외성기에 단일증상으로 나타난 일차성 림프부종 = Primary (Congenital) Lymphedema of the External Genitalia

다국어 초록 (Multilingual Abstract)

The etiology of the primary(congenital) lymphedema is as an unknown abnormal development of the subcutaneous lymphatic tissue itself. Lymphedema is expressed at different ages, and may be sporadic or inherited. Congenital lymphedema are rarely isolated to the external genitalia, but rather have lower extremity involvement. Isolated congenital lymphedema of the external genitalia is also extremely rare; to our knowledge, there has been no case report in the Korean literature. Our experienced case was that of a 17 year old male patient, who was treated surgically (scrotal reconstruction), with a relatively good result. (Korean J Urol 2004;45: 1174-1177)

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