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이중건(Jung Geon Lee),안규리(Gu Rie Ahn),황대연(Dae Yeon Hwang),황영환(Yeong Hwan Hwang),김기원(Ki Won Kim),이서진(Seo Jin Lee),나기영(Ki Young Na),한진석(Jin Suk Han),김성권(Sung Gwon Kim) 대한내과학회 2000 대한내과학회지 Vol.58 No.1
Background : ADPKD is one of the most common hereditary renal disease in adult and is a systemic disorder with a variety of cardiovascular manifestations. To elucidate the clinical characteristics of cerebrovascular complications in Korean ADPKD patients, we reviewed the medical records of ADPKD patients who was registered in ADPKD clinic of Seoul National University Hospital. Methods : A total of 18 adult patients were included and their sex ratio was 8:10. The median age of ADPKD diagnosis was 45.5 year(range 19-85), and age at cerebrovascular accident(CVA) was 52 years(22-82). The median duration from hypertension to CVA was 8 years(0-30). Results : There were 5 cases of infarction, 4 cases of intracerebral hemorrhage, 4 cases of subarachnoid hemorrhage, and 4 cases of transient ischemic attack. Other clinical parameters of ADPKD were not different from patients who were not complicated with CVA. Intracranial aneurysms were detected in 6 patients and their median age at diagnosis was 47.5 years(33-66). Four cases were manifested as subarachnoid hemorrhage. Five cases were diagnosed through TFCA, and two of them were revealed as multiple aneurysms. Five cases received surgical treatment and five of six cases improved without any neurologic sequeale. MR angiography(MRA) were taken in 16 asymptomatic patients, and multiple aneurysms were newly detected in one of them. Conclusion : Cerebrovascular complications in Korean ADPKD patients were not significantly different from western patients. Intracranial aneurysms must be included in differential diagnosis in ADPKD patients who manifest an acute neurologic symptoms, and high-risk group need to be screened selectively with MRA.(Korean J Med 58:75-82, 2000)
조종태(Jong Tae Cho),김근호(Geun Ho Kim),엄재호(Jae Ho Earm),안규리(Gu Rie Ahn),한진석(Jin Suk Han),김성권(Suhng Gwon Kim),이정상(Jung Sang Lee) 대한내과학회 1990 대한내과학회지 Vol.39 No.6
N/A We observed the clinical features, underlying disorders, complications, treatment and outcome of 12 cases of distal renal tubular acidosis and the following results were obtained. 1) The patient`s age ranged from 23 to 53 years old (39±9) and female to male ratio was 10:2. 2) The chief complaints on admission were generalized weakness (5), periodic paralysis (4), recurrent renal stone (2) and paresthesia (1). 3) The identified underlying disorders were systemic lupus erythematosus (3), medullary spongy kidney (2), Sjogren`s syndrome (2), and hyperparathyroidism (1). 4) The major complications were nephrolithiasis (3), nephrocalcinosis (3), osteomalacia (2) and rhabdomyolysis (1). 5) Replacement of alkali and potassium, and specific therapy for underlying disorders showed good outcome.
CaNa2-EDTA 연 (鉛) 동원 검사에 의해 확진된 연중독 1 예
이건용(Gun Yong Lee),전노원(Rho Won Chun),김근호(Keun Ho Kim),채동완(Dong Wan Chae),노정우(Jung Woo Noh),안규리(Gu Rie Ahn),이정상(Jung Sang Lee) 대한내과학회 1996 대한내과학회지 Vol.51 No.6
Recently, cases with lead poisoning due to herb medication with unknown ingredient have been reported increasingly, In general, lead poisoning has been confirmed through estimation of the concentration of lead in serum, of amount of lead excreted in 24 hour urine and so on. But in cases when lead poisoning is suspisious but routine laboratory findings are not compatible with lead poisining, CaNa2 EDTA mobilization test with determination of excreted amount of lead in 24 hour urine has been known to be an effective method of confirming lead poisoning through determination of chelatable lead stores in the body. Authors experienced one case of suspicious lead poisoning with normal serum leaed concentration, with equivocal results in lead excretion in 24 hour urine collections. Authors confirmed lead poisoning by applying CaNa2 EDTA mobilization test, for the first time in Korea, to the patient with equivocal laboratory and clinical findings. Here, a case of lead poisoning confirmed by CaNa2 EDTA mobilization test is presented and recent literatures are reviewed.
신부전 만성도 평가에 있어 혈중 carbamylated hemoglobin 치의 유용성
김연수(Yon Su Kim),한진석(Jin Suk Han),진호준(Ho Jun Chin),이서진(Seo Jin Lee),조윤숙(Yun Suk Cho),안규리(Ahn Cu Rie),김성권(Suhng Gwon Kim),이정상(Jung Sang Lee),장인진(In Jin Jang),신상구(Sang Gu Shin),허우성(Woo Seong Huh) 대한내과학회 1996 대한내과학회지 Vol.51 No.3
Objective: Differentiation of acute from chronic renal failure is an important but difficult task in treating the azotemic patients. It is known that the degree of carbamylation reflects the duration and the severity of the uremia. To assess the usefulness in differentiating acute(ARF) from chronic reanl failure (CRF), we measured the carbamylated hemoglobin (CarHb). Methods: We measured CarHb(measured as ㎍ of carbamyl valine per g hemoglobin) prospectively in 64 patients with azotemia (24 ARF, 40 CRF) referred to the Seoul National University Hospital. High performance liquid chromatography was used for measuring CarHb. Thirteen normal controls were also studied to match 64 patients. Results: Patients with ARF had lower median (range) CarHb concentration than those with CRF [56.0(24.6-97.1) ㎍CV/gHb vs 120.4(31.7-286.5) p<0.01]. It is not different from normal control [56.0 (24.6-97.1) vs 40.9(19,9-62.9); p<0.05]. The ratio of CarHb to serum creatinine(mg/dl) was lower in ARF than in CRF [10.5(4.9-34A) vs 18.2(4.7-52.2) p<0.01]. The cut-off value for CarHb to be CRF is 80 ㎍CV/gHb(sensitivity 70%, specificity 71%, positive predictive value 80%). Conclusion: The carbamylated hemoglobin is useful in determining the chronicity of the renal failure and it could be of clinical value in deciding the further management.