마미 증후군을 동반한 요천추부 광범위 경막내 유피낭종 - 1례 보고 - = Extensive Intradural Epidermoid Cysts with Cauda Equina Syndrome in the Lumbosacral Spine - Case Report -

다국어 초록 (Multilingual Abstract)

Study Design: A case report.
Objectives: To report a rare case of extensive epidermoid cysts in the lumbosacral spine.
Summary of Literature Review: The intradural epidermoid cyst with extensive involvement is rare, and previous reports have reported only extensive intramedullary epidermoid cysts.
Materials and Methods: A 75-year-old male presented with progressive motor weakness of both extremities beginning 3 days prior.
MRI showed extensive intradural extramedullary epidermoid cysts in the lumbosacral region. We performed total laminectomy from the L1 to the L5 level, and the cystic mass was removed.
Results: We confirmed the epidermoid cyst on histopathologic examination.
Conclusions: Extensive extramedullary epidermoid cysts are difficult to remove completely. Attempting complete removal may result in neurological deficit. Therefore, when surgical intervention is planned, the poor postoperative prognosis should be taken into consideration.

국문 초록 (Abstract)

연구계획: 증례 보고.
목적: 요천추 부위의 후천성 광범위한 경막내 수외 유표피낭종의 증례보고.
선행 연구문헌의 요약: 광범위한 경막내 유표피낭종의 사례는 매우 드물며 경막내 수내 유표피낭종의 경우에서만 보고되었다.
대상 및 방법: 75세 남자가 내원 3일전 급격히 진행된 양측 다리의 감각 이상과 근력 약화를 보였다. MRI상 요천추 부위의 광범위한 경막내 수외 유표피낭종이 확인되었고, 요추 1-5번의 추궁판 절제술 및 종양 제거술을 시행하였다.
결과: 조직병리학 소견으로 유표피낭종을 확인하였다.
결론: 광범위한 경막내 수외 유표피낭종은 완전 절제가 어렵고 완전히 제거하려는 시도가 신경학적 결손을 유발할 수 있다. 그러므로 수술적 치료를 함에있어 나쁜 예후에 대한 고려가 필요하다.

참고문헌 (Reference)

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