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Symptomatic pheochromocytoma with normal urinary catecholamine levels
( Jung Re Yu ),( Mi Yeon Kim ),( Gil Myeong Seong ),( Woo Seong Jeong ),( Sang Ah Lee ),( Dae Ho Lee ),( Gwan Pyo Koh ) 대한내과학회 2011 대한내과학회 추계학술발표논문집 Vol.2011 No.1
A 53-year old female presented with headache, sweating and chest discomport. On admission, she showed a left adrenal mass on CT scan. Repeated measurements of 24-hour urinary fractionated metanephrines, total catecholamines, vanillylmandelic acid (VMA) and plasma catecholamine were within normal range. Scintigraphic 131I-MIBG revealed selective concentration of the radiotracer, corresponding to the CT mass. Plasma and urine catecholamine levels were within normal range even during paroxysmal episodes. Successful surgical excision of the tumor was performed and the pathological examination confirmed the diagnosis of a pheochromocytoma with a 2.3cm sized solid tumor. This is a rare case of a symptomatic pheochromocytoma without elevated catecholamine and its metabolite levels. Our case illustrates that in all patients with high clinical suspicion of pheochromocytoma, a routine nuclear scintigraphy should be performed even in the setting of normal biochemical testing.
Fulminant type 1 diabetes associated with coxachievirus B4: A report of 2 cases
( Jung Re Yu ),( Mi Yeon Kim ),( Jae Geun Lee ),( Seong Joo Ko ),( Sang Ah Lee ),( Gwanpyo Koh ),( Dae Ho Lee ) 대한내과학회 2011 대한내과학회 추계학술발표논문집 Vol.2011 No.1
Recently fulminant type1 diabetes (T1DM) has been identified as a new subtype of idiopathic diabetes. It develops rapidly without any evidence of autoimmunity. Here, we report two cases of patients; each patient presented with abrupt and extreme hyperglycemia and ketoacidosis without an evidence of previous diabetes mellitus. A 74-year-old man presented with a 2-day history of polydipsia. His serum C-peptide level was 0.06 ng/ml and HbA1c level was 6.7%. The serum lipase was elevated. The other 21-year-old man presented with a 2-week history of polydipsia. His serum c-peptide and HbA1c levels were 0.73 ng/ml and 17.6%, respectively. The serum lipase was within normal range in the young patient. In both patients, anti-GAD antibody tests were negative whereas tests for coxsackievirus B4 virus infection were positive. Furthermore, both patients required insulin therapy to control their blood glucose levels at discharges and during the follow-up period.
유정래 ( Jung Re Yu ),진현정 ( Hyoun Jung Chin ),김미연 ( Mi Yeon Kim ),정우성 ( Woo Seong Jeong ),이상아 ( Sang Ah Lee ),이대호 ( Dae Ho Lee ),고관표 ( Gwan Pyo Koh ) 대한내과학회 2012 대한내과학회지 Vol.83 No.4
A 53-year-old woman had a 1.7 cm left adrenal mass on an abdominal computed tomography (CT) scan. She presented with paroxysmal headache, palpitation, sweating, and hypertension. The patient was highly suspected of having a pheochromocytoma, but measurements of 24-hour urinary metanephrine, catecholamines, and vanillylmandelic acid were normal. Plasma and urine catecholamine levels were within the normal range even during paroxysmal episodes. A scintigraphic study with 131I-metaiodobenzylguanidine (MIBG) revealed selective concentration of the radiotracer, corresponding to the CT mass. The patient underwent a left adrenalectomy and the pathological examination confirmed the diagnosis of pheochromocytoma. In this report, we describe a rare case of a symptomatic pheochromocytoma with normal catecholamine levels. Our case illustrates that routine nuclear scintigraphy, such as 131I-MIBG, should be performed even in cases with normal hormonal testing for all patients with high clinical suspicion of pheochromocytoma. (Korean J Med 2012;83:503-509)
Ho Cheol Kim,I Re Heo,Tae Hoon Kim,Jong Hwan Jeong,Manbong Heo,Sun Mi Ju,Jung-Wan Yoo,Seung Jun Lee,Yu Ji Cho,Yi Yeong Jeong,Jong Deog Lee 대한결핵및호흡기학회 2023 Tuberculosis and Respiratory Diseases Vol.86 No.2
BackgroundThe objective of this study was to investigate whether alcohol consumption might affect the quality of life (QOL), depressive mood, and metabolic syndrome in patients with obstructive lung disease (OLD). MethodsData were obtained from the Korean National Health and Nutrition Examination Survey from 2014 and 2016. OLD was defined as spirometry of forced expiratory volume in 1 second/forced vital capacity <0.7 in those aged more than 40 years. QOL was evaluated using the European Quality of Life Questionnaire-5D (EQ-5D) index. Patient Health Questionnaire-9 (PHQ-9) was used to assess the severity of depressive mood. Alcohol consumption was based on a history of alcohol ingestion during the previous month. ResultsA total of 984 participants with OLD (695 males, 289 females, age 65.8±9.7 years) were enrolled. The EQ-5D index was significantly higher in alcohol drinkers (n=525) than in non-alcohol drinkers (n=459) (0.94±0.11 vs. 0.91±0.13, p=0.002). PHQ-9 scores were considerably lower in alcohol drinkers than in non-alcohol drinkers (2.15±3.57 vs. 2.78±4.13, p=0.013). However, multiple logistic regression analysis showed that alcohol consumption was not associated with EQ-5D index or PHQ-9 score. Body mass index ≥25 kg/m2, triglyceride ≥150 mg/dL, high-density lipoprotein <40 mg/dL in men and <50 mg/dL in women, and blood pressure ≥130/85 mm Hg were significantly more common in alcohol drinkers than in non-alcohol drinkers (all p<0.05). ConclusionAlcohol consumption did not change the QOL or depressive mood of OLD patients. However, metabolic syndrome-related factors were more common in alcohol drinkers than in non-alcohol drinkers.
김미연 ( Mi Yeon Kim ),한상훈 ( Sang Hoon Han ),유정래 ( Jung Re Yu ),정우성 ( Woo Seong Jeong ),김현우 ( Hyun Woo Kim ),이재천 ( Jae Chun Lee ),현창림 ( Chang Lim Hyun ) 대한내과학회 2012 대한내과학회지 Vol.83 No.3
Human herpes virus-8 (HHV-8)-negative primary effusion lymphoma (PEL) is frequently observed in patients with chronic liver disease. We describe herein a case of PEL in a patient with chronic kidney disease. A 59-year-old woman presented with dyspnea. The patient had a history of uncontrolled pleural effusion. The pleural effusion revealed a malignant cell-dominant exudate. Serological tests were negative for human immunodeficiency virus (HIV). Initial chest and abdomen computed tomography showed bilateral pleural effusion; however, no evidence of a tumor mass or lymph node enlargement was found. A malignant lymphoma of diffuse large B-cell type was confirmed by pleural fluid cytology. Immunohistochemical staining of malignant cells was negative for HHV-8. She was treated with rituximab and CHOP (cyclophosphamide, adriamycin, vincristine, prednisolone) chemotherapy. We report a case of PEL in a patient with chronic kidney disease that may be a plausible predisposing factor for HHV-8-negative PEL.
( Jae Geun Lee ),( Sung Joo Koh ),( So Yeon Yoo ),( Jung Re Yu ),( Sang Ah Lee ),( Gwan Pyo Koh ),( Daeho Lee ) 대한내과학회 2012 The Korean Journal of Internal Medicine Vol.27 No.3
Background/Aims: The clinical implications of hypocholesterolemia have not been well studied, although some studies have revealed an association between hypocholesterolemia and intracerebral hemorrhage (ICH). We evaluated the clinical characteristics of subjects with very low-density lipoprotein cholesterol (LDL-C) and compared the risk for ICH using various clinical parameters. Methods: Using hospital records, we evaluated the clinical characteristics of subjects with LDL-C levels ≤ 40 mg/dL (very low LDL-C group). We also evaluated the risk for ICH in this very low LDL-C group and in subjects with low LDL-C ≤ 70 mg/dL (low LDL-C group). Results: Among 34,415 subjects who presented at the laboratory for serum LDL-C measurements, 250 subjects had a very low serum LDL-C level (≤ 40 mg/dL). About half of the subjects were statin users; the very low LDL levels in the other subjects were likely attributable to alcohol consumption or a various chronic illness such as liver disease or endstage renal disease (ESRD). ICH occurred in three subjects with very low LDL-C, all of whom had no history of statin use. ESRD tended to be associated with ICH in subjects with serum LDL-C ≤ 70 mg/dL. Conclusions: About 1% of the subjects whose LDL-C was measured in the hospital had a LDL-C level ≤ 40 mg/dL, and about half of these subjects had no history of hypolipidemic therapy. ICH incidence was not related to LDL-C level or statin use.