A case of unilateral pulsating exophthalmos due to defective development of the sphenoid bone with plexiform neurofibroma was reported.
There were missing of orbital plate of the frontal bone, lesser and great wing of the sphenoid, and lacrymal plate...
A case of unilateral pulsating exophthalmos due to defective development of the sphenoid bone with plexiform neurofibroma was reported.
There were missing of orbital plate of the frontal bone, lesser and great wing of the sphenoid, and lacrymal plate of the ethmoid bone.
Middle fossa became deepening accompaning with thining of temporal bone, and the tip of the temporal lobe was covered by tremendously dilated subarachnoid spaces with thick membranes.
There were diffuse neurofibromatosis and plesiform aeurofibroma resulted in elephantiasis of the lids.
The skull bone defect was covered with Resin after removal of the plexiform neurofibroma. The patient was improved.