베체트병에서 병발된 고도난청환자에 시행한 인공와우이식술 1예 = A Case of Cochlear Implantation in a Postlingual Deaf Patient with Behcet Disease

다국어 초록 (Multilingual Abstract)

Recurrent iritis and oral/genital ulcers have ben described for the first time as a separate pathological entity by the Turkish dermatologist Hulusi Behcet. Behcet disease is a chronic, multi-systemic disorder, which afects many organs as a result of vas-：major (oral ulcers, eye lesions, genital ulcerations, and skin lesions) and minor (arthritis, gastrointestinal lesions, epididymitis, thrombophlebitis, and central nervous system involvement) criteria. The incidence of hearing loss in Behcet disease has been reported as 12% to 80% in several studies. A 37-year-old man diagnosed as Behcet disease was admitted to our department with complaints of profound right hearing los and dizines. He al bone CT scan revealed right cochlear osification. Cochlear implantation was performed within 4 weks after the completion of steroid therapy in the left cochlea, which was partially obstructed by fibrotic tisue. However, the electrode was fully inserted without resistance. Wound healing complications were not encountered in the postoperative period. The hearing threshold was restored to 30 dBHL, while spech discrimination did not improve as much as expected. We propose that the routine hearing examinations be employed in the evaluation and management of Behcet disease. According to our experience, we find that cochlear implantation should be caried out at an early stage, before the development of labyrinthine osification.

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