/A A clinical study was made on 261 cases of Mycoplasma pneumoniae pneumonia from January 1985 to June 1992. Those patients were composed of 220 in-patients and 41 out-patients. The results were as follows. 1. Annual distribution showed increased incidence in 1990 and seasonal distribution showed increased incidence in spring and autumn. 2. Out of 261 cases, 147 cases were male, 114 cases were female and high incidence was in the age of 1 to 6 years (75.5%). Male to female ratio was 1.4:1. 3. The cases which had allergic history were 53 cases. Bronchial asthma were 22 cases and atopic dermatitis were 11 cases. 4. Sinusitis was the most common concomitant disease. 5. Cough was the most common chief complaint (93.5%) and duration was less than 7 days on initial visit (48.1%). 6. The most common auscultatory finding was coarse breathing sound (180 cases, 69%) and then followed by rale and wheezing. 7. Leukocyte counts in peripheral blood were most common in the range of 5,001-10,000/㎣ (53.1%). Erythrocyte sedimentation rate were in the range of 10-19㎜/hr. Positive CRP cases were 86 cases (36.3%). 8. Radiologic finding of pulmonary infiltration was the most common in right lower lobe.
제대 혈청 IgE 치 ( Ultra RIA ) 에 대한 고찰
강진섭(Jin Seop Kang),고재욱(Jae Wook Ko),홍영진(Young Jin Hong),안돈희(Don Hee Ahn),이명익(Myung Ik Lee) 대한소아알레르기호흡기학회(구 대한소아알레르기 및 호흡기학회) 1995 소아알레르기 및 호흡기학회지 Vol.5 No.1
N/A The objectives of this report is to evaluate and determine the normal level of cord serum IgE which is regarded as one of successful parameters , predicting the development of atopic disease in neonate. Forty mothers who were admitted to NMC for the purpose of fullterm delivery and their newborns were investigated. We had titrated cord serum IgE levels by new method , IgE Ultra RIA, and also checked maternal serum IgE by IgE RIA method. Additionally, allergic and smoking histories of mothers and informations of neonate were taken for comparison of cord serum IgE levels . The following results were obtained. 1. The median value of cord serum IgE measured by Ultra RIA method was 0.22(range : 0.11-2.19) IU/ml and that of maternal serum IgE by RIA method was 59.5(range 6-448) IU/ml. 2. There was no significant correlation between log10 value of maternal and cord serum IgE. 3. According to the sex and birth weight, there was no significant differences of cord serum IgE levels. 4. According to birth order , cord serum IgE levels of first babies showed significantly higher than those of others. 5. According to allergic family history and maternal smoking history , there was no significant difference of cord serum IgE levels .
신생아, 영아 및 소아 발열 환아에 있어서 CRP, 백혈구수, 혈침치, 중성구 및 질병분포의 비교 관찰
안돈희,조병래,이명익,손근찬 대한감염학회 1988 감염 Vol.20 No.3
We studied total 413 cases of febrile neonates, infants and children, which were divided into 232 cases of CRP positive group and 181 cases of CRP negative group, and compared ESR, WBC, polymorphonuclear leucocyte count, band form neutrophil and disease distribution in both group. We concluded that CRP is important and may be valuable screening test for the detection of bacterial infection in febrile and infectious neonates, infants and children.