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Sweet’s Syndrome Associated with Graves’ Disease
용호진,강미일,김도희 대한갑상선학회 2017 International Journal of Thyroidology Vol.10 No.1
Sweet’s syndrome, or acute febrile neutrophilic dermatosis, occurs in association with autoimmune diseases such as Hashimoto’s thyroiditis but is rare in Graves’ disease, in which all cases are induced by propylthiouracil (PTU). We report a case of Sweet’s syndrome in a patient with Graves’ disease treated with methimazole (MMI) during three weeks. A 34-year-old man presented with the acute onset of high fever, skin rashes on the whole body, arthralgia, and acroparesthesia. Laboratory results showed leukocytosis and elevated C-reactive protein. MMI first stopped and antibiotics and antihistamine therapy started, but his symptoms dramatically improved after oral prednisolone. Graves’ disease has again been treated by MMI because of his aggravated ophthalmopathy. After one year of retreatment with MMI, there has been no recurrence of Sweet’s syndrome, supporting that Sweet’s syndrome in this case was not related to MMI exposure. To our knowledge, this is the first report of Sweet’s syndrome associated with Graves’ disease per se but not PTU or MMI use.
백현진,Doo Hyuk Lee,Kyu Hyung Han,Young Min Kim,Hyunbeom Kim,Byeongwook Cho,이인국,최강현,용호진,홍구현 대한중환자의학회 2016 Acute and Critical Care Vol.31 No.2
In critically ill patients, disseminated intravascular coagulation (DIC) is a common and fatal hematological disorder. DIC is a physiological response to a variety of underlying stimuli that provoke generalized activation of the hemostatic mechanism and is common in septic patients and those with hematological or non-hematological malignant neoplasms. Bleeding is a common clinical feature, and diffuse or multiple-site mucocutaneous bleeding, such as petechia, ecchymosis and hemorrhage from gastrointestinal tract, is often seen. A 58-year-old male was recently diagnosed with intracranial hemorrhage (ICH) caused by DIC associated with sepsis. Mortality of ICH caused by DIC is very high because the underlying condition cannot be quickly treated. Awareness of the possibility of DIC developing in a critically ill patient and the need for immediate initiation of plasma or platelet replacement therapy are important. To the best of our knowledge, this is the first reported case of intracranial hemorrhage in a Korean patient with DIC associated with sepsis.