복막 위점액종 = A Case of Pseudomyxoma Peritonei

다국어 초록 (Multilingual Abstract)

Pseudomyxoma peritonei is a rare disease in which the peritoneal cavity becomes distended with a pa]e, translucent, semisolid material that is shown biochemically and histochemically to be a mucin and in which peritoneal surface and omentum are diffusely invo]ved with gelatinous mucinous irnplants and gelatinous ascites. There are two major causes of this mucinous ascites: mucinous cystadenoma and cystadenocarcinoma of the ovary and appendix. Other less comrnon antecedent ]esions include uterine carcinoma, mucinous adenocarcinoma of the bowel, adenocar- cinoma in urachal cyst, mucoid omphalomesenteric cyst of the nave], carcinoma of the bile dwct, and colloid carcinoma of the pancreas. The term pseudomyxoma peritonei was originated by Werth in 1884. Pseudomyxoma peritonei is usual]y presented in the peritoneal cavity, lymphatics, and parenchymal tissue. The disease rare]y spreads extraperitoneally. We experienced a case of pseudomyxoma peritonei due to rnucinous adenocarcinoma of unknown primary focus. He was a 38-year old male presented with marked abdominal distention and ascites. At laparotomy, diagnosis was confirmed and aggressive debulking of intraperitoneal myxoid tumor was performed. Posto- perative chemotherapy using carboplatin and cyclophosphamide had been tried. (Korean J Gastroenterol 1996; 28:298 - 302)