폐동맥 고혈압과 심부전으로 발현된 폐분리증과 선천성 엽기종이 동반된 1례 = A Case of Pulmonary Sequestration and Congenital Lobar Emphysema Presenting with Congestive Heart Failure and Pulmonary Hypertension

국문 초록 (Abstract)

저자들은 영아기에 폐동맥 고혈압, 심부전으로 발현된 폐분리증과 선천성 엽기종이 동반된 증례를 진단하였고, 이환된 폐엽절제수술 후 폐동맥 고혈압 및 심부전이 호전된 증례를 경험하였기에 보고하는 바이다.

다국어 초록 (Multilingual Abstract)

Congenital cystic disease of the lung represents pulmonary sequestration, congenital lobar emphysema, bronchogenic cyst and congenital cystic adenomatoid malformation. It has a variety of clinical manifestations from immediate postnatal respiratory distress to heart failure. Pulmonary sequestration sometimes causes heart failure in neonates through a shunt between an anomalous systemic feeding artery and the pulmonary venous system. We hereby report a case with both pulmonary sequestration and congenital lobar emphysema presenting with congestive heart failure and pulmonary hypertension, which improved after lobectomy. [Pediatr Allergy Respir Dis(Korea) 2009;19:434-439]