A case of disseminated intravascular coagulation developed after surgical management of corpus luteal hemorrhage in a patient with Klippel-Trenaunay syndrome = A case of disseminated intravascular coagulation developed after surgical management of corpus luteal hemorrhage in a patient with Klippel-Trenaunay syndrome

다국어 초록 (Multilingual Abstract)

Klippel-Trenaunay syndrome (KTS) is a rare congenital vascular malformation characterized by the clinical triad of bony or soft tissue hypertrophy, usually affecting one extremity; hemangiomas and/or lymphangiomas, and varicosities or venous malformations. Vascular malformation of KTS can involve several organs and be a source of significant morbidity and even mortality. Clinical manifestations of KTS range from occult to massive, life-threatening hemorrhage. Several cases of lifethreatening gastrointestinal bleeding in KTS patients have been reported. In contrast, large venous malformations can be associated with low-grade consumptive coagulopathy. Spontaneous hemoperitoneum may occur in various gynecological conditions. The most common gynecological causes of spontaneous hemoperitoneum in women of childbearing age are ectopic pregnancy and ruptured corpus luteal cyst . The treatment of spontaneous hemoperitoneum of gynecological causes is well established. However in patients with coagulopathy, the management has to be planned differently. The authors present a case of a 29-year-old female with KTS who presented with a spontaneous hemoperitoneum by corpus luteal hemorrhage and subsequent life-threatening disseminated intravascular coagulation (DIC) after ovarian cystectomy.