선천작은동공 환자에서 홍채당김기를 이용한 백내장 수술 1예 = A Case of Cataract Operation Using Iris Retractor in Congenital Microcoria

다국어 초록 (Multilingual Abstract)

Purpose: To report an case regarding phacoemulsification and intraocularlens (IOL) implantation using an iris retractor in a congenital microcoria patient. Case summary: A 53-year-old male patient visited the office with a complaint of gradual decrease of visual acuity. The patient`s best corrected visual acuity (BCVA) was 0.3, and his refractive index could not be measured, as a very small pupil was observed in both eyes. After applying tropicamide and phenylephrine four times, the refractive index of both eyes remained immeasurable. In addition, on slit-lamp biomicroscopic examination, a nucleosclerotic cataract was observed in both eyes. Any signs of increased intraocular pressure or gonioscopic findings seen in glaucomatous patients was not detected in either eyes. Using an ultrasound biomicroscope and Pentacam, the pupil diameter were 0.31 mm in both eyes, and changed to 0.92 mm in the right eye, and 1.0 mm in the left eye, after applying mydriatics. Phacoemulsification and IOL implantation were performed one month apart from each other, using an iris retractor. On the follow-up examination 2 to 3 months postoperatively, BCVA was 0.7 in the right eye, and 1.0 in the left eye. After the operation, the pupil diameter was not changed before and after mydriasis, and measured 2.53 mm in the right eye, and 2.83 mm in the left eye. Conclusions: The authors have reported a case regarding visual acuity that improved in a congenital microcoria patient performing a phacoemulsification and IOL implantation operation using an iris retractor. J Korean Ophthalmol Soc 2009;50(4):618-623

참고문헌 (Reference)

1 Rouillac C, "Mapping of congenital microcoria locus to 13q31-q32" 62 : 1117-1122, 1998

2 Bremner FD, "Genotypic and phenotypic heterogeneity in familial microcoria" 88 : 469-473, 2004

3 Ramprasad VL, "Genetic homogeneity for inherited congenital microcoria loci in an asian indian pedigree" 11 : 934-940, 2005

4 Zenker M, "Congenital nephrosis, mesangial sclerosis, and distinct eye abnormalities with microcoria: An autosomal recessive syndrome" 130 : 138-145, 2004

5 Kong IH, "Congenital miosis: 4 cases in a family" 8 : 31-32, 1967

6 Pietropaolo A, "Congenital microcoria: Case report and histologic study" 35 : 125-127, 1998

7 Tawara A, "Congenital microcoria associated with late-onset developmental glaucoma" 14 : 409-413, 2005

8 Vila-coro AA, "Congenital Idiopathic microcoria" 15 : 439-440, 1989

9 Toulemont PJ, "Association of congenital microcoria with myopia and glaucoma. A study of 23 patients with congenital microcoria" 102 : 193-198, 1995