굴측부 망상 색소이상 1예 = Short Report : A Case of Reticulate Pigmented Anomaly of the Flexures (Dowling-Degos Disease)

다국어 초록 (Multilingual Abstract)

Reticulate pigmented anomaly of the flexures is a rare autosomal dominant genodermatosis, and this is also known as Dowling-Degos disease. The clinical symptoms are characterized by the progressive evolution of small hyperpigmented macules in a reticulate distribution, and this shows a predilection for the flexural regions, including the axillae, antecubital fossae, inframammary regions, neck and groin. The histopathology of reticulate pigmented anomaly of the flexures typically shows filiform epithelial down-growth of the epidermal rete ridges along with basal hyperpigmentation. We report here on a case of reticulate pigmented anomaly of the flexures in a 45-year-old male who showed multiple, asymptomatic, scaly brownish reticulated macules on the flexural areas. (Korean J Dermatol 2009;47(10):1199∼1202)

참고문헌 (Reference)

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