정신지체를 동반한 다수의 위성병변을 가진 거대선천멜라닌세포모반 = Giant Congenital Melanocytic Nevus with Multiple Satellite Lesions in a Korean Woman with Mental Retardation

다국어 초록 (Multilingual Abstract)

Giant congenital melanocytic nevi (GCMN) are defined as melanocytic nevi that are greater than 20 cm in largest dimension at birth. GCMN is a relatively rare condition, affecting approximately 1 in 20,000 newborns. Patients with GCMN on the posterior axis and in the presence of many satellite nevi are associated with neurocutaneous melanosis. A 37-year-old female with mental retardation had dark brown nevi with hair on her back (paraspinal) and on her lower extremities. In addition, she has multiple satellite lesions distributed over her trunk and extremities. Herein, we present a case that demonstrates a relationship between CNS abnormality and multiple satellite nevus in GCMN patients with a review of the relevant literature. (Korean J Dermatol 2013;51(3):185∼188)