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Shah, Saiquat,Huh, Kyung-Hoe,Yi, Won-Jin,Heo, Min-Suk,Lee, Sam-Sun,Choi, Soon-Chul Korean Academy of Oral and Maxillofacial Radiology 2014 Imaging Science in Dentistry Vol.44 No.4
Primitive neuroectodermal tumor (PNET), which belongs to the Ewing's sarcoma (ES) family of tumors, is mainly seen in children and young adults. PNETs are extremely rare in the maxilla. Here, we report a case of PNET of the left maxillary sinus in an elderly male. Magnetic resonance imaging (MRI) revealed a slightly enhanced solid mass occupying the left maxillary sinus and infiltrating into the retroantral space. A partial maxillectomy was performed. Despite postoperative chemotherapy, follow-up computed tomography (CT) and MRI revealed a nodal metastasis in the submandibular space. Neck dissection was performed. However, the patient died 10 months after the second surgery because of distant metastasis to the liver. MRI and CT were particularly useful in detecting the extent of the tumor, recurrence, and metastasis. Further, a literature review of the previously reported PNET cases of the maxilla was carried out. In this paper, we also discuss the current approach for the diagnosis and management of these tumors.
김진수,박상근,안용붕,이상열 인제대학교 1990 仁濟醫學 Vol.11 No.2
저자들은 신경학적 증세가 급속히 악화되고, 연속적으로 시행한 뇌전산화 단층촬영 소견상 급속한 성장을 보인 원시 신경 외배엽 종양을 치험하고 문헌 고찰과 함께 보고한다. We present a case of primitive neuroectodermal tumor with review of the literatures. The tumor was multiple and growing very rapidly We excised this tumor through suboccipital route, and the pathological examination revealed primitive neuroectodermal tumor.
Saiquat Shah,허경회,이원진,허민석,이삼선,최순철 대한영상치의학회 2014 Imaging Science in Dentistry Vol.44 No.4
Primitive neuroectodermal tumor (PNET), which belongs to the Ewing's sarcoma (ES) family of tumors, is mainly seen in children and young adults. PNETs are extremely rare in the maxilla. Here, we report a case of PNET of the left maxillary sinus in an elderly male. Magnetic resonance imaging (MRI) revealed a slightly enhanced solid mass occupying the left maxillary sinus and infiltrating into the retroantral space. A partial maxillectomy was performed. Despite postoperative chemotherapy, follow-up computed tomography (CT) and MRI revealed a nodal metastasis in the submandibular space. Neck dissection was performed. However, the patient died 10 months after the second surgery because of distant metastasis to the liver. MRI and CT were particularly useful in detecting the extent of the tumor, recurrence, and metastasis. Further, a literature review of the previously reported PNET cases of the maxilla was carried out. In this paper, we also discuss the current approach for the diagnosis and management of these tumors.
Ewing`s Sarcoma Of The Lesser Sac Masquerading As A Pancreatic Tumor
( Lakshmi Rao ),( Vidya Monappa ),( Gabriel Rodrigues ),( B P Suresh ) 대한내과학회 2012 The Korean Journal of Internal Medicine Vol.27 No.1
Extraosseous Ewing`s sarcoma/primitive neuroectodermal tumor (ES/PNET) is an uncommon, aggressive, and malignant tumor with a poor patient outcome. Its occurrence in the lesser sac is a rare event and to the best of our knowledge, has not been previously described. The present case was clinically and radiologically misdiagnosed as a pancreatic tumor/gastrointestinal stromal tumor. Histopathology revealed a tumor with "small round cells" that were positive for CD99, confirming the diagnosis of ES/PNET. This report highlights the importance of considering Ewing`s sarcoma in the differential diagnosis of intraabdominal, extraintestinal masses.
Primary Epidural Peripheral Primitive Neuroectodermal Tumor of the Lumbar Spine: A Case Report
최우정,이승훈,주경빈,백승삼,이영호,전영진 대한영상의학회 2011 대한영상의학회지 Vol.64 No.5
A primitive neuroectodermal tumor (PNET) is a highly malignant tumor in children and young adults, and extremely rare in the spine. We report a case of a primary epidural peripheral PNET of the lumbar spine. The present extremely rare case of primary epidural peripheral PNET of the lumbar spine illustrates the unexpected occurrence and should be included in differential diagnoses for patients with spinal tumors.
Multimodal Treatment of Primary Extraskeletal Ewing’s Sarcoma of the Chest Wall: Report of 2 Cases
이우성,김요한,지현근,황재준,김준석,이송암,황은구,조요한,전규락 대한암학회 2009 Cancer Research and Treatment Vol.41 No.2
Extraskeletal Ewing’s sarcoma (EES) is a type of Ewing’s sarcoma that arises in soft tissue and is now regarded as a member of a family of small round cell neoplasms of bone and soft tissue, including primitive neuroectodermal tumors (PNETs). EES occurs predominantly in adolescents and young adults between the ages of 10 and 30 years. The disease follows an aggressive course with a high recurrence rate. The presence of a distant metastasis is also common. EES arises in the soft tissue of either the trunk or extremities. We recently experienced two cases of EES that occurred in the chest wall. The two patients underwent wide resection and combined radiochemotherapy. There was no evidence of disease 30 and 22 months, respectively, after surgery. Although extremely rare, EES should be considered in the differential diagnosis of chest wall tumors. We report two cases of EES with a brief review of the literature.
전호규,하영수,박종운,김영,채권병,이상돈,김재중,진태경 대한신경외과학회 1994 Journal of Korean neurosurgical society Vol.23 No.8
Primitive neuroectodermal tumors(PNETs) are composed of undifferentiated cells resembling germinal matrix cells of the embryonic neural tube. The concept of the primitive neuroectodermal tumors is controversial due to indistinct clinicopathologic entities. While some neuropathologists believe that the PNET concept should be applied to all these tumors with the addition of qualifying terms, the opponents of this approach believe this concept to be too simplistic and that well-established diagnostic entities should not be grouped together as a single entity. Four patients with PNET were reviewed. Although the PNETs bear some differences to posterior fossa medulloblastomas, we should be grouped together as a single pathologic entity because of their primitive nature. The purpose of this study is to review the similarities and differences between two tumors from their histologic and embryologic features.