Clinical manifestations and anesthetic management of Kearns-Sayre syndrome -A case report-

다국어 초록 (Multilingual Abstract)

Kearns-Sayre syndrome (KSS) is a mitochondrial disorder resulting in multi-system dysfunction. A 14-year-old boy with KSS underwent external levator muscle resection for correction of ptosis. There were no abnormalities on the pre-operative evaluation, except for low-grade heart block and ocular problems. General anesthesia was conducted with a minimum dose of thiopental sodium and sevoflurane under close monitoring, and a laryngeal mask was inserted without muscle relaxation. The surgery was uneventful;however, a careful approach was required during anesthesia because life-threatening complications may occur in patients with KSS. (Anesth Pain Med 2011; 6: 290∼293)

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