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비후성 뇌수막염과 대동맥주위염으로 발현한 IgG4 연관 질환
은정수 ( Jung Su Eun ),권상훈 ( Sang Hoon Kwon ),이은송 ( Eun Song Lee ),강영모 ( Young Mo Kang ),남언정 ( Eon Jeong Nam ) 대한내과학회 2015 대한내과학회지 Vol.88 No.1
Immunoglobulin G4 (IgG4)-related disease (RD) is an immune-mediated, systemic fibroinflammatory condition characterizedby a lymphoplasmacytic infiltration of IgG4-positive plasma cells, storiform fibrosis, and obliterative phlebitis. IgG4-RD has becomerecognized with increasing frequency since the turn of the century and may affect almost any organ. IgG4-RD also involvesthe meninges but, to the best of our knowledge, no case of IgG4-related intracranial pachymeningitis with periaortitis has been reportedin Korea to date. Here, we report on a 65 year-old male with IgG4-RD involving the meninges and aorta. (Korean J Med 2015;88:114-119)
폐쇄세기관지기질화폐렴이 합병된 피부근염 환자에서 동반된 전립샘암
강종완 ( Jong Wan Kang ),은정수 ( Jung Su Eun ),김나리 ( Na Ri Kim ),임철현 ( Churl Hyun Im ),강영모 ( Young Mo Kang ),남언정 ( Eon Jeong Nam ) 대한내과학회 2013 대한내과학회지 Vol.84 No.3
Dermatomyositis (DM) is a kind of systemic autoimmune disease characterized by chronic inflammation leading to progressive weakness of proximal muscles and typical cutaneous lesions. DM has been known to be strongly associated with malignancies, such as ovarian, lung, and gastric cancers. Prostate cancer is rarely associated with DM and, to our knowledge, no case of prostate cancer has been reported in patients with DM combined with interstitial lung disease in Korea. Here, we report a case of DM with bronchiolitis obliterans organizing pneumonia that was simultaneously diagnosed as advanced prostate cancer by a thorough evaluation for hidden malignancy. (Korean J Med 2013;84:457-463)
강종완 ( Jong Wan Kang ),은정수 ( Jung Su Eun ),김나리 ( Na Ri Kim ),임철현 ( Churl Hyun Im ),강영모 ( Young Mo Kang ),남언정 ( Eon Jeong Nam ) 대한내과학회 2013 대한내과학회지 Vol.84 No.3
COPD imposes significant morbidity and mortality in Korea. The Korean Academy of Tuberculosis and Respiratory Diseases (KATRD) revised the practice guideline of COPD in 2012. The revised guideline was developed not only with the agreement of the KATRD members but also with the input from the representatives of Korean Physician`s Association and Health Insurance Review & Assessment Service. In the revised guideline, recommendations were developed by systematic reviews based on PICO (population, intervention, comparison, and outcome) and GRADE (The Grading of Recommendations Assessment Development and Evaluation). Patients aged over 40 with smoking history, dyspnea, cough, and phlegm should be suspected to have COPD. To confirm and diagnose COPD, pulmonary function test of spirometry is required. In addition to pulmonary function, dyspnea symptom and exacerbation frequency should be evaluated to classify COPD patients into three groups, A, B, and C. The guideline recommends for patients in group A an inhaled short-acting bronchodilator to control the symptoms; for patients in B, an inhaled long-acting anticholinergics or an inhaled long-acting beta2 agonist; for patients in C, an inhaled long-acting anticholinergics, an inhaled long-acting beta2 agonist, or a combination of inhaled corticosteroid and long-acting beta2 agonist (low level of evidence and strong recommendation). (Korean J Med 2013;84:464-479)
파미드로네이트 불응성 다발 장기 전이성 석회화를 동반한 고칼슘혈증
배기범 ( Gi Bum Bae ),은정수 ( Jung Su Eun ),김나리 ( Na Ri Kim ),임철현 ( Churl Hyun Im ),남언정 ( Eon Jeong Nam ),강영모 ( Young Mo Kang ) 대한내과학회 2013 대한내과학회지 Vol.85 No.5
Paget`s disease of bone (PDB) is a disorder featuring high-level bone turnover associated with the presence of disorganized and immature bone tissue with excessive levels of fibrosis. The risk of deformity is very high. The etiology of PDB is not well understood, but includes both genetic and environmental factors among which is bone trauma. Hypercalcemia can occur as a complication of PDB in patients who are immobilized and dehydrated. However, to date, no case of severe hypercalcemia with metastatic calcifications in multiple organs has been reported in any PDB patient. The drugs of choice for treatment of PDB are bisphosphonates. These drugs effectively suppress bone turnover. Patients with extensive PDB may require higher doses of bisphosphonates, and acquired resistance to a particular bisphosphonate may be overcome by use an alternative drug. Here, we report a case of suspicion of PDB. The patient presented with hypercalcemia and metastatic calcifications and his condition improved dramatically after treatment with zoledronic acid. (Korean J Med 2013;85:545-550)
정상 Creatine Kinase를 보인 조직학적으로 증명된 피부근염
권상훈 ( Sang Hoon Kwon ),은정수 ( Jung Su Eun ),이은송 ( Eun Song Lee ),강영모 ( Young Mo Kang ),남언정 ( Eon Jeong Nam ) 대한내과학회 2016 대한내과학회지 Vol.90 No.3
Dermatomyositis (DM) is an idiopathic inflammatory myopathy (IIM) characterized by skeletal muscle inflammation and typical skin manifestations. Creatine kinase (CK) has traditionally been considered to be the most useful serum enzyme for the diagnosis and assessment of adult patients with IIM. To our knowledge, there has been no reported case of biopsy-proven DM without CK elevation in Korea, to date. Panniculitis is an uncommon cutaneous manifestation in adult patients with DM. A search of the PubMed database reveals fewer than 30 reported cases of panniculitis in adult patients with DM. Here, we report a case of a 42-year-old female who was diagnosed with biopsy-proven DM with normal serum CK levels and panniculitis. (Korean J Med 2016;90:274-279)