십이지장의 낭포성위축증은 특징적으로 이소성 췌장조직에서 발생하는 드문 질환이다. 임상 증상, 이하학적 소견 및 검사실 소견은 비특이적이라 진단이 쉽지 않다. 낭포성위축증이 발생하...
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https://www.riss.kr/link?id=A75164432
Gu, Mi Jin (Department of Pathology, Holy Trinity Hospital) ; Park, Won Kyu (Department of Radiology, College of Medicine, Yeungnam University) ; Bae, Yeung Kyong (Department of Pathology, College of Medicine, Yeungnam University) ; Cho, Jae Ho (Department of Radiology, College of Medicine, Yeungnam University) ; Chang, Jay Chun (Department of Radiology, College of Medicine, Yeungnam University) ; Kim, Jae Woon (Department of Radiology, College of Medicine, Yeungnam University) ; Cho, Kil Ho (Department of Radiology, College of Medicine, Yeungnam University) ; Hwang, Mi Soo (Department of Radiology, College of Medicine, Yeungnam University) ; Park, Bok Hwan (Department of Radiology, College of Medicine, Yeungnam University) ; Choi, Joon Hyuk (Department of Pathology, College of Medicine, Yeungnam Univeristy)
2007
English
510.5
KCI등재
학술저널
647-651(5쪽)
0
상세조회0
다운로드국문 초록 (Abstract)
십이지장의 낭포성위축증은 특징적으로 이소성 췌장조직에서 발생하는 드문 질환이다. 임상 증상, 이하학적 소견 및 검사실 소견은 비특이적이라 진단이 쉽지 않다. 낭포성위축증이 발생하...
십이지장의 낭포성위축증은 특징적으로 이소성 췌장조직에서 발생하는 드문 질환이다. 임상 증상, 이하학적 소견 및 검사실 소견은 비특이적이라 진단이 쉽지 않다. 낭포성위축증이 발생하는 기전은 아직 명확히 밝혀지지 않았다. 병리학적으로는 십이지장 벽에 존재하는 낭포성 병변과 이소성 췌장조직을 발견할 수 있어 쉽게 진단이 가능하다. 영상학적으로는 두꺼워진 십이지장 벽내에 역시 다양한 크기의 낭종을 관찰할 수 있다. 근본적인 치료를 위해서는 수술적 절제를 하여야 하며 췌십이지장절제술이 가장 좋은 방법으로 알려져 있다.
다국어 초록 (Multilingual Abstract)
Cystic dystrophy is an uncommon, benign poorly understood disease. It is characterized by the development of cysts in heterotopic pancreatic tissue. A 57-year-old-man was hospitalized for abdominal pain for a week. He is a heavy alcohol drinker. There...
Cystic dystrophy is an uncommon, benign poorly understood disease. It is characterized by the development of cysts in heterotopic pancreatic tissue. A 57-year-old-man was hospitalized for abdominal pain for a week. He is a heavy alcohol drinker. There was a cyst at second portion of duodenum on CT. Under the impression of peptic ulcer perforation, Whipple's operation was performed. Grossly, a cystic space, measuring 3.0 cm in diameter, was noted within the thickened duodenal wall. Microscopically, the cyst was lined by columnar epithelium and granulation tissue and embedded in ectopic pancreatic tissue. The adjacent pancreatic tissue showed focal chronic pancreatitis.
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