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박석연,강경훈,노재윤,제니퍼블랙,정진수,이강현,홍은경,박원서 대한병리학회 2008 Journal of Pathology and Translational Medicine Vol.42 No.1
Mucinous tubular and spindle cell carcinoma (MTSCC) is a rare type of kidney tumor that has only been recently described. Furthermore, a case of MTSCC associated with a simultaneous lung cancer in the same patient has never been reported in the literature. In this paper, we describe a kidney tumor that was detected during staging work-up in a 72-year-old lung cancer patient. The kidney tumor was removed and shown to exhibit histological and immunophenotypic features of MTSCC, completely distinct from the pulmonary adenocarcinoma. In addition, this case was unique because it was characterized by neuroendocrine differentiation as well as p53 and Ki-67 overexpression in tumor cells. Therefore, we report a case of MTSCC diagnosed in a patient with pulmonary adenocarcinoma and describe the detailed histologic and immunohistochemical features of MTSCC. Mucinous tubular and spindle cell carcinoma (MTSCC) is a rare type of kidney tumor that has only been recently described. Furthermore, a case of MTSCC associated with a simultaneous lung cancer in the same patient has never been reported in the literature. In this paper, we describe a kidney tumor that was detected during staging work-up in a 72-year-old lung cancer patient. The kidney tumor was removed and shown to exhibit histological and immunophenotypic features of MTSCC, completely distinct from the pulmonary adenocarcinoma. In addition, this case was unique because it was characterized by neuroendocrine differentiation as well as p53 and Ki-67 overexpression in tumor cells. Therefore, we report a case of MTSCC diagnosed in a patient with pulmonary adenocarcinoma and describe the detailed histologic and immunohistochemical features of MTSCC.
이지숙,이범하,이혜경,이민희,이광우,문아림 대한영상의학회 2013 대한영상의학회지 Vol.69 No.6
Mucinous tubular and spindle cell carcinoma of the kidney has been recognized as a distinct entity in the 2004 World Health Organization classification of adult renal tumors; it constitutes less than 1% of all the renal neoplasm. Radiological features of mucinous tubular and spindle cell carcinoma have been published in a small number of cases. This case report presents a case of mucinous tubular and spindle cell carcinoma, including CT and MR finding. 점액성 세관 방추세포 신장암종은 최근 세계 보건 기구(World Health Organization) 2004년 신세포암 분류에 포함된 질병으로 세관 구조, 방추형 세포, 점액성 기질로 구성되어 있다. 이는 신장암종의 1% 미만을 차지하는 드문 질병으로 아직 영상소견이 확립되지 않았으며 적은 수의 보고가 있다. 본 증례는 점액성 세관 방추세포 신장암종 1예의 CT 및 MR 소견을 보고하고자 한다.
Myxoid Solitary Fibrous Tumor on the Scalp
김지현,김동철,이륜,신치호,한이식,정상훈,백소야 대한두개안면성형외과학회 2017 Archives of Craniofacial Surgery Vol.18 No.4
Myxoid solitary fibrous tumor (SFT) is very rare soft tissue neoplasm. It is microscopically composed of spindle cells which is individually separated by delicate band of collagen fibers. And this tumor cells are immunohisto-chemistrically highlighted by CD34. Myxoid SFT has indolent clinical course and a good prognosis, so it is important to make a diagnosis because of its morphological similarities to myxoid spindle cell neoplasms that have different prognoses and treatment. We report the case of a 20-year-old female with a myxoid SFT found in the left temporo-parietal scalp. This case report appears to be the first reported scalp occurrence of this rare tumor.
Retropharyngeal Spindle Cell/Pleomorphic Lipoma
이현경,황승배,정경호,홍기환,장규윤 대한영상의학회 2013 Korean Journal of Radiology Vol.14 No.3
Spindle cell/pleomorphic lipoma is an uncommon benign adipose tissue tumor most frequently arising from the subcutaneous tissue of the back, shoulder, head and neck, and extremities. The deep cervical spaces are the rarely affected locations. Herein we report on the imaging findings of spindle cell/pleomorphic lipoma involving the retropharyngeal space in an elderly woman.
Clinical-pathologic profile of head and neck rhabdomyosarcoma in children: a systematic review
Ludimila Lem es Moura(Ludimila Lemes Moura ),Beatriz Della Terra Mouco Garrido(Beatriz Della Terra Mouco Garrido ),Nelson Leonel Del Hierro Polanco(Nelson Leonel Del Hierro Polanco ),Mattheus Augusto 대한구강악안면외과학회 2023 대한구강악안면외과학회지 Vol.49 No.2
This systematic review aimed to analyze the clinicopathological profile and relevant prognostic factors of head and neck rhabdomyosarcoma in pediatric patients. The search was carried out in the electronic search portals PubMed, Lilacs, Embase, Scopus, and Web of Science. The search yielded studies that were then analyzed regarding study topic, data extraction, and risk of bias using the STROBE (Strengthening the Reporting of Observational Studies) guidelines. Finally, three studies were included for qualitative analysis. Most of the cases involved embryonic and alveolar rhabdomyosarcoma. Expression of MYOD1 was highly correlated with diagnosis of spindle cell/sclerosing rhabdomyosarcoma, which appears to have a poor prognosis in children. Furthermore, tumor size <5 cm and absence of metastasis accompanied by complete resection and administration of adjuvant therapies such as chemotherapy and radiotherapy favored a better prognosis.
오미혜,정은아,이지혜,조현득,양승하,곽정자 대한병리학회 2010 Journal of Pathology and Translational Medicine Vol.44 No.6
We report a case of spindle cell epithelioma, a so-called benign mixed tumor of the vagina. The patient was a 35-year-old nulliparous woman who presented with a polypoid mass in the posterior wall of the lower vagina just above the hymenal ring. The tumor was relatively welldefined with an expansile margin and composed of stromal-type spindle cells with a myxoid stroma arranged in short fascicles and an irregular cord-like or reticular pattern. A few glandular structures lined by cuboidal cells with squamous metaplasia were also noted. Cellular atypia was not conspicuous and mitosis was not found. We examined this tumor immunohistochemically to identify the histogenesis. The coexpression of epithelial and mesenchymal markers in stromal-type spindle cells suggested a multipotential cell origin for this tumor. The patient has been well with no signs of recurrence during the 12 months after surgery.
A case of spindle cell neoplasm of the neck in a child patient
( Jin Hee Kim ),( Ji Su Lee ),( Sung Min Kim ),( Ji Youn Hong ),( Joo Ran Hong ),( Hye In Cheon ),( Min Seok Hur ),( Yang Won Lee ),( Yong Beom Choe ),( Kyu Joong Ahn ) 대한피부과학회 2019 대한피부과학회 학술발표대회집 Vol.71 No.1
A 5-year-old boy presented with pea-sized vascular lesions on the neck, 2 months ago. The lesions consisted of 6 mm width, 2 mm height sized, indurated, yellowish and firm lesion. The lesion was asymptomatic and had been enlarged in size. He had no specific personal medical history, nor the family history of the lesion. The lesion was suspected as molluscum contagiosum, so we tried to remove through curettage and it was easily removed as whole mass without residual mass tissue visually. In histopathologic examination, mass was consisted with bland-looking spindle cells, with lower than 1 per 10 HPF of mitotic activity. We suspected myofibroma or fibroma, so we performed immunohistochemical staining. The results were positive in SMA stain, negative in CD 34 stain, and negative in desmin stain. Cutaneous tumors are relatively common in children, and most are benign. Spindle cell tumor with cutaneous involvement in children include myofibroma, a variety of cutaneous fibroblastic and myofibroblastic tumors, smooth muscle tumors and other variants. The differential diagnosis with a combination of clinical and histological features and immunohistochemistry is important.
Extraordinarily aggressive cutaneous sarcomatoid squamous cell carcinoma of the face: a case report
Lee, Yunjae,Lee, Dongkyu,Yeo, Hyeonjung,Park, Hannara,Park, Hyochun Korean Cleft Palate-Craniofacial Association 2022 Archives of Craniofacial Surgery Vol.23 No.2
Sarcomatoid squamous cell carcinoma (SSCC), a biphasic malignant tumor consisting of atypical squamous epithelial and mesenchymal elements mixed with epithelioid and spindle cells, is a variant of squamous cell carcinoma. Cutaneous SSCC is very rare and aggressive and has a poor prognosis. Here, we report a case of cutaneous SSCC with satellites and in-transit metastases. A 79-year-old woman presented with a protruding mass on the left temporal area sized 1.2×1.0 cm. The punch biopsy report indicated keratoacanthoma or well-differentiated squamous cell carcinoma. The size of the tumor increased to 2.7×2.0 cm after 8 days. An excisional biopsy was performed with a 2 mm safety margin. The tumor was identified as SSCC with a clear resection margin. Reoperation was performed thrice with an increased safety margin of 10 mm; however, the cancer recurred along with satellites and in-transit metastases. Chemoradiotherapy was administered; however, the size of the tumor increased along with satellites and in-transit metastases. The patient expired 162 days after the initial excision. Complete excision and immediate multidisciplinary approach should be combined during the early stages due to the aggressiveness and poor prognosis of cutaneous SSCC with satellites and in-transit metastasis.
폐에 발생한 다형태 암종 환자에서 전이부위 절제술 후 장기 생존
이진구,정경영,박인규,김대준,변천성,조상호 대한흉부외과학회 2007 Journal of Chest Surgery (J Chest Surg) Vol.40 No.8
Pulmonary pleomorphic carcinomas are rare malignant tumors that account for 0.1 to 0.4% of all lung cancers. They are notable for their aggressive clinical behavior and poor prognosis. We report here on a patient who is alive and disease-free 12 years after receiving surgical treatment for the rib recurrence of pulmonary pleomorphic carcinoma. 폐에서 다형태 암종은 전체 폐암의 0.1∼0.4%를 차지하는 매우 드문 악성 종양으로 나쁜 임상경과와 좋지 않은 예후로 알려져 있다. 저자들은 폐에 발생한 다형태 암종 치료 후 발생한 늑골전이에서 외과적 치료를 통해 12년의 무병 장기 생존을 얻었기에 보고하는 바이다.