경부와 인두의 양성 다발성 대칭적 지방종증 = Multiple Symmetric Lipomatosis (Madelung’s Disease) of the Neck and Pharynx

다국어 초록 (Multilingual Abstract)

Multiple symmetric lipomatosis (Madelung’s disease) is an infrequent disease of unknown etiology. The typical characteristic of the disease is bulging, symmetric masses of fat tissue on the neck, upper extremities, and upper parts of the trunk. The disease strongly affects middle-aged men, people from Mediterranean regions and with alcohol abuse history. We report three cases of middle to old age males with long-standing multi-lobulated bulging of the neck, which gradually enlarged over many years. Of peculiar interest is one patient who presented with snoring and apnea together with typical findings of Madelung’s disease. The case had involvement of the hypopharynx, which was successfully managed with microscopic laryngeal surgery with CO2 laser. The authors elucidate three cases of Madelung’s disease found in the pharynx and neck, and report a review of the literature.
Korean J Otorhinolaryngol-Head Neck Surg 2014;57(12):865-9

참고문헌 (Reference)

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