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구본산 ( Bon San Koo ),송윤아 ( Yoonah Song ),이승훈 ( Seunghun Lee ),김태환 ( Tae-hwan Kim ),전재범 ( Jae-bum Jun ) 대한내과학회 2018 대한내과학회지 Vol.93 No.5
Systemic sclerosis (SSc) is a chronic autoimmune disorder characterized by endothelial and fibroblast dysfunction, resulting in progressive fibrosis of the skin and internal organs. Ankylosing spondylitis (AS) is an arthritic condition affecting the axial skeleton and peripheral joints. An association between SSc and AS is relatively rare, as the two diseases share few characteristics. Here, we present a case of limited SSc in a 44-year-old man who exhibited low-grade AS, and discuss several cases of coexisting SSc and AS in the literature. Patients with both diseases showed several common features, including male predominance, middle age, and combined interstitial lung disease. However, unlike our case, the patients reported in the literature had advanced ankylosis and diffuse SSc. (Korean J Med 2018;93:492-496)