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만성 염증성 탈수초 다발성 신경근병증이 동반된 낭창성 신염
이규백(Kyu Beck Lee),김향(Hyang Kim),이상종(Sang Jong Lee),박찬필(Chan Pil Park),박문향(Moon Hyang Park),박범준(Bum Joon Park),김현승(Hyun Seung Kim),이한보(Han Bo Lee),이준(Jun Lee),오재인(Jae In Oh) 대한신장학회 2000 Kidney Research and Clinical Practice Vol.19 No.3
Systemic lupus erythematosus(SLE) is a multisys-temic disease. Peripheral neuropathy occurs in about 10% of patients with SLE. Chronic inflammatory demyelinating polyneurpathy has been reported rarely in SLE. We experienced a case of chronic inflammatory polyneuropathy in lupus nephritis. 32-year-old housewife presented to chronic progressive muscle weakness and heavy proteinuria. Kidney biopsy showed compatible with lupus nephritis (WHO Class V, membranous nephropathy). Nerve conduction studies showed reduction in conduction velocity and sural nerve biopsy revealed demyeli-nating polyneuropathy. Steroid therapy led to improvement in clinical symptoms and proteinuria.
실내디자인에 있어 투명성 재료의 표현 특성에 관한 연구
이규백(Lee, Gyoobaek) 한국실내디자인학회 2009 한국실내디자인학회논문집 Vol.18 No.4
Design trend, transparency, which has been developed under a reflection of current periodic environment, has been exposed to people all over the world through varieties of architecture facade and interior space. As interior space follows this trend, which has difference in showing space from the past, transparency becomes an important measure of showing openness of certain space. Main objective of this research is to understand a characteristics of materials that leads transparency a important measure to the modern interior design, and this will set the range to this applicable materials for appropriate areas of defining transparency in an interior. Characteristic uses of transparent materials found in this research which leads transparency into interior space are described below: First, there are two perspectives in transparency. One is visibility and material wised transparency and the other is conditional and spacial wised transparency. With this knowledge, we can expand a level of transparency with ideas such as clarity, opacity, visible transmission, and reflection, and this broadened range will vary the acceptable materials used to show transparency. Second, transparent materials are used with many different purposes in modern interior space as furnitures, sanitary fixtures, partitions, and other structures. With using modern technology in reforming this materials brought new methods in structure composing. last, transparent materials" expnt pable characteristics made modern interior space to have a control over spacial homogeneity, a simplified octlines, weakened boundaries, and compositional effects by interference and vision.
이규백(Kyu Back Lee),변현주(Hyun Ju Byoun),최태승(Tae Seung Choi),김선숙(Sun Sook Kim),조원용(Won Young Cho),김형규(Hyoung Kyu Kim),정태시(Tae See Chung) 대한내과학회 1990 대한내과학회지 Vol.39 No.2
N/A Carbon disulfide (CS2) is a volatile, colorless liquid and has an aromatic odor at room temperature. It has been used as a solvent for the spinning process in viscose rayon plants and also in cellophane and agricultural medicine plants, We experienced 38 workers who possibly suffered from chronic CS2, intoxication. Accordingly, we are reporting our opinions on synthetics and their effects on humanes. The time of exposure to CS2, gas was noted from 2 to 19years/(mean±SD 12±4.5yrs). The age range was from 30 to 64 years. With respect to clinical findings, patiets complained of neuralgia (86.8%), headache (63. 2%), memory disturbance (44.7%), visual dimness (36.8%), decreased sexual libido (29.6%), and hypertension (26.3%). The laboratory findings showed proteinuria in eight patients, azotemia in three patients, anemia in three patients and low HDL-cholesterol level in eight patients. Among the 38 workers, there was polyneuropathy in 13 patients by EMG, sensory neural hearing loss in nine patients, hemorrhage and exudate in eight patients by funduscopy, and cortical dysfunction in six patients by EEG.
상염색체 우성 다낭신 환자에서 신장 해부학적 지표에 따른 고혈압과 신기능의 변화
이규백(Kyu Beck Lee),김향(Hyang Kim),이영래(Young Rae Lee) 대한신장학회 2001 Kidney Research and Clinical Practice Vol.20 No.2
상염색체 우성 다낭신(ADPKD)은 다낭신 유전자를 받은 환자에서 점진적으로 신장에 낭종들의 수와 크기가 커져서 신혈관과 신실질을 압박하여 고혈압, 신부전을 발생시킨다. 그리고 ADPKD 환자에서 고혈압과 신부전 발생 이전부터 신장의 해부학적 변화가 발생한다. 따라서 오랜 기간의 임상경과를 가진 ADPKD에서 신장 해부학적 지표에 따른 고혈압과 신기능 변화를 평가하는 것은 중요하다. 그리고 신장 해부학적 지표를 ADPKD의 임상경과를 예측할 수 있을지를 알아보는 것은 의미 있다. 본 연구에서 강북삼성병원을 내원한 ADPKD환자 가운데 복부초음파검사로 진단하고, 해부학적 구조를 정확히 볼 수 있는 복부 전산화단층촬영을 시행한 67명의 환자를 대상으로 신장 해부학적 지표에 따른 고혈압, 신기능을 비교하였다. 한명의 방사선과 전문의가 복부 전산화단층촬영 필름을 분석하여 신장의 해부학적 지표로 신장의 길이, 용적, RSI(anatomical renal severity index), 최대 신낭종직경을 측정하였다. ADPKD 환자(평균 연령 45±12세, 남녀비42:25) 가운데 고혈압은 41명(61%)에서 있었으며, 신기능 부전 (크레아티닌 청소율50mL/min/1.73m2 이하)은 15명(22%)에서 있었다. 정상 혈압 군에 비하여 고혈압 군에서 신장길이, 신장용적, RSI, 최대 신낭종직경 모두 유의하게 증가되어 있었다(p<0.01)(신장용적 360±154mL/1.73 m2 대 833±585mL/1.73 m2 ). 정상 신기능 군에 비하여 신부전 군에서 신장길이, 신장용적, RSI, 최대 신낭종직경 모두 유의하게 증가되어 있었다(p<0.01)(신장용적499±335mL/1.73 m2 대 1171±700mL/1.73m2 ). 환자의 크레아티닌 청소율은 신장 해부학적 지표인 신장길이(r= -0.39), 신장용적(r= -0.49), RSI(r= -0.39), 최대 신낭종직경(r= -0.38)과 유의한 상관관계가 있었다(p<0.01). 본 연구 결과 ADPKD 환자에서 신장 해부학적 지표인 신장길이, 신장용적, RSI, 최대 신낭종직경은 고혈압, 신기능과 상관관계를 가지고, 고혈압 군과 신부전 군에서 증가되어 있다. ADPKD에서 신장의 낭종이 많아지고, 신장이 커질수록 고혈압이 발생하고, 신기능이 감소함을 객관으로 증명하였다. 향후에 ADPKD환자의 임상경과를 보는데 이러한 신장 해부학적 지표를 유용하게 사용할 수 있을 것으로 생각된다. Autosomal dominant polycystic kidney disease (ADPKD) is a common hereditary disorder, and its major morbidities are hypertension and renal failure. It is a characteristic feature of ADPKD that renal cysts increase in size and number with age continuously. Hypertension and renal failure in ADPKD result from compression of residual normal renal parenchyma by expanding cysts, since renal tissue is trapped within the poorly distensible renal capsule. Renal structural deformities in ADPKD occur prior to hypertension and renal failure. The present study was undertaken to explore the potential role of renal cyst enlargement in initiating hypertension and renal failure in ADPKD. We therefore measured renal structural indices by computed tomography(CT) to examine the relation between clinical progression and renal structural deformities. Sixty-seven adult subjects(45±12 years, rnale-female ratio 42: 25) with ADPKD were studied at our PKD clinic from 1997 to 2000, and a complete abdominal CT was performed on all subjects. One radiologist measured the renal structural indices which were renal length, volume, RSI(anatomical renal severity index) and maximal cyst size. The renal structural indices were significantly greater in hypertensive group compared to the normotensive group (hypertensive 833±585 vs. normotensive 360±154mL/ 1.73m------------², p<0.01). The renal structural indices were significantly greater in renal failure group compared to the normal renal function group(renal failure 1,171±700 vs. normal 499±335mL/1.73m², p<0.01). The renal function in ADPKD correlated with the renal structural indices. We concluded that the clinical progression in ADPKD correlates with the renal structural indices well. These structural indices provide considerable information about the progression of ADPKD.