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김진휘(Jin Hwi Kim),구양서(Yang Suh Koo),정종익(Jong Ik Jeong),정상용(Sang Yong Jeong),권덕호(Duk Ho Kwun),신동우(Dong Woo Shin),한병철(Byung Chul Hahn),서동진(Dong Jin Suh) 대한내과학회 2000 대한내과학회지 Vol.59 No.1
Rotor syndrome is a rare benign familial disorder characterized by chronic, fluctuating, nonhemolytic and predominantly conjugated hyperbilirubinemia with normal liver tissue. In contrast to Dubin-Johnson syndrome, there is no liver hyperpigmentation in Rotor syndrome, and BSP clearance does not show a secondary retention peak. The serum bilirubin in patients with Gilbert's syndrome is almost all unconjugated in contrast to Rotor syndrome. A 29-year-old male was admitted due to persistent jaundice. Physical examination revealed icteric sclera without hepatosplenomegaly. Laboratory findings showed increased serum bilirubin with indirect bilirubin predominance. Urinary excretion of total coproporphyrin was markedly elevated, and coproporphyrin Ⅰ was 66% of total urinary coproporphyrin. Oral cholecystography showed well visualized the gallbladder, but 99mTc-DISIDA scan showed markedly decreased hepatic uptake and poor visualization of the gallbladder and biliary tract. Histology of the liver showed no abnormal finding. We report the case with the review of literature.(Korean J Med 59:109-113, 2000)
정상용 ( Sang Yong Chung ),신동우 ( Dong Woo Shin ),신재욱 ( Jae Wook Shin ),천정현 ( Jeong Hyun Chun ),김진휘 ( Jin Hwi Kim ),정종익 ( Jong Ik Jeong ),권덕호 ( Duk Ho Kwun ),신미경 ( Mi Kyung Shin ),송태의 ( Tae Eui Song ) 대한류마티스학회 1999 대한류마티스학회지 Vol.6 No.2
Approximately half of the patients with systemic lupus erythematosus(SLE) develop localized or diffuse lymphadenopathy during the evolution of the disease. But hilar and mediastinal lymph node enlargement due to SLE is rare. The histologic findings of lupus lymphadenitis range from nonspecific lymphadenitis with variable degrees of cellular necrosis to the less common but more specific appearance of extensive necrosis. Advanced lesions are characterized by hematoxylin bodies and condensation of DNA on the vessel walls. Hematoxylin bodies are amorphous homogeneous violet or lilac colored structures composed of partially depolymerized DNA, mixed with protein, carbohydrates and globulins which may be seen deposited on vessel walls and within the paracortex of lymph node. They are virtually diagnostic of SLE and would exclude malignant lymphoma. SLE with mediastinal lymphadenopathy is rare so we report this case with a review of literatures, which was diagnosed by hematoxylin bodies on pathologic findings of cervical lymph node.