급성 간염에 의한 간부전증에 병발된 재생불량성 빈혈 1례 = A Caes of Aplastic Anemia following Hepatic Failure by Acute Hepatitis

다국어 초록 (Multilingual Abstract)

Aplastic anemia following acute hepatitis or acute hepatic failure is an uncommon disease and has a poor prognosis. We experienced a case of aplastic anemia following acute hepatic failure in a 10- year-old girl. She was admitted because of jaundice and lethargy for 8 days. Laboratory findings revealed marked elevated serum transaminases and bilirubin levels, prolonged prothrombin time and partial thromboplastin time, and massive hepatic necrosis on the pathological study. There was no evidence of metabolic, toxic or autoimmune hepatitis. During the treatment of acute hepatic failure, pancytopenia developed and marked hypocellularity of all hematopoietic elements in bone marrow was revealed. She recovered partially from aplastic anemia after treatment with anti-thymocyte globulin, corticosteroid and cyclosporine.

국문 초록 (Abstract)

저자들은 8일간의 황달과 기면으로 내원한 10세 여아에서 비-A, 비-B, 비-C형 간염 바이러스에 의한 감염에 의해 급성 간부전증으로 진단되어 치료받던 중 재생불량성 빈혈이 병발하여 anti-thymocyte globulin과 corticosteroid, cyclosporine 병합 요법으로 치료 후 부분 관해 상태로 외래 추적 관찰 중인 1례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

참고문헌 (Reference)

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